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Differential
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aminoacidopathies
cirrhosis
cirrhosis, infancy
emergencies, neurologic
enzyme, defect
genetic neurologic disorders
genetic screening
hepatic failure
hypertonia
hyponatremia
ileus, paralytic
inborn errors of metabolism
liver disease
mortality
muscle weakness
nerve biopsy
neuropathy
neuropathy, painful
neuropathy, peripheral
pain
prognosis
respiratory failure
self-mutilation
tyrosine
tyrosinemia
weakness
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Neurologic Crises in Hereditary Tyrosinemia
NEJM 322:432-437, Mitchell,G.,et al, 1990
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