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We describe a patient with presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia.There were demyelinating MRI changes in the parieto-occipital white matter bilaterally,including the splenium of the corpus callosum.Therapeutic trials using 1-deamino-(8-D- arginine)-vasopressin,very long-chain fatty acid-free diet,and y-globulin were of no benefit. |
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