Neurology Specific Literature Search   
 
[home][thesaurus]
    
Click Here to return To Results

 

Familial Infantile Bilateral Striatal Necrosis
Neurol 59:983-989, Straussberg,R.,et al, 2002
See this aricle in Pubmed

Article Abstract
Familial infantile bilateral striatal necrosis was inherited as an autosomal recessive trait. Clinical features included developmental arrest, dysphagia, and choreoathetosis. Imaging and pathology showed atrophy and degeneration of the bas al ganglia. Oral biotin may have benefited three children.
 
Related Tags
(click to filter results - removes previous filter)

basal ganglia
basal ganglia,degeneration
basal ganglia,lesion of
basal ganglia,lesion,bilateral
biotin
choreoathetosis
familial
genetic neurologic disorders
infantile bilateral striatal necrosis
lenticular nucleus,lesion of,bilateral
MRI,abnormal
neuropathology
striatum,lesion of
treatment of neurologic disorder

Click Here to return To Results