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Diagnosis of Human Prion Disease Using Real-Time Quaking-Induced Conversion Testing of Olfactory Mucosa and Cerebrospinal Fluid Samples
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Creutzfeldt-Jakob Disease (Subacute Spongiform Encephalopathy)
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Cortical Restricted Diffusion as the Predominant MRI Finding in Sporadic Creutzfeldt-Jakob Disease
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Clinicopath conf., Human Prion Disease, Sporadic CJD
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14-3-3 Testing in Diagnosing Creutzfeldt-Jakob Disease
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Heroin-Induced Spongiform Leukoencephalopathy: Value of Diffusion MF Imaging
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Progressive Aphasia with Rapidly Progressive Dementia in a 49 Year Old Woman
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Surgical Treatment and Risk of Sporadic Creutzfeldt-Jakob Disease:A Case-Control Study
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Risk of Transmission of Bovine Spongiform Encephalopathy to Humans in the United States, Report of the Council on Scientific Affairs
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Detection of 14-3-3 Protein in Cerebrospinal Fluid Supports Dx of Creutzfeldt-Jakob Disease
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Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
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Heroin Inhalation and Progressive Spongiform Leukoencephalopathy
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The 14-3-3 Brain Protein and Transmissible Spongiform Encephalopathy
NEJM 336:873-875, Moussavian,M.,et al, 1997
Rapid Spongiform Degeneration of the Cerebrum and Cerebellum in Creutzfeldt-Jakob Encephalitis:Serial MR Findings
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The Risk of Bovine Spongiform Encephalopathy ('Mad Cow Disease') to Human Health
JAMA 278:1008-1011, Brown,P., 1997
Clinical, Neuroimaging, and Pathologic Features of Progressive Nonfluent Aphasia
Ann Neurol 39:166-173, Turner,R.S.,et al, 1996
Bovine Spongiform Encephalopathy and Creutzfeldt-Jakob Disease
BMJ 312:790-791, Brown,P., 1996
A New Variant of Creutzfeldt-Jakob Disease in the UK
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Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
Ann Neurol 39:343-351, Rahman,S.,et al, 1996
The 14-3-3 Brain Protein in Cerebrospinal Fluid as a Marker for Transmissible Spongiform Encephalopathies
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MRI of Creutzfeldt-Jakob Disease:Asymmetric High Signal Intensity of the Basal Ganglia
Neurol 45:1932-1933, Yoon,S.S.,et al, 1995
Creutzfeldt-Jakob Disease and Bovine Spongiform Encephalopathy:Any Connection?
BMJ 311:1415-1421, Almond,J.W., 1995
Human Prion Diseases
Ann Neurol 35:385-395, Prusiner,S.B.&Hsiao,K.K., 1994
Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
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Leigh Disease (Subacute Necrotizing Encephalomyelopathy) :CT & MR in Five Cases
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