Transmissible Spongiform Encephalopathy in the 21st Century: Neuroscience for the Clinical Neurologist
Neurol 70:713-722, Brown,P., 2008
Leigh Disease (Subacute Necrotizing Encephalomyelopathy) :CT & MR in Five Cases
J Comput Assist Tomogr 12:40-44, Geyer,C.A.,et al, 1988
Transmissible Spongiform Encephalopathies
Lancet 363:51-61, Collins,S.J.,et al, 2004
Neurodegenerative Diseases and Prions
NEJM 344:1516-1526,1548, Prusiner,S.B., 2001
14-3-3 Testing in Diagnosing Creutzfeldt-Jakob Disease
Neurol 55:514-516, Lemstra,A.W. et al, 2000
Progressive Aphasia with Rapidly Progressive Dementia in a 49 Year Old Woman
JNNP 66:238-243, Greene,J.D.W.,et al,, 1999
Surgical Treatment and Risk of Sporadic Creutzfeldt-Jakob Disease:A Case-Control Study
Lancet 353:693-697, Collins,S.,et al, 1999
Risk of Transmission of Bovine Spongiform Encephalopathy to Humans in the United States, Report of the Council on Scientific Affairs
JAMA 281:2330-2339, Tan,L.,et al, 1999
Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
NEJM 339:1994-2004, Johnson,R.T. & Gibbs,Jr.,C.J., 1998
The Risk of Bovine Spongiform Encephalopathy ('Mad Cow Disease') to Human Health
JAMA 278:1008-1011, Brown,P., 1997
Transmissible Spongiform Encephalopathies
NEJM 337:1821-1828, Haywood,A.M., 1997
Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
Ann Neurol 39:343-351, Rahman,S.,et al, 1996
Canavan Disease:From Spongy Degeneration to Molecular Analysis
J Pediatr 127:511-517, Matalon,R.,et al, 1995
Human Prion Diseases
Ann Neurol 35:385-395, Prusiner,S.B.&Hsiao,K.K., 1994
Human Spongiform Encephalopathy:The NIH Series of 300 Cases of Experimentally Transmitted Disease
Ann Neurol 35:513-529, Brown,P.,et al, 1994
Infectious Prions or Cytotoxic Metabolites?
Lancet 341:159-161, Pablos-Mendez,A.,et al, 1993
The Spongiform Encephalopathies, Editorial
JNNP 54:761-763, Will,R.G., 1991
Creutzfeldt-Jakob Disease and Other Transmissible Spongiform Encephalopathies
Ed, F. O. Bastian, Mosby Year Book, St. Louis 9:153, Maertens,P.&Quindlen,E.A., 1991
Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
Neurol 40:1876-1882, Gascon,G.G.,et al, 1990
Diffuse Lewy Body Disease and Progressive Dementia
Neurol 38:1520-1528, Burkhardt,C.R.,et al, 1988
Prions & Neurodegenerative Diseases
NEJM 317:1571-1581, 15971987., Prusiner,S.B., 1987
Creutzfeldt-Jakob Disease after Administration of Human Growth Hormone
Lancet 2:244-246, Powell-Jackson,J.,et al, 1985