The Polymerase Chain Reaction:Application to Nervous System Disease
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Fragile X-Associated Tremor or Ataxia Syndrome in a Patient with Difficulty Walking, Falls, a Tremor, and Erectile Dysfunction
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Hereditary Spastic Paraplegia:From Diagnosis to Emerging Therapeutic Approaches
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Pantothenate Kinase - Associated Neurodegeneration (PKAN)
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Dentate Update: Imaging Features of Entities that Affect the Dentate Nucleus
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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Leukodystrophy and Progressive Myoclonic Epilepsy Disclosing DRPLA
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A Young Man with Progressive Language Difficulty and Early-Onset Dementia
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Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
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Ataxia, Dementia, and Hypogonadotropism Caused by Disordered Ubiquitination
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Clinicopathologic Conference, Kufs Disease (Autosomal Dominant) Parry Type Neuronal Ceroid Lypofuscinosis
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Differential Diagnosis of Bilateral Abnormalities of the Basal Ganglia and Thalamus
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Huntingtons Disease
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Progressive Supranuclear Palsy: A Current Review
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T2* and FSE MRI Distinguishes Four Subtypes of Neurodegeneration With Brain Iron Accumulation
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Rapidly Progressive Dementia
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Individual Dopaminergic Neurons Show Raised Iron Levels in Parkinson Disease
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Neuroimaging Findings in Human Prion Disease
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The "Eye-of-the-Tiger" Sign is Not Pathognomonic of the PANK2 Mutation
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Imaging Cerebral Atrophy:Normal Ageing to Alzheimer's Disease
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Genetic, Clinical, and Radiographic Delineation of Hallervorden-Spatz Syndrome
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MR Features of Diseases Involving Bilateral Middle Cerebellar Peduncles
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Clinicopath Conf, Neuronal Ceroid Lipofuscinosis, Late-Onset Infantile Subtype
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Headache and CNS White Matter Abnormalities Associated with Gluten Sensitivity
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CSF Detection of the 14-3-3 Protein in Unselected Patients with Dementia
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A New Metabolite Contributing to N-Acetyl Signal in 1H MRS of the Brain in Salla Disease
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Progressive Atrophy of Cerebellum & Brainstem, Age & Size of Expanded CAG Repeats in the MJDI Gene in Machado-Joseph Dis
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Machado-Joseph Disease in 4 Chinese Pedigrees:Molecular Analysis of 15 Pts
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CT and MR Findings of Neuroacanthocytosis
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Cerebral & Cerebellar Atrophy on Serial MRI in an Initially Symptom Free Subject at Risk of Familial Prion Disease
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Wolfram Syndrome:Hereditary Diabetes Mellitus with Brainstem and Optic Atrophy
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Neurodegeneration and Diabetes:UK Nationwide Study of Wolfram (DIDMOAD) Syndrome
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Magnetic Resonance Imaging of Brain Iron in Health and Disease
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Trinucleotide Repeat Expansion in Neurological Disease
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Magnetic Resonance Imaging in Hereditary and Idiopathic Ataxia
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Wolfram Syndrome:Evidence of a Diffuse Neurodegenerative Disease by Magnetic Resonance Imaging
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MR Imaging of the Spinal Cord:Current Status and Futue Advances
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Degeneration of the Posterior Columns of the Spinal Cord:Postmortem MRI and Histopathology
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Neurodegenerative Diseases of Childhood:MR and CT Evaluation
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The Marinesco-Sjogren Syndrome Examined by CT, MR, and 18F-2-Fluoro-2-Deoxy-D-Glucose & PET
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Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
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Magnetic Resonance Imaging in Familial Paroxysmal Ataxia
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Posterior Cortical Atrophy
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Syndrome of Palatal Myoclonus & Progressive Ataxia:Two Cases with Magnetic Resonance Imaging
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Olivopontocerebellar Atrophy in Children:A Report of Seven Cases in Two Families
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