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Progressive Pontobulbar Palsy With Deafness
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Olivopontocerebellar Atrophy in Children:A Report of Seven Cases in Two Families
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Consequences of the Delayed Diagnosis of Ataxia-Telangiectasia
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Wolfram Syndrome:Hereditary Diabetes Mellitus with Brainstem and Optic Atrophy
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Wolfram Syndrome:Evidence of a Diffuse Neurodegenerative Disease by Magnetic Resonance Imaging
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Familial Multisystem Atrophy with Possible Thalamic Dementia
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Familial Subacute Necrotizing Encephalomyelopathy of the Adult Form (Adult Leigh Syndrome)
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Stridor in Multiple System Atrophy
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Atypical Parkinsonian Syndromes: A General Neurologists Perspective
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A Young Man with Progressive Language Difficulty and Early-Onset Dementia
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Multiple-System Atrophy
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Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
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Differential Diagnosis of Bilateral Abnormalities of the Basal Ganglia and Thalamus
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Huntingtons Disease
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Fragile X-Associated Tremor/Ataxia Syndrome: An Aging Face of the Fragile X Gene
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Spinal Muscular Atrophy
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Rapidly Progressive Dementia
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Second Consensus Statement on the Diagnosis of Multiple System Atrophy
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Recessive Ataxia With Ocular Apraxia
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Headache and CNS White Matter Abnormalities Associated with Gluten Sensitivity
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CT and MR Findings of Neuroacanthocytosis
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Excitatory Amino Acids as a Final Common Pathway for Neurologic Disorders
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Chronic Neurodegenerative Disease Associated with HTLV-II Infection
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Protein Processing in Lysosomes:The New Therapeutic Target in Neurodegenerative Disease
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MR Imaging of the Spinal Cord:Current Status and Futue Advances
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Neurological Clues from Environmental Neurotoxins
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Fatal Familial Insomnia & Dysautonomia with Selective Degeneration of Thalamic Nuclei
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Epidemiology of Motor-Neuron Diseases
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