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Degenerative Diseases of the Nervous System, Amyotrophic Lateral Sclerosis
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Degenerative Diseases of the Nervous System, Primary Lateral Sclerosis
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Rapidly Progressive Frontotemporal Dementia with Amytrophic Lateral Sclerosis in an Elderly Female
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Young Adult with Dysphagia and Severe Weight Loss
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Primary Lateral Sclerosis, Clin Features, Neuropath & Dx Criteria
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Chronic Progressive Spinobulbar Spasticity, A Rare Form of Primary Lateral Sclerosis
Arch Neurol 45:509-513, Gastaut,J.L.,et al, 1988
Lathyrism:Evidence for Role of the Neuroexcitatory Aminoacid BOAA
Lancet 2:1066-1067, Spencer,P.S.,et al, 1986
Clinical & Electrophysiological Studies in Primary Lateral Sclerosis
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A 60-Year-Old Man with Weakness and Gait Dysfunction
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Spinal Muscular Atrophy
UpToDate, Oct, Bodamer,O.A., 2022
Non-Alzheimers Dementia 1 Frontotemporal Dementia
Lancet 386:1672-1682, Bang, Jee.,et al, 2015
Degenerative Diseases of the Nervous System, Kugelberg-Welander Syndrome SMAIII
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Spinal Muscular Atrophy
Lancet 371:2120-2133, Lunn,M.R. &Wang,C.H., 2008
Amyotrophic Lateral Sclerosis
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Amyotrophic Lateral Sclerosis
NEJM 344:1688-1700, Rowland,L.P. & Shneider,N.A., 2001
Inborn Errors of Metabolism as a Cause of Neurological Disease in Adults: An Approach to Investigation
JNNP 69: 5-12, Gray,R.G.F. et al, 2000
Flail Arm Syndrome: A Distinctive Variant of Amyotrophic Lateral Sclerosis
JNNP 65:950-951, Hu, M.T.M.,et al, 1998
Motor Neuron Disease
JNNP 57:886-896, Leigh,P.N.&Ray-Chaudhuri,K., 1994
MRI and SPECT in Amyotrophic Lateral Sclerosis, Demonstr of Upper Motor Neurone Invol by Neuroimaging
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Pick's Disease:A Case Clinically Resembling Amyotrophic Lateral Sclerosis
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Selective Involvement of the Pyramidal Tract on Magnetic Resonance Imaging in Primary Lateral Sclerosis
Neurol 40:1799-1800, Marti-Fabregas,J.&Pujol,J., 1990
HTLV-1 Associated Myelopathy and Polymyositis in a US Native
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Incontinentia Pigmenti:Association with Anterior Horn Cell Degeneration
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Hopkins Syndrome
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Amyotrophic Lateral Sclerosis
NEJM 377:162-172, Brown, R.H.,et al, 2017
Acute Flaccid Myelitis; A Clinical Review of US Cases 2012-2015
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Owls Eye Sign
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Acute Flaccid Myelitis of Unknown Etiology in California 2012-2015
JAMA 314:2663-2671, Van Haren, K.,et al, 2015
Motor Neurone Disease
BMJ 349:g4052, Nageshwaran, S.,et al, 2014
Degenerative Diseases of the Nervous System, Progressive Muscle Atrophy
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Degenerative Diseases of the Nervous System, Progressive Bulbar Palsy
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Degenerative Diseases of the Nervous System, Werdnig-Hoffman Disease, Spinal Muscular Atrophy
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Spinal Muscular Atrophy A Timely Review
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Diagnosis and Management of Motor Neurone Disease
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The Natural History of Primary Lateral Sclerosis
Neurol 66:647-653, Gordon,P.H.,et al, 2006
Frontotemporal Lobar Degeneration with Motor Neuron Disease
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Polymyositis Masquerading as Motor Neuron Disease
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Inclusiong Body Myositis Mimicking Motor Neuron Disease
Arch Neurol 58:1253-1256, Dabby,R.,et al, 2001
Nonpoliovirus Poliomyelitis Simulating Guillain-Barre Syndrome
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Amyotrophic lateral Sclerosis Mimic Syndromes, A Population-Based Study
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Atypical Form of Amyotrophic Lateral Sclerosis
JNNP 66:581-585, Sasaki,S.&Iwata,M., 1999
Brachial Amyotrophic Diplegia, A Slowly Progressive Motor Neuron Disorder
Neurol 53:1071-1076, Katz,J.S.,et al, 1999
Distal Hereditary Upper Limb Muscular Atrophy
JNNP 64:217-220, Gross,D.W.,et al, 1998
Amyloid Neuropathy Simulating Lower Motor Neuron Disease
Neurol 51:600-602, Quattrini,A.,et al, 1998
Prognosis in Familial ALS:Progr & Surv in Pts with glu100gly & ala4val Mutations in Cu, Zn Superoxide Dismutase
Neurol 48:55-57, Juneja,T.,et al, 1997
Neurogenic Muscle Hypertrophy
Muscle & Nerve 19:811-818996., Gutmann,L., 1996
Avoiding False Positive Diagnoses of Motor Neuron Disease:Lessons from the Scottish Motor Neuron Disease Register
JNNP 60:147-151, Davenport,R.J.,et al, 1996
Diagnosing Motor Neurone Disease
BMJ 312:650-651, Chancellor,A.M., 1996