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Unmasking Cerebrotendinous Xanthomatosis, Clinical Recognition of a Treatable Cause of Progressive Ataxia
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A 72-year-old Man with a Progressive Cognitive and Cerebellar Syndrome
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Challenging Diagnosis of Gerstmann-Straussler-Scheinker Disease
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Clinicopathologic Conference, Creutzfeldt-Jakob Disease
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Cerebellar Ataxia and Hearing Impairment
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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A 50-year-old Man with Headache and Cognitive Decline
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Neuronal Intranuclear Inclusion Disease Cases with Leukoencephalopathy Diagnosed via Skin Biopsy
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Creutzfeldt-Jakob Disease (Subacute Spongiform Encephalopathy)
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Clinical Reasoning: A Woman with Rapidly Progressive Apraxia
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Limbic Encephalitis as the Presenting Feature of Sj�gren Syndrome
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Ataxia, Dementia, and Hypogonadotropism Caused by Disordered Ubiquitination
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Central Nervous System Involvement in Whipple Disease
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Expanding the Clinical, Radiological and Neuropathological Phenotype of Chronic Lymphocytic Inflammation with Pontine Perivascular Enhancement Responsive to Steroids (CLIPPERS)
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Anti-Glutamic Acid Decarboxylase Limbic Encephalitis Without Epilepsy Evolving Into Dementia with Cerebellar Ataxia
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Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease
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A 23-Year-Old Man With Seizures and Visual Deficit
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Infantile Neuroaxonal Dystrophy,Clinical Spectrum and Diagnostic Criteria
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Fluid Attenuation Inversion Recovery (FLAIR) Images of Dentatorubropalliodoluysian Atrophy:Case Report
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Posterior Cerebral Artery Syndromes
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Cerebral & Cerebellar Atrophy on Serial MRI in an Initially Symptom Free Subject at Risk of Familial Prion Disease
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Clinical, Neuropath & Genetic Studies of Large Spinocerebellar Ataxia Type 1 (SCA1) Kindred: (CAG) n Early Premonitory Signs & Symp
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Methylmercury Poisoning:Long-Term Clinical, Radiological, Toxicological, and Pathological Studies of an Affected Family
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Brain MRI and Electrophysiologic Abnormalities in Preclinical and Clinical Adrenomyeloneuropathy
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Cerebrotendinous Xanthomatosis:Clinical and MRI Study (A Case Report)
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Ethanol and the Nervous System
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Gerstmann-Straussler-Scheinker Disease, I, Extending the Clinical Spectrum
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Granulomatous Angiitis of the Central Nervous System:Protean Manifestations and Response to Treatment
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Hereditary Dentatorubral-Pallidoluysian Atrophy:Clinical and Pathologic Variants in a Family
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Neurologic Aspects of Boxing
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Ataxic Creutzfeldt-Jakob Disease:Diagnostic Techniques & Neuropathologic Observations in Early Disease
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Long-Term Treatment of Cerebrotendinous Xanthomatosis with Chenodeoxycholic Acid
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A 68-YEar-Old Man with Progressive Numbness, Vertigo, and Cognitive Decline
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A 60-Year-Old Man with Weakness and Gait Dysfunction
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Rapidly Progressive Frontotemporal Dementia with Amytrophic Lateral Sclerosis in an Elderly Female
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Acute and Progressive Cognitive Decline in a 38-Year-Old Man
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A 30-Year-Old Woman Presenting with Rapidly Progressive Dementia and Extreme Hypoglycorrhachia
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A 51-Year-Old Woman with Abnormal Corups Callosum Signal
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