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Differential
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abdominal distention
acetazolamide
aciduria
acyl CoA dehydrogenase deficiency
addiction, heroin
adverse drug reaction
aggression
agitation
alcohol intoxication
alcoholic withdrawal states, DT's, convulsions, etc.
alcoholism
alkalosis, respiratory
alopecia
aminoacidopathies
aminoacidurias
ammonia
amyloidosis
anemia
anemia, megaloblastic
anesthesia, general
anion gap
anorexia
anorexia nervosa
antibiotics
antibiotics, neurologic complications with
Apgar score
aphasia
areflexia
arm weakness
arrhythmia, cardiac
Asians
asymptomatic
ataxia
ataxia, cerebellar
ataxia, progressive
ataxia, truncal
ataxic gait
autonomic dysfunction
B 12 deficiency
Babinski sign
basal ganglia
basal ganglia, calcification of
basal ganglia, lesion of
basal ganglia, lesion, bilateral
bat bite
bath salts, psychoactive
behavior, combative
behavioral disorder
behavioral disorder, acute
beriberi
beta-D-glucon
biotin
biotin deficiency
biotin deficiency, juvenile form
biotinidase deficiency
blindness
blindness, sudden
bradykinesia
brain atrophy
brain biopsy
brainstem, lesion of
BUN, elevated
buried bumper syndrome
cachexia
calcification, intracranial
Canavan's disease
carbonic anhydrase II deficiency
carcinoma
cardiac arrest
cardiomegaly
cardiomyopathy
carnitine deficiency
carnitine deficiency myopathy
CAT scan
CAT scan, abnormal
CAT scan, disappearing lesion on
CAT scan, false negative
cataracts
caudate nucleus, lesion of
central nervous system, infection of
cerebellar atrophy, primary
cerebellar atrophy, secondary
cerebellar degeneration
cerebellar hemorrhage
cerebral cortex
cerebral cortical atrophy
cerebral edema
cerebral infarction
cerebral palsy
cerebral palsy, risk factors
cerebrospinal fluid, elevated protein of
cerebrospinal fluid, lactic acid concentration
cerebrospinal fluid, proteincytologic dissociation
cerebrovascular accident
cerebrovascular accident, familial occurrence
cerebrovascular accident, infancy and childhood
cerebrovascular accident, mimics
cerebrovascular accident, multiple
cerebrovascular accident, nonvascular territory
cerebrovascular accident, recurrent
cerebrovascular accident, young adult
children
chorea
choreoathetosis
chromosome 19
chronic progressive external ophthalmoplegia
Clinical Pathologic Conference(C.P.C.)
clonus
coagulopathy
cobalamin C deficiency
cocaine
coenzyme Q10
coenzyme Q10 deficiency
cognition
coma
coma, sudden onset
compartment syndrome
compartment syndrome, abdominal
complications
compression fracture
confusion
conjunctival biopsy
conjunctivitis
cornea, abnormal
cortical blindness
cranial nerve palsies
creatine phosphokinase(CPK)elevated
creatinine, elevated
cultured skin fibroblasts
cyanide poison
cyanosis
D-dimer
deafness
deep gray nuclei
degenerative diseases of CNS
delirium
delusion
dementia
dementia, rapidly progressive
dentate nuclei
dentate nuclei, lesion of
depressants
depression
dermatitis
designer drugs
developmental milestones
developmental milestones, loss of
developmental retardation
dexterity, impaired
diabetes dialysis basal ganglia syndrome
diabetes mellitus
diabetes mellitus, neurologic manifestations of
dialysis
diarrhea
diet
differential diagnosis
diplopia
disability, neurological
disorientation
disseminated intravascular coagulation(DIC)
distal muscle weakness
disulfiram
dizziness
D-lactate acidosis
downward deviation of eyes
drug abuse
drug abuse, toxic screen In
drug induced neurologic disorders
drug overdose
dysarthria
dysphagia
dyspnea
dystonia
dystonic reaction, acute
echocardiogram
electrocardiogram, abnormal
electroencephalogram, abnormalities of
electron microscopy
emotional lability
encephalitis
encephalitis, viral
encephalomyopathy
encephalopathy
encephalopathy, acute
encephalopathy, metabolic
encephalopathy, neonatal
encephalopathy, progressive
endocarditis
endocarditis, marantic
enzyme, defect
episodic neurologic deficits
ethylene glycol
exercise
exercise intolerance
exercise-induced neurologic dysfunction
exome sequencing
eye movement, disorders of
facial asymmetry
facial weakness
Fahr disease
failure to thrive
falling
false negative
familial
fatigue
fetal distress
fever
fingerprint bodies
fluctuate
formication
fracture, pathologic
gadolinium
gait disorder
gait, spastic
gastrointestinal bleeding
gastrostomy, percutaneous endoscopic
gender
gene
gene mutation
genetic counselling
genetic neurologic disorders
genetic screening
genetic testing
globus pallidus, hemorrhage
globus pallidus, infarction
globus pallidus, lesion of
globus pallidus, lesion of, bilateral
glutaric acidemia
glutaric aciduria
gout
growth retardation
hallucination
hallucination, auditory
headache
headache, severe
hearing loss
hemianopia
hemianopia, transient
hemiparesis
hemiparesis, transient
hemiplegia
hemorrhagic diathesis
hemorrhagic shock encephalopathy syndrome
hepatic failure
hepatomegaly
heralding manifestation
herniated disc, differential diagnosis of
herpes simplex encephalitis
hirsutism
Hispanics
histochemistry of muscle
homocysteine, serum
homocystinuria
hydrocephalus
hydrophobia
hyperammonemic encephalopathy
hyperbilirubinemia
hypercapnia
hypercoagulable state
hyperhomocysteinemia
hyperkalemia
hyperreflexia
hypersegmented polys
hypertension
hyperthermia
hypoglycemia
hypokalemia
hypotonia
hypoxia
hypoxia, newborn
iatrogenic neurologic disorders
ileus, paralytic
imbalance
immunofluorescence
impulsivity
inappropriate behavior
inattention
inborn errors of metabolism
inclusion bodies
infection
in-hospital
intellectual deficit
intellectual deterioration
internal capsule
intracranial pressure, increased
intravenous drug abuse
iron, brain
isoniazid
isopropyl alcohol
jaundice
kaliuresis
Kearns-Sayre syndrome
keratoconjunctivitis
ketoacidosis
ketonuria
lactic acidemia
lactic dehydrogenase(LDH)
laughing, pathologic
Leigh's disease
lenticular nucleus, lesion of
lenticular nucleus, lesion of, bilateral
lentiform fork sign
lethargy
leukocytosis
leukodystrophy
level of consciousness, decreased
level of consciousness, decreased acute
lipid storage myopathy
liver function enzymes
Lowe's syndrome
lysosomal storage disease
magnetic susceptibility
malabsorption
malignant hyperpyrexia
maple syrup urine disease
marche a petits pas
MELAS syndrome
memory, defect of recent
memory, impairment of
meningitis
meningitis, aseptic
mental retardation
mental status, abnormal
mental status, abnormal, acute
metabolic acidosis
metabolic disorder, primary
metformin
methcathinone
methylmalonic acid, serum
methylmalonic acidemia
methylmalonic aciduria
metronidazole
microangiopathic hemolytic anemia
microhemorrhage, intracerebral
midbrain, infarction of
midbrain, lesion of
middle cerebellar peduncle
middle cerebellar peduncle, lesion
middle cerebellar peduncle, lesion, bilateral
migraine
misdiagnosis
mitochondrial disease
mitochondrial encephalomyopathy
molecular genetics
mortality
motor neuron disease
movement disorder
movement disorder, extrapyramidal
MRI
MRI, abnormal
MRI, complications with
MRI, contrast enhanced
MRI, diffusion weighted
MRI, disappearing lesion on
MRI, FLAIR
MRI, paramagnetic effect
MRI, serial
MRI, spinal cord
MRI, spinal cord, increased intramedullary cord signal
MRI, susceptibility weighted
MRI, T1 weighted high signal foci
mucormycosis
multiple organ failure
multiple sclerosis
multiple sclerosis, differential diagnosis of
muscle biopsy
muscle cramp
muscle pain
muscle relaxant
muscle weakness
muscle weakness, proximal
myasthenia gravis, differential diagnosis
myasthenia gravis, misdiagnosis of
myelitis, longitudinal
myeloneuropathy
myelopathy
myoclonus
myoclonus, epilepsy
myoglobinuria
myopathy
myopathy, mitochondrial
myopathy, proximal
myotonia
myotonia congenita
myotonia, treatment of
nausea and vomiting
neck weakness
negative
Negri bodies
neonatal epileptic encephalopathy
nephrotic syndrome
neuroendocrinology
neurologic complications of, systemic disease
neurologic disease
neurologic disease, diagnoses of
neurologic examination, focal
neurologic signs
neurologic testing
neuromuscular blockade
neuronal ceroid-lipofuscinosis
neurons
neuroophthalmology
neuropathology
neuropathology, brain
neuropathy
neuropathy, peripheral
neuropathy, sensory
neuropathy, toxic
neurotoxic
neurotoxicity, acute
neurotoxin
night sweats
nitrous oxide
normal
numbness, ascending
numbness, generalized
nutritional deficiency
nystagmus
nystagmus, rotary
obesity
occipital lobe, infarction
occipital lobe, infarction, bilateral
ophthalmoplegia
ophthalmoplegia, progressive external
optic atrophy
optic foramina
optic foramina, abnormal
ornithine transcarbamylase deficiency
osteopetrosis
osteoporosis
pain
pain, abdominal
pain, arm
pancytopenia
paramyotonia congenita
paranoia
paraplegia
paresthesias
paresthesias, feet
paresthesias, generalized
paresthesias, hands
Parkinsonism syndrome
paroxysmal neurologic deficits
partial thromboplastin time, prolonged
pernicious anemia
peroxisomal disease
personality change
pleocytosis of cerebrospinal fluid
polymerase chain reaction
pons, lesion of
posterior cerebral artery territory infarction
posterior column disease
precipitating factors
prevention of neurologic disorders
prognosis
progressive neurologic disorder
propionic aciduria
propofol
proptosis
proteinuria
pruritus
psychiatric problems in neurologic disorders
psychomotor retardation
psychosis
psychotic behavior
ptosis
pulmonary edema
pulmonary embolism
putamen, lesion of
putamen, lesion of, bilateral
pyramidal tract dysfunction
pyridoxine
pyridoxine deficiency
pyruvate dehydrogenase deficiency
pyruvate metabolism, abnormality of
quadriparesis
rabies prophylaxis
rabies, nervous system involvement with
ragged-red fibers
rapidly progressing neurologic illness
rash
recurrent
renal biopsy
renal failure
renal failure, acute
renal tubular acidosis
respiratory tract infection
retina, abnormal
retinitis pigmentosa
reversible neurologic disorder
review article
rhabdomyolysis
rickets
rigidity
risk factors
Romberg's sign
salicylate intoxication
schistocytes
sedation
seizure
seizure, children
seizure, drug-induced
seizure, intractable
seizure, intractable, treatment of
seizure, neonatal
seizure, treatment of
self harm
sensorineural hearing loss
sensory level
sensory loss
sensory loss, glove-stocking
shock, hypovolemic
short stature
skin, biopsy
skin, lesions in neurologic disorders
skin, pink
skull x-ray, abnormal
slurred speech
small-bowel bypass
somnolence
spasticity
speech, loss of
speech, pressured
speech, slowed
spinal cord
spinal cord, infarction of
spinal cord, lesion of
splenomegaly
spontaneous remission
status epilepticus
stimulant drugs
stool, guaiac positive
striatonigral degeneration
striatonigral degeneration, infantile
striatum, lesion of
strokelike episodes
stuporous
substantia nigra
sudden death
suicide
sweating
symmetric brain lesions
sympathomimetic drugs
systemic illness
tachycardia
tachypnea
tangential
temporal lobe, lesion
tetany
thalamus, lesion of
thalamus, lesion of-bilateral
thiamine
thiamine deficiency
thrombocytopenia
thrombophlebitis
thrombotic microangiopathy
thyroxine, low
tinnitus
titubation
toxic encephalopathy
toxins, nervous system
transient neurologic deficit
treatment of neurologic disorder
tremor
tremor, intention
tremulousness
Trousseau's syndrome
uncal herniation
undiagnosed
upgaze, paralysis of
urea-cycle enzymopathies
uremia
uremic encephalopathy
urinalysis, abnormal
urine sediment
urine test for metabolic disorders
urine test in toxic screen
vecuronium
vegetarianism
venous thrombosis, non-cerebral
vibratory sensation, abnormal
violent behavior
viral infection
viral infection, CNS
vision, failure of in childhood
visual acuity, decreased
visual loss
visual loss, progressive
visual loss, slow
vitamin deficiency
walking, difficulty with
weakness
weakness, fluctuating
weakness, generalized
weakness, progressive
weakness, proximal
weight loss
Wernicke's encephalopathy
white matter disease
white matter disease, subcortical
workup
x-linked mental retardation
Showing articles 50 to 74 of 74 << Previous

Ophthalmologic Manifestations in MELAS Syndrome
Arch Neurol 50:977-980, Fang,W.,et al, 1993

Clinicopath Conf, Herpes Simplex Encephalitis
Am J Med 93:327-334, Krogstad,D., 1992

Clinicopath Conf
Infantile Striatonigral Regeneration, with Cerebellar Degeneration, Familial, Case 30-1992, NEJM 327, 261-1992., 1992

Persistent Paralysis in Critically Ill Patients after Long-Term Administration of Vecuronium
NEJM 327:524-528, Segredo,V.,et al, 1992

Reversal of Prolonged Isoniazid-Induced Coma by Pyridoxine
Arch Int Med 150:1751-1753, Brent,J.,et al, 1990

Kearns-Sayre Syndrome Presenting as Renal Tubular Acidosis
Neurol 40:1761-1763, Eviatar,L.,et al, 1990

Hemorrhagic Shock and Encephalopathy:Clinical, Pathologic, and Biochemical Features
J Pediatr 114:194-203, Levin,M.,et al, 1989

Acute Profound Dystonia in Infants with Glutaric Acidemia
Pediatrics 83:228-234, Bergman,I.,et al, 1989

Mitochondrial Encephalomyopathy with Associated Aminoacidopathy in a Male Sibship
J Pediatr 115:81-88, Sooth,F.A.,et al, 1989

Perinatal Brain Damage:Predictive Value of Metabolic Acidosis & The Apgar Score
BMJ 297:24-27, Ruth,V.J.&Raivio,K.O., 1988

Acute Extrapyramidal Syndrome in Methylmalonic Acidemia:"Metabolic Stroke"Involving the Globus Pallidus
J Pediatr 113:1022-1027, Heidenreich,R.,et al, 1988

MELAS Syndrome Involving a Mother & Two Children
Arch Neurol 44:971-973, Driscoll,P.F.,et al, 1987

Bilateral Lucency of the Globus Pallidus Complicating Methylmalonic Acidemia
Ann Neurol 20:364-366, Korf,B.,et al, 1986

Carbonic Anhydrase II Deficiency in 12 Families with Osteopetrosis with Renal Tubular Acidosis & Cerebral Calcification
NEJM 313:139-181, Sly,W.S.,et al, 1985

Biotinidase Deficiency:Initial Clinical Features & Rapid Diagnosis
Ann Neurol 18:614-617, Wolf,B.,et al, 1985

D-Lactate Encephalopathy
Am J Med 79:717-721, Thurn,J.R.,et al, 1985

Mitochondrial Myopathy, Encephalopathy, Lactic Acidosis, & Strokelike Episodes:A Distinctive Clinical Syndrome
Ann Neurol 16:481-488, Pavlakis,S.G.,et al, 1984

Mitochondrial Encephalomyopathy:Fluctuating Symptoms & CT
Neurol 34:1456-1460, Yamamoto,T.,et al, 1984

Cerebellar Hemorrhage Complication Methylmalonic & Propionic Acidemia
Arch Neurol 41:1293-1296, Dave,P.,et al, 1984

Ultrastructural, Neurological, & Glycosaminoglycan Abnormalities in Lowe's Syndrome
Ann Neurol 16:40-49, Wisniewski,K.E.,et al, 1984

Acute Cocaine Poisoning
Am J Med 75:1061-1064, Jonsson,S.,et al, 1983

Biotin-Responsive Carboxylase Deficiency Associated With Subnormal Plasma & Urinary Biotin
NEJM 304:817-820, Thoene,J.,et al, 1981

Osteopetrosis, Renal Tubular Acidosis & Basal Ganglia Calcification in Three Sisters
Am J Med 69:64-74, Whythe,M.P.,et al, 1980

Lactic Acidemia, Mitochondrial Myopathy, & Basal Ganglia Calcification
Neurol 29:1057-1061, Markesbery,Wm.R., 1979

Effects of Acetazolamide on Myotonia
Ann Neurol 3:531, Griggs,R.C.,et al, 1978



Showing articles 50 to 74 of 74 << Previous