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Differential
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areflexia
calf hypertrophy
creatine phosphokinase(CPK)elevated
diaphragmatic paralysis
distal muscle weakness
dyspnea
electromyogram
familial
gait disorder
gene mutation
hemidiaphragm, paralysis of
hereditary myopathy with early respiratory failure
inability to sit up
muscle weakness
myopathy
myopathy, hereditary
orthopnea
respiratory failure
steppage gait
titinopathy
vital capacity
weakness
weakness, progressive
Showing articles 650 to 700 of 4613 << Previous Next >>

Practical Problems in the Respiratory Care of Patients with Muscular Dystrophy
NEJM 316:1197-1205, Smith,P.E.M.,et al, 1987

Cardiorespiratory Arrest & Autonomic Neuropathy in AIDS
Lancet 2:16-18, Craddock,C.,et al, 1987

Aneurysmal Subarachnoid Hemorrhage Presenting as Cardiorespiratory Arrest
Arch Int Med 147:1661-1662, Tabbaa,M.A.,et al, 1987

Clinical Assessment of 31 Patients with Wilson's Disease, Correlations with Struct. Changes on MRI
Arch Neurol 44:365-370, Starosta-Rubinstein,S.,et al, 1987

Post-Traumatic Central Sleep Apnea in a Child
J Pediatr 110:906-909, Quera-Salva,M.A.&Guilleminault,C., 1987

Life Spans of Duchenne Muscular Dystrophy Patients in the Hospital Care Program in Japan
J Neurol Sci 81:155-158, Mukoyama,M.,et al, 1987

Fatal Familial Insomnia & Dysautonomia with Selective Degeneration of Thalamic Nuclei
NEJM 315:997-1003, Lugaresi,E.,et al, 1986

Positive Response to Edrophonium in Patients with Neurotoxic Envenoming by Cobras (NAJA NAJA PHILIPPINENIS)
NEJM 315:1444-1448, Watt,G.,et al, 1986

Adult-Onset Autosomal Dominant Limb-Girdle Muscular Dystrophy
Ann Neurol 20:240-248, Chutkow,J.G.,et al, 1986

Progressive Myoclonus Epilepsies:Specific Causes & Diagnosis
NEJM 315:296-305, Berkovic,S.F.,et al, 1986

Preventive Screening for Fragile X Syndrome
Editorial, Lancet 2:1191-11921986., , 1986

Cogan's Syndrome:18 Cases & a Review of the Literature
Mayo Clin Proc 61:344-361, Vollertsen,R.S.,et al, 1986

Hyponatremia, Convulsions, Respiratory Arrest, & Perm Brain Damage After Elective Surgery in Healthy Women
Ann Neurol 314:1529-1535, 1573-15751986., Arieff,A.I., 1986

Clinicopath. Conference
Acquired Immunodeficiency Syndrome, Rhabdomyosarcoma, with Extensive Metastases, Case 9-1986, NEJM 3, 4:620,1986., 1986

The Neurologic Manifestations of Fat Embolism
Neurol 36:847-851, Jacobson,D.M.,et al, 1986

Neurological Manifestations in Xeroderma Pigmentosum
Ann Neurol 20:70-75, Mimaki,T.,et al, 1986

Successful Treatment with Tocainide of Recessive Generalized Congenital Myotonia
Ann Neurol 19:501-504, Streib,E.W., 1986

Apnea Testing in Brain Death
Arch Int Med 146:2385-2388, Belsh,J.M.,et al, 1986

Facioscapulohumeral Dystrophy, in Myology, Basic & Clinical
McGraw-Hill Book Co, NY, p1251986., Munsat,T.L., 1986

Guillain-Barre Syndrome:Management of Respiratory Failure
Neurol 35:1662-1665, Ropper,A.H.&Kehne,S.M., 1985

Improved Neurologic Function After Long-Term Correction of Vitamin E Deficiency in Children with Chronic Cholestasis
NEJM 313:1580-1586, Sokol,R.J.,et al, 1985

Inflammatory Myopathies
Ann Neurol 17:215-227, 317-3231985., Mastaglia,F.L.,et al, 1985

Mitochondrial Myopathies
Ann Neurol 17:521-538, DiMauro,S.,et al, 1985

Neurological Findings in Patients with the Fragile-X Syndrome
JNNP 48:150-153, Finelli,P.F.,et al, 1985

Amyotrophic Lateral Sclerosis:Part 1. Clinical Features, Pathology, & Ethical Issues in Management
Ann Neurol 18:271-280, Tandan,R.,et al, 1985

Carbonic Anhydrase II Deficiency in 12 Families with Osteopetrosis with Renal Tubular Acidosis & Cerebral Calcification
NEJM 313:139-181, Sly,W.S.,et al, 1985

Atypical Alzheimer's Disease with Spastic Paresis & Ataxia
Ann Neurol 17:297-300, Aikawa,H.,et al, 1985

Autosomal Recessive Distal Muscular Dystrophy:A Comparative Study with Distal Myopathy with Rimmed Vacuole Formation
Ann Neurol 17:51-59, Nonaka,I.,et al, 1985

Clin. Path. Conference
Coproporphyria with Polyneuropathy, Case Record 39-1984, NEJM 311:839-847984., , 1984

Is Hypokalemia the Cause of Paralysis in Barium Poisoning
BMJ 289:882, Smith,R.P.,et al, 1984

Mitochondrial Myopathy, Encephalopathy, Lactic Acidosis, & Strokelike Episodes:A Distinctive Clinical Syndrome
Ann Neurol 16:481-488, Pavlakis,S.G.,et al, 1984

Ultrastructural, Neurological, & Glycosaminoglycan Abnormalities in Lowe's Syndrome
Ann Neurol 16:40-49, Wisniewski,K.E.,et al, 1984

Respiratory Arrest in Subarachnoid Hemorrhage
Neurol 34:1501-1503, Hijdra,A.,et al, 1984

Autonomic Dysfunction & Sleep Apnea in Olivoponto Cerebellar Degeneration
Arch Neurol 41:926-931, Chokroverty,S.,et al, 1984

Ventilatory Support by Pacing of the Conditioned Diaphragm in Quadriplegia
NEJM 310:1150-1155, Glenn,W.W.L.,et al, 1984

Bilateral Diaphragmatic Paralysis Complicating Local Cardiac Hypothermia During Open Heart Surgery
Am J Med 77:243-249, Chandler,K.W.,et al, 1984

Acute Ventilatory Failure & Myoglobinuria
Neurol 34:369-371, Taverner,D.,et al, 1984

Nemaline Myopathy Appearing in Adults as Cardio-myopathy
Arch Neurol 41:443-445, Meier,C.,et al, 1984

Respiratory Failure in Myasthenia Gravis Due to Vocal Cord Paresis
Arch Neurol 41:567-568, Schmidt-Nowara,W.W.,et al, 1984

Clinicopathological Conference
Case 2-1984, Fabry's Disease, NEJM 310:106-114984., , 1984

Neurologic Outcome in Children with Inborn Errors of Urea Synthesis
NEJM 310:1500-1505, Msall,M.,et al, 1984

Leber's Congenital Amaurosis
Arch Neurol 41:204-206, Weinstein,J.M.,et al, 1984

Clinicopathological Conference
Maroteaux-Lamy Syndrome, Case 44-1983, NEJM 309:1109-1117983., , 1983

Mechanical Ventilation for Respiratory Failure in Myasthenia Gravis
Mayo Clin Proc 58:597-602, Gracey,D.R.,et al, 1983

Recognising & Preventing Duchenne Muscular Dystrophy
BMJ 287:1083-1084, Firth,M.A.,et al, 1983

Neuropathologic Evaluation of 40 Confirmed Cases of Legionella Pneumonia
Neurol 33:1340-1344, Pendlebury,W.W.,et al, 1983

Ataxia-Telangiectasia:A Multisystem Hereditary Disease with Immunodeficiency
Ann Int Med 99:367-379, Waldmann,T.A.,et al, 1983

Idiopathic Hemochromatosis (IHC) :Dementia & Ataxia as Presenting Signs
Neurol 33:1479-1483, Royden,H.,et al, 1983

Myositis of Chronic Graft Versus Host Disease
Neurol 33:1222-1224, Reyes,M.G.,et al, 1983

Acute Respiratory Failure in Motor Neuron Disease
Arch Neurol 40:30-32, Hill,R.,et al, 1983



Showing articles 650 to 700 of 4613 << Previous Next >>