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Differential
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absence
acrocyanosis
agitation
Aicardi-Goutieres syndrome
akathisia
alcohol
alcohol intolerance
alcohol, neurologic complications with
Alexanders disease
Alexanders disease, adult onset
alternating rapid movement
alternating rapid movement, impaired
Alzheimer's disease
Alzheimer's disease, early onset
Alzheimer's disease, familial
amyloid angiopathy, cerebral
animal exposure
anticonvulsants
anticonvulsants, discontinuation in seizure-free epileptics
anticonvulsants, effectiveness
anticonvulsants, selection of
anxiety
aphasia
aphasia, progressive
apolipoprotein E
APP gene
apraxia
areflexia
arm weakness
asymptomatic
ataxia
ataxia, cerebellar
ataxia, hereditary
ataxia, progressive
ataxia, truncal
ataxic gait
atypical
autonomic dysfunction
axonal spheroid
Babinski sign
basal ganglia, calcification of
basal ganglia, degeneration
basal ganglia, lesion of
basal ganglia, lesion, bilateral
behavioral disorder
benign essential tremor
beta adrenergic blocker
biologic markers
blindness
bone pain
bovine spongiform encephalopathy
brain atrophy
brain biopsy
brainstem, atrophy
brainstem, lesion of
CAG repeats
calcification, intracranial
CAT scan
CAT scan, abnormal
CAT scan, false negative
cerebellar ataxia, children
cerebellar atrophy, primary
cerebellar degeneration
cerebellar lesion
cerebellar plaques, amyloid
cerebral cortex
cerebral cortical atrophy
cerebral vasculature
cerebrospinal fluid, abnormal
cerebrospinal fluid, lactic acid concentration
cerebrospinal fluid, protein of
cerebrovascular accident
cerebrovascular accident, multiple
cerebrovascular accident, young adult
ceruloplasmin, serum
cherry red spot
cherry red spot-myoclonus syndrome
chewing movements
chilbran skin lesions
children
choking
chorea
chorea, familial
chorea, treatment of
choreoathetosis
choreoathetosis, paroxysmal
chromosomal abnormality
chromosome 12
chromosome 2
chromosome 7
chromosome 8
chronic progressive external ophthalmoplegia
Clinical Pathologic Conference(C.P.C.)
clonazepam
clonus
cognition
cognition, slowed
cogwheel rigidty
color vision, impaired
coma
confabulation
consanguinity
copper metabolism, abnormal
Creutzfeldt-Jakob disease, genetic
crying, pathologic
deafness
degenerative diseases of CNS
delay in diagnosis
dementia
dementia, differential diagnosis of
dementia, familial
dementia, presenile
dementia, rapidly progressive
dementia, thalamic
dementia, transmissible
dentate nuclei, lesion of
dentatorubral-pallidoluysian atrophy
depression
developmental milestones
developmental milestones, loss of
developmental retardation
diabetes insipidus
diabetes mellitus
diagnostic criteria
differential diagnosis
difficulty climbing stairs
diplopia
disability, neurological
distal muscle atrophy
distal muscle weakness
dizziness
Dravet syndrome
drooling
dropped head syndrome
dysarthria
dysdiadochokinesia
dysmetria
dysphagia
dyssynergia cerebellaris myoclonica
dystonia
dystonia, children
dystonia, face
dystonia, treatment of
electroencephalogram
electroencephalogram, abnormalities of
electroencephalogram, periodic complexes
electroencephalogram, video monitoring with
encephalopathy
encephalopathy, neonatal
encephalopathy, progressive
enzyme, defect
epidemiology of neurology
epileptic encephalopathy
epsilon sarcoglycan gene
eye movement, disorders of
failure to thrive
falling
familial
familial adult myoclonic epilepsy
fasciculation
fatal familial insomnia
fatigue
feeding disorder
fever
finger nose finger test
fingerprint bodies
fundus, abnormality of
gait disorder
gangliosidosis GM2
Gaucher's disease
Gaucher's disease, adult onset
gaze palsy, supranuclear
gene
gene mutation
genetic counselling
genetic diagnosis, prenatal
genetic linkage
genetic neurologic disorders
genetic testing
globus pallidus, lesion of
granular osmiphilic material
growth hormone
growth retardation
Hallervorden Spatz disease
hallucination
hallucination, visual
handwriting
head lag
head nodding
headache
hearing loss
heel-knee-shin test
hepatic failure
hepatolenticular degeneration(Wilson's disease)
hepatomegaly
hepatosplenomegaly
heralding manifestation
hexosaminidase-A
HLA
hyperekplexia
hyperhidrosis
hyperpyrexia, CNS disorder causing
hyperreflexia
hypertension
hyperthermia
hypertonia
hypertonia, congential
hypomyelination
hypothermia
hypotonia
iatrogenic neurologic disorders
imbalance
inattention
inborn errors of metabolism
inclusion bodies
inclusion bodies, eosinophilic cytoplasmic
inclusion bodies, intracytopasmic
insight, loss
insomnia
intellectual deficit
intellectual deterioration
interferon alpha
intrauterine
irritability
Jakob-Creutzfeldt disease
Jakob-Creutzfeldt disease, cerebellar variant
Jakob-Creutzfeldt disease, variant
Jewish
juvenile myoclonus epilepsy
Kayser-Fleischer ring
lactic acidemia
Lafora body
Lafora's disease
Leigh's disease
Leigh's disease, adult variety
lethargy
leukodystrophy
leukoencephalopathy
leukoencephalopathy, differential diagnosis
life expectancy
linear lesion
lipid storage disorder of CNS
liver biopsy
liver disease
lysosomal storage disease
macular degeneration
MELAS syndrome
memory, defect of recent
memory, impairment of
mental retardation
MERRF syndrome
microcephaly
mimics
misdiagnosis
mitochondrial disease
mitochondrial encephalomyopathy
molecular genetics
monoparesis
mortality
motor cortex
movement disorder
movement disorder, paroxysmal
movement disorder, treatment of
MRI
MRI, abnormal
MRI, diffusion weighted
MRI, FLAIR
MRI, hypointense signal foci on
MRI, punctate pattern
MRI, susceptibility weighted
multiple sclerosis, misdiagnosis
muscle biopsy
muscle spasm
muscle stiffness
muscle weakness
muscle weakness, proximal
mutism
myasthenia gravis, differential diagnosis
myasthenia gravis, misdiagnosis of
myelination of nervous system
myoclonic dystonia
myoclonic jerks
myoclonus
myoclonus, action
myoclonus, cortical
myoclonus, epilepsy
myoclonus, essential
myoclonus, sleep
myoclonus, stimulus sensitive
myopathy, mitochondrial
mysoline
negative
neuraminidase deficiency
neuroaxonal dystrophy
neuroaxonal dystrophy, infantile
neuroaxonal dystrophy, juvenile
neuroendocrinology
neurologic disease, diagnoses of
neurologic signs
neuronal ceroid-lipofuscinosis
neuroophthalmology
neuropathology
neuropathology, brain
neuropathy
neuropathy, peripheral
neuropsychiatry
next-generation sequencing
normal
nystagmus
nystagmus, rotary
ophthalmoplegia
optic atrophy
optic atrophy, hereditary
palatal myoclonus
paraparesis
paraparesis, spastic
paratonia
Parkinson disease
Parkinsonism syndrome
paroxysmal dystonic choreoathetosis
paroxysmal kinesigenic dyskinesia
paroxysmal neurologic deficits
PAS positive
PAS positive material in the brain
pediatric neurology
penicillamine
pituitary, hormones of
pleocytosis of cerebrospinal fluid
polymerase chain reaction
polyneuropathy
pontocerebellar atrophy
prenatal
prion disease
prognosis
progressive myoclonic epilepsy
progressive neurologic disorder
progressive pallidum atrophy
propranolol
protein 14-3-3, cerebrospinal fluid
psychiatric problems in neurologic disorders
psychomotor retardation
psychosis
ptosis
Purkinje cell
pyramidal tract dysfunction
pyruvate metabolism, abnormality of
quadriparesis
ragged-red fibers
rapidly progressing neurologic illness
real-time quaking-induced conversion
respiratory failure
retinal degeneration
review article
rigidity
Romberg's sign
Rosenthal fibers
SCN1A gene
screening
seizure
seizure, children
seizure, diagnosis of
seizure, drug resistance
seizure, familial
seizure, febrile
seizure, intractable
seizure, neonatal
seizure, paradoxical
seizure, photosensitive
seizure, prognosis in adults
seizure, stimulus sensitive
seizure, teenager
seizure, tonic-clonic
seizure, treatment of
sensorineural hearing loss
short stature
skin, biopsy
skin, lesions in neurologic disorders
sleep pathology and physiology
sodium channel dysfunction
sodium valproate
spastic dysphonia
spasticity
speech disorder
speech disorder, childhood
speech, loss of
sphingolipodoses
spinocerebellar ataxia
spinocerebellar ataxia type 1
spinocerebellar ataxia type 16
spinocerebellar ataxia type 7
spinopontine atrophy, dominant
spongy degeneration of brain
startle myoclonus
startle reaction
status epilepticus
stereotypy
storage disease of CNS
striatonigral degeneration
striatonigral degeneration, infantile
strokelike episodes
stuporous
stuttering
systemic illness
tachycardia
tandem gait, ataxic
Tay-Sachs disease
thalamus, atrophy of
thalamus, lesion of
thalamus, lesion of-bilateral
titubation
tone, muscle, increased
topiramate
treatment of neurologic disorder
tremor
tremor, intention
tremor, jaw
tremor, leg
tremor, treatment of
trichopoliodystrophy
trinucleotide repeats
Unverricht-Lundborg disease
upgaze, paralysis of
visual acuity, decreased
visual loss
walking frame
walking, difficulty with
weakness
weakness, acute
weakness, focal
weight loss
wheelchair
white matter disease
wide based gait
Wolfram syndrome
workup
Showing articles 300 to 350 of 1998 << Previous Next >>

Degenerative Diseases of the Nervous System, Hereditary Spastic Paraplagia
Adams & Victors Principles of Neurology, Chp 39, pg 1119, Ropper, A.H.,et al, 2014

Sturge-Weber Syndrome
UptoDate , Nov, Bodensteiner, J.B., 2014

Clinical Manifestations and Diagnosis of Bicuspid Aortic Valve in Adults
UpToDate Nov, Braverman, D.C., 2014

Inherited Metabolic Diseases of the Nervous System, Infantile Gaucher Disease
Adams & Victors Principles of Neurology, Chp 37, pg 958, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Infantile Niemann-Pick Disease
Adams & Victors Principles of Neurology, Chp 37, pg 958, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Globoid Cell Leukodystrophy (Krabbe Disease, Galactocerebrosidase)
Adams & Victors Principles of Neurology, Chp 37, pg 959, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Lipogranulomatosis (Farber Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 960, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Metachromatic Leukodystrophy
Adams & Victors Principles of Neurology, Chp 37, pg 971, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Neuroaxonal Dystrophy
Adams & Victors Principles of Neurology, Chp 37, pg 972, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Neuronal Ceroid Lipofuscinosis (Batten Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 973, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Hepatolenticular Degeneration (Wilson Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 982, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Adrenoleukodystrophy
Adams & Victors Principles of Neurology, Chp 37, pg 988, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Fabry Disease
Adams & Victors Principles of Neurology, Chp 37, pg 991, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Subacute Necrotizing Encephalopathy (Leigh Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 996, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Alzheimer Disease
Adams & Victors Principles of Neurology, Chp 39, pg 1063, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Familial Dementia with Spastic Paraparesis
Adams & Victors Principles of Neurology, Chp 39, pg 1081, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Parkinson Disease
Adams & Victors Principles of Neurology, Chp 39, pg 1082, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Friedreich Ataxia
Adams & Victors Principles of Neurology, Chp 39, pg 1102, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Cerebellar Degeneration
Adams & Victors Principles of Neurology, Chp 39, pg 1105, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Olivopontocerebellar Atrophy
Adams & Victors Principles of Neurology, Chp 39, pg 1106, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Machado-Joseph-Azorean Disease
Adams & Victors Principles of Neurology, Chp 39, pg 1107, Ropper, A.H.,et al, 2014

Degenerative Diseases of the Nervous System, Amyotrophic Lateral Sclerosis
Adams & Victors Principles of Neurology, Chp 39, pg 1109, Ropper, A.H.,et al, 2014

Imaging Findings in MR Imaging-Guided Focused Ultrasound Treatment for Patients with Essential Tremor
AJNR 35:891-896, Wintermark, M.,et al, 2014

Brugada Syndrome in Spinal and Bulbar Muscular Atrophy
Neurol 82:1813-1821, Araki, A.,et al, 2014

A 72-year-old Man with Rapid Cognitive Decline and Unilateral Muscle Jerks
Neurol 82:e194-e197, Duncan, M.,et al, 2014

Familial Risk of Cerebral Palsy: Population Based Cohort Study
BMJ 349:g4294, g4514, Tollanes, M.C.,et al, 2014

Red Papules on the Tongue of a Patient with Hemiparesis
JAMA 312:741-742, Chiu, H.Y. & Lin, S.J., 2014

Somatic Mutations in Cerebral Cortical Malformations
NEJM 371:733-743, Jamuar, S.S.,et al, 2014

A 52-year-old Woman with Progressive Proximal Weakness
Neurol 83:e106-e109, Enduri, S.,et al, 2014

Cerebral Abnormalities in Adults with Ataxia-Telangiectasia
AJNR 35:119-123, Lin, D.D.M.,et al, 2014

Chronic and Slowly Progressive Weakness of the Legs and Hands
BMJ 348:g459, Nightingale, H.,et al, 2014

Neuronal Intranuclear Inclusion Disease Cases with Leukoencephalopathy Diagnosed via Skin Biopsy
JNNP 85:354-356, Sone, J.,et al, 2014

Serotonin Syndrome
BMJ 348:g1626, Buckley, N.A.,et al, 2014

Enterovirus Vaccines for an Emerging Cause of Brain-Stem Encephalitis
NEJM 370:792-794, McMinn, P.C., 2014

Tremor
JAMA 311:948-954, Elias, W.J. & Shah, B.B., 2014

Early-Onset Stroke and Vasculopathy Associated with Mutations in ADA2
NEJM 370:911-920, Zhou, Q.,et al, 2014

Autism
Lancet 383:896-910, Lai, M.C.,et al, 2014

Parkinson Disease Subtypes
JAMA 71:499-504, Thenganatt, M. & Jankovic, J., 2014

A Case of Slowly Progressive Painful Paraparesis
Neurol 82:1476-1479, Corbetto, M.,et al, 2014

Mycoplasma Pneumoniae Infection: Neurologic Complications
www.MedLink.com, Oct, Greenlee, J.E., 2013

Chediak-Higashi Syndrome: Pathognomonic Feature
Lancet 382:1514, Antunes, H.,et al, 2013

Extending the KCNQ2 encephalopathy Spectrum
Neurol 81:1697-1703, Weckhuysen, S.,et al, 2013

Subacute Sclerosing Panencephalitis
www.MedLink.com, February, Auwaeter,P.G.&Johnson,R.T., 2013

Clinical Reasoning: A Woman with Rapidly Progressive Apraxia
Neurol 80:e162-e165, Pressman, P.,et al, 2013

Longitudinally Extensive Transverse Myelitis in Neuro-Beh�et Disease
Neurol 80:e189-e190, Graham, D.,et al, 2013

Clinicopathologic Conference, West Nile Virus Infection, Case 15-2013
NEJM 368:1919-1927, Vyas, J.,et al, 2013

Efficacy and Safety of Everolimus for Subependymal Giant Cell Astrocytomas Associated with Tuberous Sclerosis Complex (EXIST-1): A Multicenter, Randomized, Placebo-Controlled Phase 3 Trial
Lancet 381:125-132, Franz, D.,et al, 2013

The Eye of the Beholder: Inter-rater Agreement among Experts on Psychogenic Jerky Movement Disorders
JNNP 84:742-747, Van de Salm, S.,et al, 2013

A Pilot Study of Focused Ultrasound Thalamotomy for Essential Tremor
NEJM 369:640-648, Elias, W.J.,et al, 2013

Sturge-Weber Syndrome
MedLink Neurology, July, Comi, A.M., 2013



Showing articles 300 to 350 of 1998 << Previous Next >>