Clinicopath Conf
Progressive Muscular Atrophy, Case 36-1995, NEJM 333:1406-1412995., , 1995
Neurodegeneration and Diabetes:UK Nationwide Study of Wolfram (DIDMOAD) Syndrome
Lancet 1458-1463, Barrett,T.G.,et al, 1995
The Electrophysiological Study of Diff Dx Between ALS & Cervical Spondylotic Myelopathy
EMG & Clin Neurophysiology 35:231-238995., Kang,D.X.&Fan,D.S., 1995
Growth Factors:Potential Therapeutic Applications in Neurology
JNNP 54:1445-1450, Drago,J.,et al, 1994
Becker Muscular Dystrophy with Onset after 60 Years
Neurol 44:2388-2390, Heald,A.,et al, 1994
Detection of Cortical Neuron Loss in Motor Neuron Disease by Proton Magnetic Resonance Spectroscopic Imaging in Vivo
Neurol 44:1933-1938, Pioro,E.P.,et al, 1994
Superoxide Dismutase and ALS
Lancet 344:1651-1652, Orrell,R.W.&deBelleroche,J.S., 1994
Monomelic Amyotrophy
Muscle & Nerve 17:1129-1134994., Donofrio,P.D., 1994
Trinucleotide Repeat Expansion in Neurological Disease
Ann Neurol 36:814-822, LaSpada,A.R.,et al, 1994
Clinical Significance of Hypointensity in the Motor Cortex on T2-Weighted Images
Neurol 44:1181, Iwasaki,Y.,et al, 1994
Posterior Cortical Atrophy:Neuropathologic Correlations
Arch Neurol 51:269-274, Victoroff,J.,et al, 1994
Cerebral Involvement in McLeod Syndrome
Neurol 44:117-120, Danek,A.,et al, 1994
Clinical Genetics in Neurological Disease
JNNP 57:7-15, MacMillan,J.C.&Harper,P.S., 1994
A Controlled Trial of Riluzole in Amyotrophic Lateral Sclerosis
NEJM 330:585-591, Bensimon,G.,et al, 1994
Conjugal Amyotrophic Lateral Sclerosis:A Report on Two Couples from Southern France
Neurol 44:547-548, Camu,W.,et al, 1994
Amyotrophic Lateral Sclerosis Patient Antibodies Label CA2+Channel a1 Subunit
Ann Neurol 35:164-171, 1311994., Fumiharu,K.,et al, 1994
Distal Vacuolar Myopathy in Nephropathic Cystinosis
Ann Neurol 35:181-188, Charnas,L.R.,et al, 1994
Bilateral Distal Upper Limb Amyotrophy and Watershed Infarcts from Vertebral Dissection
Stroke 25:1870-1872, Pullicino,P., 1994
Intestinal Pseudo-Obstruction in Adult Spinal Muscular Atrophy
Muscle & Nerve 17:946-948994., Ionasescu,V.,et al, 1994
Location of the Corticospinal Tract in the Internal Capsule at MR Imaging
Radiology 191:455-460, Yagishita,A.,et al, 1994
Motor Neuron Disease
JNNP 57:886-896, Leigh,P.N.&Ray-Chaudhuri,K., 1994
Recent Developments in the Drug Treatment of Motor Neurone Disease
BMJ 309:140-141, , 1994
Sequences Specific for Enterovirus Detected in Spinal Cord from Patients with Motor Neurone Disease
BMJ 308:1541-1543, Woodall,C.J.,et al, 1994
Phenotype of Chromosome 14-Linked Familial Alzheimer's Disease in a Large Kindred
Ann Neurol 36:368-378, Lampe,T.H.,et al, 1994
Myotonic Dystrophy
In Myology, Engel & Franzini-Armstrong, McGraw-Hill, Inc, New York V2, Ch 43, P1192, Harper,P.S.&Rudel,R., 1994
Clinicopath Conf
Acquired Demyelinating Neuropathy, ? CIDP, ? Motor Neuropathy with Multifocal Conduction Blocks, Cas, 41-1EJM 329:1182-1190,1993., 1993
Inherited Primary Peripheral Neuropathies
JAMA 270:2326, 23301993., Lupski,J.R.,et al, 1993
Conjugal Amyotrophic Lateral Sclerosis:Report of a Young Married Couple
Neurol 43:2378-2380, Cornblath,D.R.,et al, 1993
Amyotrophic Lateral Sclerosis:T2 Shortening in Motor Cortex at MR Imaging
Radiology 189:843-846, Oba,H.,et al, 1993
Evidence for a Dopaminergic Deficit in Sporadic Amyoptrophic Lateral Sclerosis on Positron Emission Scanning
Lancet 324:1016-1018, Takahashi,H.,et al, 1993
Signs and Symptoms of Reflex Sympathetic Dystrophy:Prospective Study of 829 Patients
Lancet 342:1012-1016, Veldman,P.H.J.M.,et al, 1993
Molecular Genetics in Neurology
Ann Neurol 34:757-773, Martin,J.B., 1993
Clinicopath Conf
Spongiform Encephalopathy (Creutzfeldt-Jakob Disease) , with Amyloid (KURU) Plaques, Case 17-1993, N, JM 328:66,1993., 1993
Neuropathic Findings in Oculopharyngeal Muscular Dystrophy, Seven Cases & Review of Literature
Arch Neurol 50:481-488, Hardiman,O.,et al, 1993
Tibial Muscular Dystrophy
Arch Neurol 50:604-608, Udd,B.,et al, 1993
Single-Photon Emission Computed Tomographic Investigation of Patients with Motor Neuron Disease
Neurol 43:1569-1573, Abe,K.,et al, 1993
Spinal Fluid Cells and Protein in Amyotrophic Lateral Sclerosis
Arch Neurol 50:489-491, Norris,F.H.,et al, 1993
The Natural History of Amyotrophic Lateral Sclerosis
Neurol 43:1316-1322, Ringel,S.P.,et al, 1993
Hereditary Motor-Sensory Neuropathy (Charcot-Marie-Tooth Disease) with Nerve Deafness:A New Variant
J Pediatr 123:431-434, Hamiel,O.P.,et al, 1993
Charcot-Marie-Tooth Disease Type 1A:Association with a Spontaneous Point Mutation in the PMP22 Gene
NEJM 329:96-101, Roa,B.B.,et al, 1993
Magnetic Resonance Imaging of Brain and the Neuromotor Disorder in Endemic Cretinism
Ann Neurol 34:91-94, Ma,T.,et al, 1993
Discrete Cortical Infarction with Prominent Impairment of Thumb Flexion
Stroke 24:2118-2120, Terao,Y.,et al, 1993
Competent Pts with Adv States of Perm Paralysis Have the Right to Forgo Life-Sustaining Therapy
Neurol 43:224-225, Bernat,J.L.,et al, 1993
Intramedullary Spinal Sarcoidosis:Clinical and Magnetic Resonance Imaging Characteristics
Neurol 43:333-337, Junger,s.S.,et al, 1993
Fatal Rabies Associated with Extensive Demyelination
Arch Neurol 50:317-323, Nelson,D.A.&Berry,R.G., 1993
Cell Culture Evidence for Neuronal Degeneration in ALS to Glutamate AMPA/Kainate Receptors
Lancet 341:265-268, Couratier,P.,et al, 1993
Home Ventilation for ALS Patients:Outcomes, Costs, and Patient, Family and Physician Attitudes
Neurol 43:438-443, Moss,A.H.,et al, 1993
Motor Neuron Diseases and Amyotrophic Lateral Sclerosis:GM1 Antibodies and Paraproteinemia
Neurol 43:418-420, Sanders,K.A.,et al, 1993
Signal Loss in the Motor Cortex on Magnetic Resonance Images in Amyotrophic Lateral Sclerosis
Ann Neurol 33:218-222, Ishikawa,K.,et al, 1993
Amyotrophic Lateral Sclerosis:Hyperintensity of the Corticospinal Tracts on MR of Spinal Cord
AJR 160:604-606, Friedman,D.P.&Tartaglino,L.M., 1993