Neudle.com: prion dementia

Differential
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abscess, intracerebral

acquired immunodeficiency syndrome

addiction, heroin

addiction, heroin-neurologic complications with

adenine arabinoside

adrenoleukodystrophy

advances in neurology

adverse drug reaction

Alice in Wonderland syndrome

alien hand syndrome

alternating rapid movement, impaired

Alzheimer's disease

Alzheimer's disease, familial

Alzheimer's disease, rapidly progressive

Alzheimer's disease, rate of clinical decline

Alzheimer's disease, visual variant

amantadine

aminoacidurias

ammonia

AMPA receptor antibodies

amyloid

amyloid angiopathy, cerebral

amyloid beta protein

amyloid plaques

amyotrophic lateral sclerosis

amyotrophic lateral sclerosis, childhood

amyotrophic lateral sclerosis, familial

amyotrophic lateral sclerosis, guamian type of

amyotrophic lateral sclerosis, Parkinson-dementia-complex

amyotrophic lateral sclerosis, post-encephalitic

anatomy of

aneuploidy

angiitis, isolated of CNS

anticonvulsants, untoward effects of

antithyroid antibodies

aphasia, progressive, primary

aphasia, transcortical

aphasia, transcortical-sensory

Arnold Chiari malformation

ataxia telangiectasia

autonomic dysfunction

basal ganglia, calcification of

basal ganglia, degeneration

basal ganglia, lesion of

basal ganglia, lesion, bilateral

basilar artery occlusion

blood dyscrasias, neurologic findings with

blood transfusion

bovine spongiform encephalopathy

brain biopsy, complications of

brain biopsy, false negative

brain biopsy, indication

brain biopsy, negative

calcification, intracranial

Canavan's disease

carbamazepine

carbamazepine, toxicity

carbon monoxide poisoning

carcinoma

carcinoma of breast

cardiac transplantation

cardiomyopathy

CAT scan

CAT scan, abnormal

CAT scan, contrast enhanced

CAT scan, demyelinating disease

CAT scan, emission

CAT scan, emission, abnormal

CAT scan, false negative

cataracts

caudate nucleus

caudate nucleus, lesion of

caudate nucleus, lesion of, bilateral

cell fusion test

central nervous system, infection of

central pontine myelinolysis

cerebellar ataxia, children

cerebellar ataxia, children, differential diagnosis of

cerebellar atrophy, primary

cerebellar atrophy, secondary

cerebellar degeneration

cerebellar lesion

cerebellar plaques, amyloid

cerebellum, disease of

cerebral autosomal dominate arteriopathy with subcortical infarction and leukoencephalopathy

cerebral cortex

cerebral cortical atrophy

cerebral glucose metabolism

cerebral infarction

cerebral venous infarction

cerebral venous thrombosis

cerebral venous thrombosis, deep

cerebrospinal fluid

cerebrospinal fluid, abnormal

cerebrospinal fluid, cell count

cerebrospinal fluid, elevated protein of

cerebrospinal fluid, enzymes in

cerebrospinal fluid, lactic acid concentration

cerebrospinal fluid, oligoclonal IgG in

cerebrospinal fluid, protein of

cerebrovascular accident

cerebrovascular accident, mimics

cerebrovascular accident, misdiagnosis

cerebrovascular accident, nonvascular territory

cerebrovascular accident, young adult

Charles Bonnet's syndrome

chemotherapy, CNS treatment and complications with

chromosomal abnormality

chromosome 20

chronic progressive external ophthalmoplegia

cingulate gyrus

Clinical Pathologic Conference(C.P.C.)

coenzyme Q10 deficiency

cognition

cognition, slowed

cogwheel rigidty

color vision, impaired

coma

comorbidities

complications

concentration, impaired

confabulation

confusion

consanguinity

contactin associated protein like 2 antibodies

controversies in neurology

corneal transplant

cortical blindness

cortical infarction

cortical-basal ganglionic degeneration

Creutzfeldt-Jakob disease, genetic

crying

cultured skin fibroblasts

cytochrome c oxidase

cytochrome c oxidase, deficiency

deafness

deafness, congenital

deep gray nuclei

degenerative diseases of CNS

dementia, diagnostic evaluation of

dementia, differential diagnosis of

dementia, familial

dementia, frontotemporal

dementia, presenile

dementia, prevention of

dementia, rapidly progressive

dementia, reversible

dementia, screening for

dementia, thalamic

dementia, transmissible

dementia, treatment of

demyelinating disease

denial of blindness(Antons syndrome)

dentate nuclei

dentate nuclei, lesion of

depression

developmental milestones

developmental milestones, loss of

developmental retardation

differential diagnosis

difficulty climbing stairs

diplopia

disorientation

dissociated sensory loss

dizziness

driving

drug abuse

drug abuse, neurologic complications of

drug induced neurologic disorders

drug withdrawal

dural graft, cadaveric

electroencephalogram, abnormalities of

electroencephalogram, complications with

electroencephalogram, depth electrode

electroencephalogram, focal delta activity

electroencephalogram, periodic complexes

electroencephalogram, triphasic delta waves

electromyogram

electron microscopy

electrophoretic pattern, CSF

electrophoretic pattern, serum

emotional lability

encephalitis

encephalitis, autoimmune

encephalitis, bornavirus

encephalitis, Japanese

encephalitis, paraneoplastic

encephalitis, viral

encephalomyelitis, postinfectious

encephalopathy

encephalopathy, carcinomatous

encephalopathy, Hashimoto's

encephalopathy, metabolic

encephalopathy, neonatal

epidemiology of neurology

epilepsia partialis continua

episodic disorders

evoked potentials

executive dysfunction

experimental allergic encephalitis

extrapyramidal

eye movement, disorders of

Fabry's disease

faciobrachial dystonic seizure

fatal familial insomnia

fatal sporadic insomnia

finger nose finger test

Fisher C.M.

flavivirus

flu-like illness

follicle stimulating hormone

fontanel, bulging

Friedreich's ataxia

frontal lobe, anatomy and physiology

frontal lobe, pathologic signs of

gadolinium

gait disorder

gait, apraxic

gamma amino butyric acid receptor antibody

gaze palsy

gaze palsy, supranuclear

genetic diagnosis, prenatal

genetic linkage

genetic neurologic disorders

genetic testing

Gerstmann syndrome

Gerstmann-Straussler-Scheinker disease

glioma

gliosis

glutaric acidemia

glycine receptor antibodies

Hallervorden Spatz disease

hallucination

hallucination, visual

hallucination, visual, benign

hemianopia, homonymous

hemiparesis

hepatolenticular degeneration(Wilson's disease)

hepatomegaly

heralding manifestation

herpes simplex encephalitis

herpes simplex virus

herpes virus infection

hiccoughs

histochemistry

histochemistry of muscle

hockey stick sign

homograft

hot cross bun sign

human immunodeficiency virus type 1

Huntington's chorea

hydrocephalus

hydrocephalus, normal pressure

hypoxic encephalopathy

iatrogenic neurologic disorders

immunosuppressive agents

inattention

inborn errors of metabolism

incidence

inclusion bodies

inclusion bodies, eosinophilic cytoplasmic

incoordination

incubation period

infant and newborn with distress, neurologic prognosis in

infant, evaluation of

insight, loss

insomnia

insular cortex

intellectual deterioration

interferon

internuclear ophthalmoplegia

internuclear ophthalmoplegia, unilateral

interobserver agreement

intestinal pseudoobstruction

intracerebral hemorrhage

intracerebral hemorrhage, multiple

intracerebral hemorrhage, recurrent

intrathecal chemotherapy

intraventricular hemorrhage

iron, brain

irritability

Jakob-Creutzfeldt disease

Jakob-Creutzfeldt disease, cerebellar variant

Jakob-Creutzfeldt disease, conjugal

Jakob-Creutzfeldt disease, Heidenhain variant

Jakob-Creutzfeldt disease, medical precaution with

Jakob-Creutzfeldt disease, unilateral

Jakob-Creutzfeldt disease, variant

Jakob-Creutzfeldt disease, young adult

jocularity

Kearns-Sayre syndrome

laminar necrosis, cortical

language disorder in adults

laughing, pathologic

lead poisoning

Leber's hereditary optic neuropathy

leg numbness

leg weakness, bilateral

Leigh's disease

Leigh's disease, adult variety

lenticular nucleus, lesion of

lenticular nucleus, lesion of, bilateral

lethargy

leucine rich glioma inactivated 1 antibodies

leukemia, neurologic findings assoc.with

leukocyte enzyme abnormality

leukodystrophy

leukoencephalitis, acute necrotizing hemorrhagic

leukoencephalopathy

leukoencephalopathy, differential diagnosis

Lewy body

Lewy body disease, diffuse

life expectancy

limbic encephalitis

linear lesion

lipid storage disorder of CNS

lithium

liver disease

liver transplantation

lobar atrophy

lymphoma

lymphoma involving CNS

lymphoma, primary of CNS

lysosomes, abnoral

macrocephaly

macropsia

magnetic susceptibility

malignancy screen

mania

maple syrup urine disease

Marinesco-Sjogren syndrome

masked facies

megalencephaly

MELAS syndrome

memory, defect of recent

memory, impairment of

meningitis

meningoencephalitis

mental retardation

mental status, abnormal

MERRF syndrome

metabolic disorder, primary

metabolic disorder, primary-screening tests

metachromatic leukodystrophy

microhemorrhage, intracerebral

Mini Mental Status Examination

misdiagnosis

mitochondrial disease

mitochondrial encephalomyopathy

mitochondrial recessive ataxic syndrome

Morvan's fibrillary chorea

motor cortex

motor neuron disease

movement disorder

movement disorder, drug induced

movement disorder, extrapyramidal

MRI

MRI pattern

MRI, abnormal

MRI, abnormal, seizure causing

MRI, ADC maps

MRI, artifacts

MRI, CAT scan compared to

MRI, cerebrovascular disease

MRI, complications with

MRI, contrast enhanced

MRI, demyelinating disease

MRI, diffusion tensor

MRI, diffusion weighted

MRI, diffusion weighted, pattern

MRI, early changes in CVA

MRI, high signal foci on

MRI, high signal intensity of basal ganglia

MRI, indications for

MRI, lesion burden

MRI, negative

MRI, paramagnetic effect

MRI, proton density

MRI, punctate pattern

MRI, serial

MRI, spinal cord

MRI, susceptibility weighted

MRI, T1 weighted high signal foci

MRI, target sign

MRS

multiple sclerosis

multiple sclerosis, differential diagnosis of

multiple sclerosis, familial

multiple system atrophy

myelitis, longitudinal

myoclonus, differential diagnosis of

myoclonus, epilepsy

myoclonus, stimulus sensitive

myopathy

myopathy, mitochondrial

nasal brushings

negative

neoplasm, intracranial

neoplasm, metastatic to CNS

neoplasm, pituitary

neoplasm, primary intracerebral

neoplasm, primary of CNS

nerve conduction studies

neuroendocrinology

neurofibrillary degeneration

neurofibromatosis 1

neurologic complications of, surgery

neurologic complications of, systemic cancer

neurologic disease

neurologic disease, diagnoses of

neurologic examination, focal

neurologic signs

neurologic testing

neuron specific enolase

neuronal cell surface antigen

neuronal ceroid-lipofuscinosis

neuropathology

neuropathology, brain

neuropathy

neuropathy, ataxia, retinitis pigmentosa

neuropathy, peripheral

neurotoxic

neurotoxin

next-generation sequencing

nucleus basalis of Meynert

nutritional deficiency

nystagmus

nystagmus, periodic alternating

nystagmus, rotary

occipital cortex

occipital lobe

occipital lobe, lesion of

occupational neurologic disorders

ocular motility, disorders of

old age, neurology of

ophthalmoplegia, plus syndrome

ophthalmoplegia, progressive external

optic atrophy

optic atrophy, hereditary

optic neuropathy

organ donor

organ transplantation

orthostatic hypotension

osmotic demyelination syndrome

overlap syndrome

owl's eye sign of spinal cord

parietal lobe, lesion of

parietal lobe, syndromes of

Parkinson disease

Parkinson disease, misdiagnosis

Parkinson disease, motor neuron disease with

Parkinson disease, postencephalitic

Parkinsonism plus syndrome

Parkinsonism syndrome

PAS positive

PAS positive material in the brain

pathognomonic

pathologic reflex

peduncular hallucinosis

pigmentary retinopathy

pituitary, hormones of

PLEDs

PLEDs, bilateral independent

pleocytosis of cerebrospinal fluid

POLG1 gene

polymerase chain reaction

polyneuropathy

polyneuropathy, chronic inflammatory demyelinating

polysomnogram

pons, lesion of

posterior cortical atrophy

posterior leukoencephalopathy syndrome

postictal encephalopathy

potassium channel antibodies

practice guidelines

preclinical

pregnancy, neurologic complications in

prenatal diagnosis by amniocentesis

prevention of neurologic disorders

progressive infantile poliodystrophy

progressive multifocal leucoencephalopathy

progressive neurologic disorder

progressive supranuclear palsy

proprioception

prosopagnosia

protein 14-3-3, cerebrospinal fluid

protein 14-3-3, cerebrospinal fluid, false negative

protein 14-3-3, cerebrospinal fluid, false positive

pruritus

psychiatric disorder

psychiatric problems in neurologic disorders

psychomotor retardation

pursuit eye movements, abnormal

putamen, lesion of

putamen, lesion of, bilateral

pyramidal tract

pyramidal tract dysfunction

pyrimethamine

pyruvate dehydrogenase deficiency

pyruvate metabolism, abnormality of

quadriparesis

quadriplegia

radiation therapy, CNS treatment and complications with

ragged-red fibers

rapidly fatal neurologic illness

rapidly progressing neurologic illness

real-time quaking-induced conversion

release phenomena

remote effect of cancer on the nervous system

respiratory failure

restless leg syndrome

retinal degeneration

retinopathy

reversible cerebral vasoconstrictive syndromes

reversible neurologic disorder

review article

rigidity

risk factors

risk-benefit assessment

Romberg's sign

rooting reflex

roving eye movements

saccadic eye movements, abnormal

seizure, nonconvulsive

senile plaques

sensorineural hearing loss

single photon emission computed tomography

skin, biopsy

sleep

sleep pathology and physiology

slow virus infection of CNS

spinal cord, lesion of

spinocerebellar degeneration

spongy degeneration of brain

spongy degeneration of brain, differential diagnosis of

status epilepticus, nonconvulsive

steroid

steroid therapy, CNS treatment and complications with

stiff legs

striatonigral degeneration

striatonigral degeneration, infantile

striatum, lesion of

striatum, lesion of, bilateral

strokelike episodes

stuporous

subacute sclerosing panencephalitis(S.S.P.E.)Dawson's disease

substantia nigra

suck, poor

sudden death

symmetric brain lesions

temporal lobe, status

term infant

thalamic tumors

thalamic tumors, bilateral

thalamus

thalamus, atrophy of

thalamus, infarction of

thalamus, infarction, bilateral

thalamus, lesion of

thalamus, lesion of-bilateral

treatment of neurologic disorder

urine test for metabolic disorders

visual acuity, decreased

visual cortex

visual distortions

visual evoked response

visual field defect

visual impairment

visual loss

visual loss, progressive

vitamin deficiency

Von Hippel Lindau

walking frame

walking, difficulty with

Wallerian degeneration

weakness

weakness, acute

weakness, focal

weakness, progressive

weight loss

Wernicke's aphasia

Wernicke's encephalopathy

West Nile fever

Western immunoblot test

wheelchair

white matter disease

white matter disease, periventricular

wide based gait

workup

Showing articles 200 to 250 of 2238 << Previous Next >>

Risk Factors for Creutzfeldt-Jakob Disease:A Reanalysis of Case-Control Studies
Neurol 46:1287-1291, Wientjens,D.P.W.M.,et al, 1996

MR Imaging of Creutzfeldt-Jakob Disease
Radiology 199:793-798, Finkenstaedt,M.,et al, 1996

Potential Transmission of BSE via Medicinal products
BMJ 312:988-989, Wickham,E.A., 1996

Bovine Spongiform Encephalopathy and Creutzfeldt-Jakob Disease
BMJ 312:790-791, Brown,P., 1996

BSE Linked to New Variant of CJD in Humans
BMJ 312:795, 791, 843, 85496., , 1996

A New Variant of Creutzfeldt-Jakob Disease in the UK
Lancet 347:921-925, 915, 916, 91796., Will,R.G.,et al, 1996

Creutzfeldt-Jakob Disease in a Young Woman
Lancet 347:945-948, Tabrizi,S.J.,et al, 1996

Creutzfeldt-Jakob Disease from Contaminated Growth Hormone Extracts in France
Neurol 47:690-695, Billette de Villemeur,T.,et al, 1996

Diagnostic Criteria for Sporadic Creutzfeldt-Jakob Disease
Arch Neurol 53:913-920, Kretzschmar,H.A.,et al, 1996

Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
Ann Neurol 39:343-351, Rahman,S.,et al, 1996

Accuracy and Reliability of Periodic Sharp Wave Complexes in Creutzfeldt-Jakob Disease
Arch Neurol 53:162-166, Steinhoff,B.J.,et al, 1996

Clinical, Neuroimaging, and Pathologic Features of Progressive Nonfluent Aphasia
Ann Neurol 39:166-173, Turner,R.S.,et al, 1996

A Case of Creutzfeldt-Jakob Disease (CJD) Started with Monoparesis of the Left Arm
Rinshi Shinkeigaku 36:1245-1248, Obi, T.,et al, 1996

MRI of Creutzfeldt-Jakob Disease:Asymmetric High Signal Intensity of the Basal Ganglia
Neurol 45:1932-1933, Yoon,S.S.,et al, 1995

Creutzfeldt-Jakob Disease and Bovine Spongiform Encephalopathy:Any Connection?
BMJ 311:1415-1421, Almond,J.W., 1995

Cerebrospinal Fluid Concentration of Neuron-specific Enolase in Diagnosis of Creutzfeldt-Jakob Disease
Lancet 345:1609-1610, Zerr,I.,et al, 1995

Creutzfeldt-Jakob Disease after Liver Transplantation
Ann Neurol 38:269-272, Creange,A.,et al, 1995

Mitochondrial DNA and Disease
NEJM 333:638-644, Johns,D.R., 1995

Clinical and Genetic Studies of Fatal Familial Insomnia
Neurol 45:1068-1075, Reder,A.T.,et al, 1995

Canavan Disease:From Spongy Degeneration to Molecular Analysis
J Pediatr 127:511-517, Matalon,R.,et al, 1995

Human Prion Diseases
Ann Neurol 35:385-395, Prusiner,S.B.&Hsiao,K.K., 1994

Human Spongiform Encephalopathy:The NIH Series of 300 Cases of Experimentally Transmitted Disease
Ann Neurol 35:513-529, Brown,P.,et al, 1994

The Pathology and Nosology of Primary Progressive Aphasia
Neurol 44:2065-2072, Kertesz,A.,et al, 1994

The Apolipoprotein E Alleles as Major Susceptibility Factors for Creutzfeldt-Jakob Disease
Lancet 344:1315-1318, 13101994., Amouyel,P.,et al, 1994

Posterior Cortical Atrophy:Neuropathologic Correlations
Arch Neurol 51:269-274, Victoroff,J.,et al, 1994

MR Diagnosis of Creutzfeldt-Jakob Disease:Significance of High Signal Intensity of the Basal Ganglia
AJR 162:137-140, Barboriak,D.P.,et al, 1994

Iatrogenic Creutzfeldt-Jakob Disease:An Example of the Interplay Between Ancient Genes and Modern Medicine
Neurol 44:291-293, Brown,P.,et al, 1994

The Mutations at nt 8993 of Mitochondrial DNA is a Common Cause of Leigh's Syndrome
Ann Neurol 34:827-834, Santorelli,F.M.,et al, 1993

Molecular Genetic Characterization of an X-Linked Form of Leigh's Syndrome
Ann Neurol 33:652-655, Matthews,P.M.,et al, 1993

Positron Emission Tomographjy and Histopathology in Creutzfeldt-Jakob Disease
Neurol 43:1828-1830, Goldman,S.,et al, 1993

Inherited Prion Disease (PrP lysine 200) in Britain:Two Case Reports
BMJ 306:301-302, 2881993., Collinge,J.,et al, 1993

Clinicopath Conf
Spongiform Encephalopathy (Creutzfeldt-Jakob Disease) , with Amyloid (KURU) Plaques, Case 17-1993, N, JM 328:66,1993., 1993

Abnormal Eye Movements in Creutzfeldt-Jakob Disease
Ann Neurol 34:192-197, Grant,M.P.,et al, 1993

Gerstmann-Straussler-Schneinker Syndrome:MR Findings
J Comput Assist Tomogr 17:326-327, Wimberger,D.,et al, 1993

Real and Imagined Clinicopathological Limits of"Prior Dementia"
Lancet 341:127-129, Brown,P.,et al, 1993

Infectious Prions or Cytotoxic Metabolites?
Lancet 341:159-161, Pablos-Mendez,A.,et al, 1993

Creutzfeldt-Jakob Disease in a Physician:A Review of the Disorder in Health Care Workers
Neurol 43:205-206, Berger,J.R.&David,N.J., 1993

Creutzfeldt-Jakob Disease and Blood Transfusion
lancet 341:205-207, Esmonde,T.F.G.,et al, 1993

MRI Abnormalities in Creutzfeldt-Jakob Disease
Neuroradiology 35:584-585, DiRocco,A.,et al, 1993

Familial Creutzfeldt-Jakob Disease (Codon 200 Mutation) with Supranuclear Palsy
Bertoni. J. M. , et al, JAMA 268:2413-2415., , 1992

Drug Induced Creutzfeldt-Jakob Like Syndrome
J Psychiatr Neurosci 17:103-105, Finelli,P.F., 1992

Analysis of the Prion Protein Gene in Thalamic Dementia
Neurol 42:1859-1863, Petersen,R.B.,et al, 1992

Creutzfeldt-Jakob Disease in a Recipient of Human Pituitary-Derived Gonadotrophin:A Second Case
JNNP 55:1094-1095, Cochius,J.I.,et al, 1992

Progressive Language Disorder Due to Lobar Atrophy
Ann Neurol 31:174-183, Snowden,J.S.,et al, 1992

Fatal Familial Insomnia, A Prion Disease with a Mutation at Codon 178 of the Prion Protein Gene
NEJM 326:444-449, Medori,R.,et al, 1992

Fatal Familial Insomnia:Clinical and Pathologic Study of Five New Cases
Neurol 42:312-319, Manetto,V.,et al, 1992

Fatal Familial Insomnia:A Second Kindred with Mutation of Prion Protein Gene at Codon 178
Neurol 42:669-670, 1992, Medori,R.,et al, 1992

Prion Disease
NEJM 326:486-487, Johnson,R.T., 1992

Creutzfeldt-Jakob Disease in a Pathologist
Neurol 42:463, Gorman,D.G.,et al, 1992

Evaluation of Cerebral Biopsies for the Diagnosis of Dementia
Arch Neurol 49:28-31, Hulette,C.M.,et al, 1992

Showing articles 200 to 250 of 2238 << Previous Next >>