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advances in neurology
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Babinski sign
basal ganglia
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benign essential tremor
bent spine syndrome
biopterin deficiency
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catecholamine
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Charcot-Marie-Tooth
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chorea
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chromosomal abnormality
chromosome 14
cirrhosis
cirrhosis, causes of childhood
Clinical Pathologic Conference(C.P.C.)
clonazepam
cogwheel rigidty
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dopa responsive dystonia
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uric acid, low
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Showing articles 1600 to 1650 of 1744 << Previous Next >>

Juvenile Neuroaxonal Dystrophy:Clinical, Electrophysiological, & Neuropathological Features
Ann Neurol 3:419, Dorfman,L.J.,et al, 1978

The Cervical Myelopathy Associated with Rheumatoid Arthritis:Analysis of 32 Patients, with Two Post-mortem Cases
Ann Neurol 3:144, Nakano,K.K.,et al, 1978

The Cherry-red Spot-Myoclonus Syndrome
Ann Neurol 3:234, Rapin,I.,et al, 1978

Familial Cavernous Angiomas
Arch Neurol 35:746-749, Bicknell,J.M.,et al, 1978

Monozygotic Twins With Presumed Metachromatic Leukodystrophy
Arch Neurol 35:689-691, Hashimoto,T.,et al, 1978

Clinical & Extraneural Histologic Diagnosis of Neuronal Ceroidlipofuscinosis
Neurol 28:1008-1012, Miley,C.E.III.,et al, 1978

Familial Incidence of Ruptured Intracranial Aneurysms
Arch Neurol 35:675-677, Acosta-Rua,G.J., 1978

Ataxia Telangiectasia
Arch Neurol 35:553-554, Teplitz,R.L., 1978

Tics & Tourette's:A Continuum of Symptoms
Ann Neurol 4:145-148, Golden,G.S., 1978

Precautions in Familial Transmissible Dementia
Arch Neurol 35:697-698, Cook,R.,et al, 1978

Obstructive Sleep Apnea in Family Members
NEJM 299:969-973, Strohl,K.P.,et al, 1978

Neurological Manifestations of Hereditary Hemorrhagic Telangiectasia (Rendu-Osler-Weber Disease)
Ann Neurol 4:130-144, Roman,G.,et al, 1978

Familial Neuromuscular Disease with Type 1 Fiber Hypoplasia, Tubular Aggregates, Cardiomyopathy, & Myasthenic Features
Neurol 28:1135-1140, Dobkin,B.H.,et al, 1978

Peripheral Neuropathy in Myotonic Dystrophy
Arch Neurol 35:741-745, Olson,N.D.,et al, 1978

Systemic Membrane Defect in the Proximal Muscular Dystrophies
NEJM 299:841-846, Pickard,N.A.,et al, 1978

Amyotrophic Lateral Sclerosis
Arch Neurol 35:638-642, Rosen,A.D., 1978

Mirror Movements after Childhood Hemiparesis
Neurol 28:1152-1158, Woods,B.T.,et al, 1978

The Lissencephaly, (Agyria) Syndrome in Siblings
Arch Neurol 35:608-611, Garcia,C.A.,et al, 1978

Familial Chorea & Myoclonus Epilepsy
Neurol 28:913-919, Takahata,N.,et al, 1978

Clinical Pathological Conference, Reticulum Cell Sarcoma of Brain
NEJM 299:1349-1359, Case Record 49-1978,Mass.Gen.Hosp., 1978

Clinical Syndromes of Myasthenia in Infancy & Childhood
Arch Neurol 35:97, Fenichel,G.M., 1978

Cervical Myelopathy Due to Ossification of the Posterior Longitudinal Ligament
Arch Neurol 35:33, Murakami,N., 1978

Late Adult-onset Metachromatic Leukodystrophy
Arch Neurol 35:475, Bosch,E.P., 1978

Familial Vascular Malformation or Chance Occurrence
Neurol 28:98, Barre,R.G.,et al, 1978

Supratentorial Leptomeningeal Hemangioblastoma
Neurol 28:727, Lee,K.R.,et al, 1978

Transient Spastic Paraparesis Following Abdominal Aortography:Management with Cerebrospinal Fluid Lavage
Ann Neurol 3:185, Morariu,M.A., 1978

Blue Rubber Bleb Nevus Syndrome with CNS Involvement & Thrombosis of a Vein of Galen Malformation
Ann Neurol 3:464, Waybright,E.A.,et al, 1978

Extreme Insulin Resistance in Ataxia Telangiectasia
NEJM 298:1164, Bar,R.S.,et al, 1978

Familial Degeneration of the Basal Ganglia with Acanthocytosis:a Clinical Neuropathological, & Neurochemical Study
Ann Neurol 3:253, Bird,T.D.,et al, 1978

Hereditary Paroxysmal Ataxia:Response to Acetazolamide
Neurol 28:1259-1264, Griggs,R.C.,et al, 1978

Pseudoxanthoma Elasticum:A Review of Neurological Complications
Ann Neurol 4:18, Iqbal,A.,et al, 1978

Malignant Hyperthermia & Central Core Disease in a Child with Congenital Dislocating Hips
Arch Neurol 35:189, Eng,G.D.,et al, 1978

Dominant Spinopontine Atrophy
Arch Neurol 35:156, Pogacar,S.,et al, 1978

Autosomal Dominant System Degeneration in Portugese Families of the Azores Islands
Neurol 28:703, Coutinho,P.,et al, 1978

Clinical pathological conference
Von Hippel-Lindau disease, Case Record 1-1978, NEJM 298:95978., , 1978

Neurological Manifestations of Fabry Disease in Female Carriers
Ann Neurol 4:537-540, Bird,T.D.,et al, 1978

Muscle Fiber-Type Disproportion
Arch Neurol 35:823-826, Eisler,T.,et al, 1978

Autosomal Dominant Neurological Disorders
Ann Neurol 4:548-552, Brady,R.O.,et al, 1978

Adrenomyeloneuropathy:A Probable Variant of Adrenoleukodystrophy
Neurol 27:1107-1113, Griffin,J.W.,et al, 1977

An unusual Cause of Apparent Epilepsy:ECG & EEG Findings in a Case of Jervell Lange-Neilson Syndrome
JNNP 40:1102, Selby,P.J.,et al, 1977

Intracranial Aneurysms:Characteristics of Aneurysms in Siblings
NEJM 297:115, 1977. (Letter), Andrews,R.J., 1977

Physostigmine in Familial Ataxias
Neurol 27:70, Kark,R.A.,et al, 1977

Spinocerebellar Ataxia & HLA Linkage:Risk Prediction by HLA Typing
NEJM 296:1138, Jackson,J.F.,et al, 1977

Hereditary Chorea Without Dementia
JNNP 40:687, Behan,P.O.,et al, 1977

Spinal Cord Compression in Thalassaemia
JNNP 40:1120 1977., Cross,J.N.,et al, 1977

Neurologic Aspects of Hereditary Hemorrhagic Telangiectasia
Arch Neurol 34:101, Adams,H.P.,et al, 1977

Reversible Cerebellocerebral Disorder in Primary Hemochromatosis
Arch Neurol 34:123, Singh,N.,et al, 1977

The Spectrum of Mild X-Linked Recessive Muscular Dystrophy
Arch Neurol 34:408, Ringer,S.P.,et al, 1977

Familial Idiopathic Cerebral Calcifications
et al. , JNNP 40:280977., Boller,F., 1977

Duane Syndrome & Congential Upper-Limb Anomalies:A Familial Occurrence
Arch Neurol 34:174, Okihiro,M.M.,et al, 1977



Showing articles 1600 to 1650 of 1744 << Previous Next >>