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advances in neurology
agenesis of corpus callosum
Aicardi's syndrome
Alzheimer's disease
amniocentesis
amyotrophic lateral sclerosis
amyotrophic lateral sclerosis, epidemiology of
amyotrophic lateral sclerosis, familial
amyotrophic lateral sclerosis, guamian type of
ANA
anti basal ganglia antibodies
anti MAG antibodies
antistreptolysin titer
antithyroid antibodies
aphasia
areflexia
arthrogryposis multiplex
ataxia
ataxia, truncal
autism
autoantibodies
autoimmune disease
axonal spheroid
Babinski sign
basal ganglia
basal ganglia, lesion of
basal ganglia, lesion, bilateral
bilateral periventricular nodular heterotopia
brain atrophy
brain biopsy
burst suppression pattern, electroencephalogram
CAT scan, abnormal
catatonia
central core disease
cerebellar degeneration
cerebral cortex
cerebrospinal fluid, elevated protein of
cerebrospinal fluid, lactic acid concentration
Charcot-Marie-Tooth
cherry red spot
cherry red spot-myoclonus syndrome
children
chorioretinitis
chromosomal abnormality
chromosome 5
Clinical Pathologic Conference(C.P.C.)
coloboma
confusion
confusional state, acute
congenital malformation
congenital malformation, non CNS
corpus callosum
cortical dysplasia, focal
cyst, porencephalic
deep gray nuclei
degenerative diseases of CNS
dentate nuclei
dentate nuclei, lesion of
developmental milestones
developmental milestones, loss of
developmental retardation
differential diagnosis
drooling
dropped head syndrome
dyskinesia
dysphagia
dystonia
electroencephalogram
electroencephalogram, abnormalities of
emotional lability
encephalitis
encephalitis, autoimmune
encephalitis, focal
encephalitis, Rasmussen's
encephalomyelitis, postinfectious
encephalopathy
encephalopathy, Hashimoto's
enzyme, defect
epidemiology of neurology
epilepsia partialis continua
eye movement, disorders of
Fabry's disease
facial asymmetry
falling
familial
Fazio-Londe's disease
fever
FLAMES
Friedreich's ataxia
gangliosidosis GM2
gaze palsy
gaze palsy, supranuclear
gene
genetic neurologic disorders
genetic screening
hallucination
headache
heavy metal intoxication
hemihypertrophy, congenital
hemiparesis
hemispherectomy
hepatomegaly
heterotopia
hexosaminidase-A
hexosaminidase-A and B
histopathology
Huntington's chorea
hyperreflexia
hypomelanosis of Ito
hypomyelination
hypopigmentation of skin
hypotonia
hypotonia, infants
inborn errors of metabolism
inclusion bodies
inclusion bodies, eosinophilic cytoplasmic
infantile bilateral striatal necrosis
infantile neuronal degeneration
infantile spasm
insomnia
intellectual deficit
intellectual deterioration
iron, brain
Jewish
Kugelberg-Welander syndrome
lactic acidemia
Leigh's disease
lethargy
leukodystrophy
level of consciousness, decreased
lipid storage disorder of CNS
lysosomal storage disease
macrocephaly
malabsorption
malformation, CNS, congenital
megalencephaly
meningeal enhancement
mental retardation
mental status, abnormal
mesial temporal sclerosis
metachromatic leukodystrophy
microcephaly
micropthalmia
misdiagnosis
molecular genetics
monoclonal antibodies
mortality
motor neuron disease
MRI
MRI, abnormal
MRI, CAT scan compared to
MRI, contrast enhanced
MRI, cortical enhancement
MRI, diffusion weighted
MRI, eye of tiger sign
MRI, gradient-echo
MRI, hypointense signal foci on
MRI, negative
MRI, paramagnetic effect
muscle biopsy
muscle spasm
muscle wasting, diffuse
muscular dystrophy, Duchenne
mutism
myasthenia gravis
myoclonus
myoclonus, epilepsy
myotonia dystrophica
neoplasm, peripheral nerve
neoplasm, primary of CNS
neoplasm, primary of CNS-children
nerve conduction studies
nerve conduction studies, motor
neuroaxonal dystrophy
neuroaxonal dystrophy, infantile
neurocutaneous disease
neurofibrillary degeneration
neurologic disease, diagnoses of
neurologic examination, focal
neuronal cell death
neuronal ceroid-lipofuscinosis
neuronal degeneration
neuronal migration disorder
neuroophthalmology
neuropathology
neuropathology, brain
neuropathy
night sweats
NMDA antagonists
nystagmus
nystagmus, rotary
opisthotonus
optic atrophy
optic nerve
optic nerve, lesion of
optic neuritis
PANK2 mutation
paraparesis, familial spastic
Parkinson disease
paroxysmal neurologic disorder
patient information and support
pediatric neurology
perineural invasion
personality change
pleocytosis of cerebrospinal fluid
pleocytosis of cerebrospinal fluid, neutrophilic
poison, mercury
poison, neurologic problems with
postural abnormality
prenatal diagnosis by amniocentesis
prognosis
psychiatric problems in neurologic disorders
psychomotor retardation
psychosis, childhood
pyramidal tract dysfunction
pyruvate metabolism, abnormality of
quadriparesis
recurrent
respiratory tract infection
retinal degeneration
retropulsion
review article
rigidity
rituximab
Sandhoff's disease
segmental demyelination
seizure
seizure, adult onset
seizure, children
seizure, focal
seizure, intractable
seizure, intractable, treatment of
seizure, neonatal
seizure, prognosis in childhood
seizure, psychomotor-temporal lobe
seizure, surgical treatment of
seizure, treatment of
skin, biopsy
skin, lesions in neurologic disorders
SMN1 gene
sore throat
spasticity
speech disorder
speech disorder, childhood
speech, loss of
spinal cord
spinal cord degeneration
spinal muscular atrophy
spinal muscular atrophy, adult onset
spinal muscular atrophy, classification
spinal muscular atrophy, intermediate form
spinocerebellar ataxia
startle reaction
status epilepticus
steroid therapy, CNS treatment and complications with
streptococcal infection
striatal encephalitis
striatonigral degeneration
striatonigral degeneration, infantile
striatum, lesion of
Sturge-Weber syndrome
subacute sclerosing panencephalitis(S.S.P.E.)Dawson's disease
survival motor neuron gene
symmetric brain lesions
Tay-Sachs disease
temporal lobe, status
thalamus, lesion of
thalamus, lesion of-bilateral
thyroiditis
titubation
tone, muscle, increased
treatment of neurologic disorder
tremor
tremor, intention
tricresylphosphate
trinucleotide repeats
tuberous sclerosis
ventricular enlargement
visual acuity, decreased
visual fields, constricted
visual loss
weakness
weakness, generalized
Werdnig-Hoffman disease
West disease
white matter disease
wide based gait
Showing articles 0 to 50 of 1428 Next >>

An 11-year-old girl with focal seizures, fevers, and unilateral, enhancing cortical lesions
Neurol 95:e3153-e3159, Russ, J.B.,et al, 2020

Histopathological Findings in Brain Tissue Obtained during Epilepsy Surgery
NEJM 377:1648-1656, Blumcke, I.,et al, 2017

Clinicopathologic Conference, Tay-Sacks Disease (GM2, Gangliosidosis)
NEJM 370:1830-1841, Case 14-2014, 2014

Late onset autism and anti-NMDA-receptor encephalitis
Lancet 378:98;378, Creten, C.,et al, 2011

Clinical Reasoning: A 9-year-old Girl With Seizures and Encephalopathy
Neurol 74:e97-e100, Nguyen,T.P. &El-Hakam,L.M., 2010

T2* and FSE MRI Distinguishes Four Subtypes of Neurodegeneration With Brain Iron Accumulation
Neurol 70:1614-1619, McNeill,A.,et al, 2008

Spinal Muscular Atrophy
Lancet 371:2120-2133, Lunn,M.R. &Wang,C.H., 2008

Clinicopath Conf, Neuronal Ceroid Lipofuscinosis, Late-Onset Infantile Subtype
NEJM 347:672-680, Case 27-2002, 2002

Post-Streptococcal Autoimmune Dystonia With Isolated Bilateral Striatal Necrosis
Dev Med Child Neurol 44:485-489, Dale,R.C.,et al, 2002

Molecular Basis of the Neurodegenerative Disorders
NEJM 340:1970-1980, Martin,J.B., 1999

Why Would You Remove Half a Brain? Outcome of 58 Children after Hemispherectomy-Johns Hopkins 1968-96
Pediatrics 100:163-171, Vining,E.P.G.,et al, 1997

Subcortical Heterotopia:A Distinct Clinicoradiologic Entity
AJNR 17:1315-1322, Barkovich,A.J., 1996

Life Threatening Focal Status Epilepticus Due to occult Cortical Dysplasia
Arch Neurol 50:695-700, Desbiens,R.,et al, 1993

Magnetic Resonance Imaging in Childhood Intractable Partial Epilepsies:Pathologic Correlations
Neurol 43:681-687, Kuzniecky,R.,et al, 1993

Hypomelanosis of Ito
Editorial, Lancet 339:651-6521992., , 1992

Gray Matter Heterotopias:MR Characteristics & Correlation with Develop & Neurologic Manifest
Radiology 182:493-499, Barkovich,A.J.&Kjos,B.O., 1992

Clinicopath Conf
Infantile Striatonigral Regeneration, with Cerebellar Degeneration, Familial, Case 30-1992, NEJM 327, 261-1992., 1992

Screening for Carriers of Tay-Sachs Disease Among Ashkenazi Jews
NEJM 323:6-12, Triggs-Raine,B.L.,et al, 1990

Neuroaxonal Dystrophy Due to Lysosomal a-N-Acetylgalactosaminidase Deficiency
NEJM 320:1735-1740, Schindler,D.,et al, 1989

Amaurotic Family Idiocy
Am J Dis Child 142:53-56, Abt,I.A., 1988

MR of Neuronal Migration Anomalies
AJR 150:179-187, Barkovich,A.J.,et al, 1988

CT in Ceroid Lipofuscinosis
Neurol 37:1025-1026, Dunn,D.W., 1987

The Cherry-Red Spot in Tay-Sachs & Other Storage Diseases
Ann Neurol 17:356-360, Kivlin,J.D.,et al, 1985

Neurodegenerative Disease of Infancy & Childhood
Ann Neurol 13:351-364, Dyken,P.,et al, 1983

Infantile Neuronal Degeneration Masquerading as Werdnig-Hoffmann Disease
Ann Neurol 8:317-324, Steiman,G.S.,et al, 1980

Prenatal Genetic Diagnosis in 3000 Amniocenteses
NEJM 300:157-163, Golbus,M.S.,et al, 1979

EEG Recognition of Aicardi's Syndrome
Arch Neurol 34:563, Fariello,R.G.,et al, 1977

Chronic Hexosaminidase A & B Deficiency
et al. , Ann Neurol 2:156977., Goldie,W.D., 1977

Epidemiology of Motor-Neuron Diseases
NEJM 288:1047, Bobwick,A.R.,et al, 1973

Tay-Sachs Disease-The Use of Tears for the Detection of Heterozygotes
NEJM 289:1072, Carmody,P.,et al, 1973

Posttransplant Anti-GABAA Receptor Antibody-Associated Autoimmune Encephalitis
Neurol 102:e209245, Togni,C.L.,et al, 2024

Anti-NMDA Receptor Encephalitis Presenting with Cerebellitis in a Pediatric Patient
Neurol 102:e209259, Moehlman,M. & Kornbluh,A.B., 2024

Diffusely Enhancing Lesions on MRI in DPPX Antibody-Associated Encephalitis
JAMA Neurol 8:418-419, Liu,M.,et al, 2024

Magnetic Resonance Imaging Characteristics of LGl1-Antibody and CASPR2-Antibody Encephalitis
JAMA Neurol 81:525-533, Kelly,Mark J., et al, 2024

Clinicopathological Conference, Glutamic Acid Decarborylase 65 Autoantibody-Associated Stiff-Person Syndrome
NEJM 390:1712-1719, Case 14-2024, 2024

Expanding Clinical Spectrum an Anti-GQ1b Antibody Syndrome, A Review
JAMA Neurol 81:762-770, Lee,S-U.,et al, 2024

MR Imaging Findings in Anti-Leucine-Rich Glioma Inactivated Protein 1 Encephalitis:A Systematic Review and Meta-Analysis
AJNR 45:977-986, Almeida,F.C.,et al, 2024

Clinicopathologic Conference, Paraneoplastic Encephalomyelitis Due to Small-Cell Lung Carcinoma and Concurrent Cerebral Amyloid Angiopathy
NEJM< 391357-369, Case 23-2024, 2024

Ictal Whistling Associated with Dominant Parahippocampal Gyrus Cortical Dysplasia
Neurol 103:e209489, Hartnett,P.,et al, 2024

Clinicopathologic Conference, Nutritional Optic Neuropathy Due to Multiple Nutritional Deficits, Including Vitamin A, Copper, and Zinc Deficiencies
NEJM 391:641-650, Gaier,E.D.,et al, 2024

Hyperventilation-Induced Alternating Hemiplegia with Concomitant Hemispheric EEG Slowing in a 7-Year-Old Girl with Headache
Neurol 103:e209759, Proietti,J.,et al, 2024

Itching Frequency and Neuroanatomic Correlated in Frontotemporal Lobar Degeneration
JAMA Neurol 81:977-984, Hadad,R.,et al, 2024

Clinical Neurologic Features and Evaluation of PTEN Hamartoma Tumor Syndrome, A Systematic Review
Neurol 103:e209844, Dhawan,A.,et al, 2024

MOG-IgG-Associated Encephalitis with FLAIR Hyperintensity Along the Brainstem Surface
Ann Neurol 96:460-462, Yin,J.,et al, 2024

Recurrent Rhombencephalitis Associatedwith Anti-GAD65 Antibody
Neurol 102:e208040, Alferes,A.R.,et al, 2024

Validation of the 2023 International Diagnostic Criteria for MOGAD in a Selected Cohort of Adults and Children
Neurol 103:e209321, Varley,J.A.,et al, 2024

Seizures When Exiting a Bath, A Rare Type of Reflex Epilepsy
Neurol 103:e210025, Pascarella,A.,et al, 2024

Cancer Frequency in MuSK Myasthenia Gravis and Histological Evidence of Paraneoplastic Etiology
Ann Neurol 96:1020-1025, Falso,S.,et al, 2024

A 65-Year-Old Woman with Isolated Macroglossia as the Initial Presentation of a Rare Disease
Neurol 103:e210070, Lara,C.,et al, 2024



Showing articles 0 to 50 of 1428 Next >>