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abscess, intracerebral
abscess, intracranial
abscess, sphenoid sinus
acetazolamide
aciduria
Adies pupil
advances in neurology
adverse drug reaction
algorithm
alpha-fetoprotein
altered states of consciousness
AMPA receptor antibodies
amyloidosis
amyotrophic lateral sclerosis
anemia
ankle edema
anti GQ1b IgG antibody
anticholinergic drugs
apraxia of eye movements
areflexia
artane
arthralgia
arthrogryposis multiplex
ascites
ataxia
ataxia telangiectasia
ataxia, cerebellar
ataxia, truncal
athetosis
athetosis, causes of
atlanto-axial subluxation
attention deficit disorder with hyperactivity
autoantibodies
autoimmune basal ganglia encephalitis
autoimmune disease
autonomic dysfunction
autonomic neuropathy
Babinski sign
basal ganglia, calcification of
basal ganglia, lesion of
behavioral disorder
benign essential tremor
biopterin deficiency
bladder dysfunction
blepharospasm
botulinum toxin
bradykinesia
brain atrophy
brainstem, atrophy
brainstem, lesion of
burning skin
calcification, intracranial
camptocormia
carbamazepine
carcinoembryonic antigen
carcinoma
carotid artery disease
carotid artery occlusion, neck
carotid artery stenosis
CAT scan
CAT scan, emission
CAT scan, emission, abnormal
cataracts
catecholamine
cavernous sinus, syndrome
central nervous system, infection of
cerebellar ataxia, children
cerebellar ataxia, hereditary
cerebellar atrophy, primary
cerebellar atrophy, secondary
cerebellar degeneration
cerebellar lesion
cerebellum
cerebral cortical atrophy
cerebral hypoperfusion
cerebral ischemia
cerebral palsy
cerebral palsy, associated problems with
cerebral venous thrombosis
cerebrospinal fluid
cerebrospinal fluid, abnormal
cerebrospinal fluid, elevated protein of
cerebrospinal fluid, gold sol.curve of
cerebrospinal fluid, xanthochromia of
cerebrovascular accident
cerebrovascular accident, infancy and childhood
ceruloplasmin, serum
cervical spine
Charcot-Marie-Tooth
chelation therapy
children
chorea
chorea, causes of
choreoathetosis
choreoathetosis, paroxysmal
chromosomal abnormality
chromosome 11
chromosome 14
chromosome 9
cisternogram, radionuclide
Clinical Pathologic Conference(C.P.C.)
coccidioidomycosis
cognition
cogwheel rigidty
complications
contractures, joint
cornea, opacity of
cranial neuropathy
cranial neuropathy, multiple
deferiprone
degenerative diseases of CNS
delay in diagnosis
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dental procedure, neurologic complications with
depression
dermatomyositis
developmental milestones, loss of
dexterity, impaired
diabetes insipidus
diabetes mellitus
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diet
differential diagnosis
diphenhydramine
diplopia
diurnal variation
DNA probes
donut sign
dopa responsive dystonia
dopamine
drooling
drop attacks
drug induced neurologic disorders
dural sinus thrombosis
dysarthria
dysarthria-clumsy hand syndrome
dysdiadochokinesia
dyskinesia
dyskinesia, causes of
dyskinesia, drug induced
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dystonia
dystonia musculorum deformens
dystonia musculorum deformens, carrier
dystonia, axial
dystonia, cervical
dystonia, children
dystonia, classification
dystonia, etiology of
dystonia, evaluation of
dystonia, face
dystonia, focal
dystonia, laryngeal
dystonia, painful
dystonia, segmental
dystonia, symptomatic
dystonia, treatment of
DYT1 mutation
edema, pedal
efficacy
empyema, epidural
empyema, subdural
encephalitis
encephalitis, autoimmune
encephalitis, brainstem
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encephalitis, paraneoplastic
encephalopathy
encephalopathy, progressive
endarterectomy, carotid
enzyme, defect
episodic neurologic deficits
equinovarus
esophageal varices
eye movement, disorders of
facial expression abnormality
facial movement disorder
facial nerve palsy
familial
fatigue
fine motor function, impaired
foot deformity
frontal lobe, pathologic signs of
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gait disorder
galactorrhea
gamma amino butyric acid
gamma amino butyric acid receptor antibody
gammaglobulin therapy, intravenous
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gene mutation
genetic counselling
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genetic neurologic disorders
genetic testing
gests antagoniste
Gilles de la Tourette syndrome
globus pallidus
globus pallidus, stimulation
GLUT1 deficiency syndrome
glutamic acid decarboxylase, antibody
granuloma, pulmonary
grasp reflex
growth retardation
Guillain Barre syndrome
hands, fisted
head nodding
hearing loss
heparin, subcutaneous
hepatic encephalopathy
hepatic encephalopathy, treatment of
hepatic failure
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hepatolenticular degeneration(Wilson's disease), presymptomatic
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hydrocephalus, normal pressure
hyperreflexia
hypertonia
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hypoparathyroidism, idiopathic
hyporeflexia
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hypotonia
iatrogenic neurologic disorders
imbalance
immunodeficiency
immunosuppression
immunotherapy
inborn errors of metabolism
intellectual deficit
intellectual deterioration
iron, brain
jugular foramen syndrome
Kayser-Fleischer ring
klippel feil syndrome
L-dopa
leg spasms
leg spasms, painful
leg weakness, bilateral
leucine rich glioma inactivated 1 antibodies
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leukopenia
Lhermitte's sign
limbic encephalitis
lithium
liver function enzymes
lymphoma
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mental retardation
mental status, abnormal
mimics
misdiagnosis
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movement disorder, treatment of
MRI
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MRI, paramagnetic effect
MRI, spinal cord
MRI, spinal cord, increased intramedullary cord signal
MRI, spine
multiple sclerosis
multiple system atrophy
Munchausen syndrome
muscle diseases, characteristics of
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muscular dystrophy, Duchenne
muscular dystrophy, facioscapulohumeral
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myasthenia gravis
myasthenic crisis
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myelitis, transverse
myelitis, transverse, idiopathic
myelitis, transverse, prognosis
myelopathy
myelopathy, chronic progressive
myoclonic jerks
myoclonus
myoglobinuria
myopathy
myopathy, carcinomatous
myopathy, thyroid disease causing
myositis
myotonia dystrophica
nasal stuffiness
neck pain
neuritis, causes of
neurochemistry
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neurologic signs
neuropathology
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neuropsychiatry
neurotomy
neurotransmitter
next-generation sequencing
NMDA antagonists
norepinephrine
numb clumsy hands syndrome
nystagmus
obsessive-compulsive disorder
ocular motility, disorders of
ophelia syndrome
optic atrophy
optic neuropathy
osteomyelitis
osteomyelitis, skull
otitis, neurologic complications with
pain
pallidotomy
PANK2 mutation
paraparesis
Parkinson disease
Parkinson disease, differential diagnosis of
Parkinson disease, dystonia with
Parkinson disease, juvenile
Parkinsonism syndrome
paroxysmal dystonic choreoathetosis
paroxysmal neurologic deficits
parsidol
pathology
pediatric autoimmune neuropsychiatric disorders associated with streptococcal infection
penicillamine
personality change
phenylketonuria
pigmentary retinopathy
plasmapheresis
pleocytosis of cerebrospinal fluid
pneumoencephalogram(PEG)
poliomyelitis
polymyositis
polyneuropathy
pons, lesion of
porphyria
postural abnormality
potassium channel antibodies
practice guidelines
precipitating factors
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prognosis
progressive neurologic disorder
prolactin, elevated
psychiatric disorder
psychiatric problems in neurologic disorders
psychological testing, neurologic problems
psychosis
pupil, abnormality in neurologic disorders
pupil, tonic
quality of life
radiation hypersensitivity
Red flags
renal stones
respiratory failure
retinopathy
reversible neurologic disorder
review article
RFLPs
rigidity
Riley-Day syndrome
risk factors
rituximab
safety
sarcoidosis
scoliosis
screening
sedimentation rate, elevated
seizure
sensorineural hearing loss
sensory level
sensory tricks
serologic testing
serologic testing, false negative
seronegative
sexual dysfunction in neurologic disease
shaking
short stature
sicca syndrome
sinemet
sinusitis
Sjogren's syndrome
Sjogren's syndrome, neurologic manifestations of
skin, lesions in neurologic disorders
sleep pathology and physiology
slit lamp examination
spastic dysphonia
speech disorder
speech disorder, childhood
speech disorder, non aphasic
spinal cord
spinal cord, lesion of
spinal muscular atrophy
splenomegaly
startle reaction
stereotaxic surgery
steroid
steroid therapy, CNS treatment and complications with
stiff man syndrome
stimulation, deep brain
stimulation, deep brain, bilateral
striatal encephalitis
substantia nigra
symmetric brain lesions
tardive dyskinesia
tardive dystonia
telangiectases
tetrahydrobiopterin
thrombocytopenia
thrombophlebitis
thrombophlebitis, prophylaxis
toe walking
tonic foot response
tonic spasms
torticollis
transient ischemic attack
transient ischemic attack, limb shaking
transient neurologic deficit
trauma
treatment of neurologic disorder
tremor
tremor, postural
trientine dihydrochloride
trigeminal neuralgia
tripping
tyrosine hydroxylase deficiency
unconsciousness
unconsciousness, transient
urinary incontinence
urinary retention
urinary urgency
valium
vasospasm, cerebral
walking
walking frame
walking, difficulty with
Werdnig-Hoffman disease
wheelchair
white matter disease
Wolfram syndrome
workup
wrist drop
writers cramp
xerophthalmia
xerostomia
zinc
Showing articles 0 to 50 of 2565 Next >>

A Young Woman With Hypertonia, Severe Scoliosis, and Encephalopathy
JAMA Neurol 81:83-84, Hua,L.,et al, 2024

Clinicopathologic Conference,Limb-Shaking Transient Ischemia Attacks
NEJM 389:1416-1423, Case 31-2023, 2023

A 6-Year-Old Girl with Progressive Toe Walking
Neurol 98:e769-e773, Libdeh, A.A. & Ibrahim, A., 2022

Autoimmune Encephalitides: A Broadening Field of Treatable Conditions
Neurologist 22:1-13, Kalman, B., 2017

Dystonia in Children and Adolescents: A Systematic Review and a New Diagnostic Algorithm
JNNP 86:774-781, Van Egmond, M.E.,et al, 2015

Autopsy Case of Severe Generalized Dystonia and Static Ataxia with Marked Cerebellar Atrophy
Neurol 85:1522-1524, Miyamoto, R.,et al, 2015

Degenerative Diseases of the Nervous System, Dystonia Musculorum Deformans
Adams & Victors Principles of Neurology, Chp 39, pg 1099, Ropper, A.H.,et al, 2014

Risk Factors for Spinal Cord Lesions in Dystonic Cerebral Palsy and Generalised Dystonia
JNNP 83:159-163, Guettard,E.,et al, 2012

Dopa-Responsive Dystonia Revisited
Arch Neurol 69:1558-1562, Tadic, V.,et al, 2012

Sjogren Syndrome: Neurologic Complications
www.Medlink.com,Jan, Roman,G.C., 2010

Transverse Myelitis
NEJM 363:564-572, Frohman,E.M. &Wingerchuk,D.M., 2010

High Doses of Deferiprone May Be Associated with Cerebellar Syndrome
BMJ 338:653, Beau-Salinas,F.,et al, 2009

Deep Brain Stimulation for Primary Generalized Dystonia: Long-Term Outcomes
Arch Neurol 66:465-470, Isaias,I.U.,et al, 2009

Clinical Spectrum of Ataxia-Telangiectasia in Adulthood
Neurol 73:430-437, Verhagen,M.M.M.,et al, 2009

Acute Deep-Brain Stimulation of the Internal and External Globus Pallidus in Primary Dystonia: Functional Mapping of the Pallidum
Arch Neurol 64:1281-1286, Houeto,J.-L.,et al, 2007

Pallidal Deep-Brain Stimulation in Primary Generalized or Segmental Dystonia
NEJM 355:1978-1990, Kupsch,A.,et al, 2006

Familial Dopa-Responsive Cervical Dystonia
Neurol 66:599-601, Schneider,S.A.,et al, 2006

Dopa-responsive Dystonic Camptocormia
Neurol 66:1779, Van Gerpen,J.A., 2006

Clinicopath Conf, Dopamine-Responsive-Dystonia Caused by a Mutation in the GCH1 Gene
NEJM 355:831-839, Case 26-2006, 2006

Dystonia
NEJM 355:818-829, Tarsy,D. &Simon,D.K., 2006

Dopamine-Responsive Dystonia
eMedicine (Apr), Nikhar,N.K., 2006

Bilateral Deep-Brain Stimulation of the Globus Pallidus in Primary Generalized Dystonia
NEJM 352:5 459-467, 498, Vidailhet, M., et al, 2005

Pallidal Stimulation Improves Pantothenate Kinase-Associated Neurodegeneration
Ann Neurol 57:738-741,613, Castelnau,P.,et al, 2005

Diagnostic Criteria for Dystonia in DYT1 Families
Neurol 59:1780-1782, Bressman,S.B.,et al, 2002

The DYT1 Phenotype and Guidelines for Diagnostic Testing
Neurol 54:1746-1753,1718, Bressman,S.B.,et al, 2000

Frequency of the DYT1 Mutation in Primary Torsion Dystonia Without Family History
ArchNeurol 57:333-335, Brassat,D.,et al, 2000

Pallidal Stimulation for Generalized Dystonia
J Neurosurg 92:453-456, Tronnier,V.M. &Fogel,W., 2000

Globus Pallidus Deep Brain Stimulation for Generalized Dystonia:Clinical and PET Investigation
Neurol 53:871-874, Kumar,R.,et al, 1999

Dopa-Responsive Dystonia, Some Pieces of the Puzzle are Still Missing
Neurol 50:853-855, Nygaard,T.G.&Wooten,G.F., 1998

Long-Term Follow-Up of Levodopa Responsiveness in Generalized Dystonia
Arch Neurol 55:1320-1323, Dewey,R.B.,et al, 1998

Pallidotomy for Generalized Dystonia
Movement Disorders 13:693-698, Ondo,W.G.,et al, 1998

Dopamine, Dystonia, and the Deficient Co-Factor
Lancet 345:1130, Williams,A.C., 1995

Diphenhydramine is Effective in the Treatment of Idiopathic Dystonia
Arch Neurol 52:405-407, Truong,D.D.,et al, 1995

Dopa-Responsive Dystonia:Pathological and Biochemical Observations in a Case
Ann Neurol 35:396-402, 3811994., Rajput,A.H.,et al, 1994

Comparison of Striatal 18F-dopa Uptake in Adult-Onset Dystonia-Parkinsonism, Parkinson's & Dopa-Responsive Dystonia
Neurol 43:1563-1568, Turjanski,N.,et al, 1993

Wilson Disease
Medicine 71:139-164, Brewer,G.J.&Yuzbasiyan-Gurkan,V., 1992

Wolfram Syndrome:Evidence of a Diffuse Neurodegenerative Disease by Magnetic Resonance Imaging
Neurol 42:1220-1224, 1992,, Rando,T.A.,et al, 1992

Dopa-Responsive Dystonia:Long-Term Treatment Response and Prognosis
Neurol 41:174-181, Nygaard,T.G.,et al, 1991

Ataxia-Telangiectasia:An Interdisciplinary Approach to Pathogenesis
Medicine 70:99-117, Gatti,R.A.,et al, 1991

The Relationship Between Trauma and Idiopathic Torsion Dystonia
JNNP 54:713-717, Fletcher,N.A.,et al, 1991

Dopa-responsive Dystonia:[18F]Dopa Positron Emission Tomography
Ann Neurol 30:24-30, Sawle,G.V.,et al, 1991

Dystonia Gene in Ashkenazi Jewish Population is Located on Chromosome 9q32-34
Ann Neurol 27:114-120, Kramer,P.L.,et al, 1990

The Triumph of Linkage Analysis, Editorial
Ann Neurol 27:111-113, Rosenberg,R.N., 1990

Dopa-Responsive Dystonia:The Spectrum of Clinical Manifestations in a Large North American Family
Neurol 40:66-69, Nygaard,T.G.,et al, 1990

Dopa Responsive Dystonia:A Treatable Condition Misdiagnosed as Cerebral Palsy
BMJ 298:1019-1020, Boyd,K.&Patterson,V., 1989

Idiopathic Hypoparathyroidism and Paroxysmal Dystonic Choreoathetosis
Ann Neurol 24:585, Barabas,G.&Tucker,S.M., 1988

Hereditary Dystonia-Parkinsonism Syndrome of Juvenile Onset
Neurol 36:1424-1428, Nygaard,T.C.&Duvoisin,R.C., 1986

Torsion Dystonia:A Double-Blind, Prospective Trial of High-Dosage Trihexyphenidyl
Neurol 36:160-164, Burke,R.E.,et al, 1986

Brain Neurotransmitters in Dystonia Musculorum Deformans
NEJM 315:347-353, Hornykiewicz,O.,et al, 1986



Showing articles 0 to 50 of 2565 Next >>