Neurology Specific Literature Search   
 
[home][thesaurus]
    
Click Here to return To Results

 

Brachial Amyotrophic Diplegia, A Slowly Progressive Motor Neuron Disorder
Neurol 53:1071-1076, Katz,J.S.,et al, 1999
See this aricle in Pubmed

Article Abstract
We reviewed the records of patients who had a neurogenic "man-in-the-barrell" phenotype documented by examination at least 18 months after onset. These patients had severe bilateral upper-extremity neurogenic atrophy that spared lower-extrem ity, respiratory, and bulbar musculature. Nine of 10 patients meeting these criteria had a purely lower motor neuron disorder. During follow-up periods ranging from 3 to 11 years from onset, only three patients developed lower-extremity weakness, and none developed respiratory or bulbar dysfunction or lost the abili8ty to ambulate. Patients presenting with severe weakness that is fully isolated to the upper limbs, without pyramidal signs, may have a relatively stable variant of motor neuron disease.
 
Related Tags
(click to filter results - removes previous filter)

amyotrophic lateral sclerosis,differential diagnosis
arm weakness
brachial amyotrophic diplegia
diplegia,atonic
diplegia,brachial
Man-In-The-Barrel syndrome
motor neuron disease

Click Here to return To Results