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A 72-year-old Man with a Progressive Cognitive and Cerebellar Syndrome
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Challenging Diagnosis of Gerstmann-Straussler-Scheinker Disease
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A 13-year-old boy with Chronic Ataxia and Developmental Delay
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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Recessive Ataxia With Ocular Apraxia
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Fluid Attenuation Inversion Recovery (FLAIR) Images of Dentatorubropalliodoluysian Atrophy:Case Report
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Clinical and Genetic Abnormalities in Patients with Friedreich's Ataxia
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Ataxia-Telangiectasia:An Interdisciplinary Approach to Pathogenesis
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The Marinesco-Sjogren Syndrome Examined by CT, MR, and 18F-2-Fluoro-2-Deoxy-D-Glucose & PET
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Hereditary Dentatorubral-Pallidoluysian Atrophy:Clinical and Pathologic Variants in a Family
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Gerstmann-Straussler-Scheinker Disease with Coincidental Familial Onset
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Peripheral Neuropathy in Cerebrotendinous Xanthomatosis
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Juvenile Neuroaxonal Dystrophy:Clinical, Electrophysiological, & Neuropathological Features
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Genetic Counseling in Retinitis Pigmentosa
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Slowly rogressive Cerebellar Ataxia in a 55-Year-Old Female Patient
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A 48-Year-Old Man With Spasticity and Progressive Ataxia
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Clinicopathologic Conference, Cerebellar Ataxia, Neuropathy and Vestibular Areflexia Syndrome
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A 47-year-old Man with Rapidly Progressive Ataxia and Vitiligo
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Stridor in Multiple System Atrophy
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Clinicopathologic Conference, Creutzfeldt-Jakob Disease
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Clinical Presentation and Cranial MRI Findings of Listeria Monocytogenes Encephalitis
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Cerebellar Ataxia and Hearing Impairment
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A 54-year-old woman with Dementia, Myoclonus, and Ataxia
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Antibiotic-Associated Encephalopathy
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Progressive Cerebellar Ataxia and New-Onset Diabetes
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Degenerative Diseases of the Nervous System, Cerebellar Degeneration
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Ataxia, Dementia, and Hypogonadotropism Caused by Disordered Ubiquitination
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Clinicopathologic Conference, Acute Infectious Mononucleosis due to Epstein-Barr Virus Infection, Complicated by Acute Otitis Media and Postinfectious Cerebellitis
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Central Nervous System Involvement in Whipple Disease
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Mycoplasma Pneumoniae Infection: Neurologic Complications
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The Autosomal Recessive Cerebellar Ataxias
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Heterogeneity of Coenzyme Q10 Deficiency
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Anti-Glutamic Acid Decarboxylase Limbic Encephalitis Without Epilepsy Evolving Into Dementia with Cerebellar Ataxia
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Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease
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Epstein-Barr Virus Infections of the Nervous System
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The Hot Cross Bun Sign in the Patients with Spinocerebellar Ataxia
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Asymmetric Cerebellar Ataxia and Limbic Encephalitis as a Presenting Feature of Primary Sjogrens Syndrome
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Late-Onset Metachromatic Leukodystrophy: Genotype Strongly Influences Phenotype
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