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Canavan Disease:From Spongy Degeneration to Molecular Analysis
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Gertsmann-Straussler Schneinker Syndrome
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Transmissible Spongiform Encephalopathy in the 21st Century: Neuroscience for the Clinical Neurologist
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Kuru in the 21st Century--An Acquired Human Prion Disease With Very Long Incubation Periods
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Neurodegenerative Diseases and Prions
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Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
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Clinical, Neuroimaging, and Pathologic Features of Progressive Nonfluent Aphasia
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A New Variant of Creutzfeldt-Jakob Disease in the UK
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Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
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The 14-3-3 Brain Protein in Cerebrospinal Fluid as a Marker for Transmissible Spongiform Encephalopathies
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Creutzfeldt-Jakob Disease and Bovine Spongiform Encephalopathy:Any Connection?
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Real and Imagined Clinicopathological Limits of"Prior Dementia"
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Infectious Prions or Cytotoxic Metabolites?
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Progressive Language Disorder Due to Lobar Atrophy
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The Spongiform Encephalopathies, Editorial
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Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
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Leigh Disease (Subacute Necrotizing Encephalomyelopathy) :CT & MR in Five Cases
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Familial Alzheimer's Disease with Myoclonus and'Spongy Change'
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Gerstmann-Straussler-Scheinker Disease:Autopsy Study of a Familial Case
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Gerstmann-Straussler-Scheinker Disease with Coincidental Familial Onset
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