Immunocompetent Patient with Multiple Cranial Nerve Palsies, Ataxia, and Cognitive Decline
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Unmasking Cerebrotendinous Xanthomatosis, Clinical Recognition of a Treatable Cause of Progressive Ataxia
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Inherited Metabolic Diseases of the Nervous System, Adrenoleukodystrophy
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Mitochondrial Respiratory-Chain Diseases
NEJM 348:2656-2668, DiMauro,S. &Schon,E.A., 2003
Clinicopath Conf, Neuronal Ceroid Lipofuscinosis, Late-Onset Infantile Subtype
NEJM 347:672-680, Case 27-2002, 2002
Treating Hearing Loss with Hearing Aids for the Prevention of Cognitive Decline and Dementia
Neurol 106:e214572, Cribb,L.,et al, 2026
A 32-Year-Old Woman with Progressive Vision Loss and Confusion
Neurol 106:e214988, Kumar,A.B.,et al, 2026
A 60-Year-Old Man with Weakness and Gait Dysfunction
JAMA Neurol 82:305-306, Jones,F.J.S.,et al, 2025
Melas Syndrome
Stat PearlsPubl Jan 25, Pia,S. & Lui,F., 2025
Hearing Aids and Cochlear Implants in the Prevention of Cognitive Decline and Dementia-Breaking Through the Silence
JAMA Neurol 80:127-128, Denham,M.W.,et al, 2023
Pachymeningitis and Aortitis as the Initial Presentation of Granulomatosis with Polyangiitis
Neurol 101:979-980, Li,X.,et al, 2023
Spontaneous Intracranial Hypotension
NEJM 385:2173-2178, Schievink, W.I., 2021
Ears of the Lynx Magnetic Resonance Imaging Sign
Ann Neurol 88:16-17, Baghbanian, S.M.,et al, 2020
Selenium Toxicity Associated with Reversible Leukoencephalopathy and Cortical Blindness
JAMA Neurol 75:1282-1283, Rae, W.,et al, 2018
Clinical Manifestations of the anti-IgLON5 Disease
Neurol 88:1736-1743,1688, Gaig, C.,et al, 2017
Precipitous Deterioration of Motor Function, Cognition, and Behavior
JAMA Neurol 74:591-596, Fernandez-Fournier, M.,et al, 2017
Development of a Suspicion Index to Aid Diagnosis of Niemann-Pick Disease Type C
Neurol 78:1560-1567,1546, Wijburg, F.A.,et al, 2012
Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
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MR Imaging of a Group I Case of Hallervorden-Spatz Disease
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Cytochrome c Oxidase Deficiency in Leigh Syndrome
Ann Neurol 22:498-506, DiMauro,S.,et al, 1987
Chronic Progressive Panencephalitis due to Rubella Virus Simulating Subacute Sclerosing Panencephalitis
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Reversible Leukoencephalopathy and Parkinsonism Due to CNS Involvement in Cryoglobulinemia
Neurol 106:e214622, German,A.,et al, 2026
Deep Venous Dural Arteriovenous Fistula Mimicking Progressive Dementia
Stroke 57:e180-181, Langlois-Therien,T.,et al, 2026
A 68-YEar-Old Man with Progressive Numbness, Vertigo, and Cognitive Decline
Neurol 104:e213437, Regan,S.M. & Davalos,L.F., 2025
Clinicopatholigic Conference, Rheumatoid Arthritis with Vasculitis Causing A Confluent Mononeuritis Multiplex
NEJM 390:1312-1322, Case 11-2024, 2024
Glucose Hypermetabolism in the Basal Ganglia
Neurol 101:90-91, Kim,Y.E.,et al, 2023
A Woman With Multifocal Ischemic Strokes and Progressive Cognitive Impairment Due to Intravascular Lymphoma
Stroke 54:e488-e451, Stamm,B., et al, 2023
A 17-Year-Old Girl with Progressive Cognitive Impairment
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Association Between Occupational Exposure to Formaldehyde and Cognitive Impairment
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Acute Cortical Lesions in MELAS Syndrome: Anatomic Distribution, Symmetry, and Evolution
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Anti-LG11 Limbic Encephalitis Presenting as an Expanding Insular Lesion
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Encephalitis with mGluR5 antibodies
Neurol 90:e1964-e1972, Spatola, M.,et al, 2018
Pantothenate Kinase - Associated Neurodegeneration (PKAN)
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Characteristics in Limbic Encephalitis with Anti-Adenylate Kinase 5 Autoantibodies
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Action Tremor, Impaired Balance, and Executive Dysfunction in Midlife
JAMA Neurol 74:603-604, Birch, R.C. & Trollor, J.N., 2017
Autoimmune Encephalitis: Pathophysiology and Imaging Review of an Overlooked Diagnosis
AJNR 38:1070-1078, Kelley, B.P.,et al, 2017
An Older Man with Memory Impairment and Convulsions
BMJ 358:J2824, Zhao, X.,et al, 2017
Long-Term Preclinical Magnetic Resonance Imaging Alterations in Sporadic Creutzfeldt-Jakob Disease
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Recognizing Autoimmune-Mediated Encephalitis in the Differential Diagnosis of Limbic Disorders
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Cognitive Deterioration in Bilateral Asymptomatic Severe Carotid Stenosis
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Psychosis in an Adolescent Girl: A Common Manifestation in Niemann-Pick Type C Disease
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Clinicopathologic Conference, Blind and Confused, Neuromyelitis Optica Spectrum Disorder
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Subacute Sclerosing Panencephalitis
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A 23-Year-Old Man With Seizures and Visual Deficit
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Subacute Sclerosing Panencephalitis
Postgrad Med J 78:63-70, Garg, R.K.,et al, 2002
Spastic Paraparesis after Anaesthesia
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