Homonymous Hemianopia with Normal Magnetic Resonance Imaging
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Clinicopathologic Conference, Creutzfeldt-Jakob Disease
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Clinicopath conf., Human Prion Disease, Sporadic CJD
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Roving Eye and Head in a Patient with Genetic Creutzfeldt-Jakob Disease
Neurol 102:e209385, Nishida,K.,, 2024
Blook Transfusion and Brain Amyloidosis, Should We Be Worried?
JAMA 330:921-922, Greenberg,S.M., 2023
Clinicopathologic Conference, Genetic Creutzfeldt-Jakob Disease
NEJM 386;674-687, Case 5-2022, 2022
Laboratory Diagnosis of Creutzfeldt-Jakob Disease
NEJM 386:1345-1350, Zerr, I., 2022
Sporadic Creutzfeldt-Jakob Disease in a Very Young Person
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Rapid Progression of Prion Disease Associated with Transverse Myelitis
Neurol 94:e1670-e1672, Hussein, O.,et al, 2020
A 45-Year-Old Man with Progressive Insomia and Psychiatric and Motor Symptoms
Neurol 94:e1213-e1218, Lima, J.E.E.,et al, 2020
Dressing Apraxia as Initial Manifestation of Creutzfeldt-Jakob Disease
Tremor and Other Hyperkinetic Movements 10:1-3, Heckmann, J.G.,et al, 2020
Variant Creutzfeldt-Jakob Disease Diagnosed 7.5 Years after Occupational Exposure
NEJM 383:83-85, Brandel, J.P.,et al, 2020
Challenging Diagnosis of Gerstmann-Straussler-Scheinker Disease
Neurol 92:101-103, Kang, M.J.,et al, 2019
Diagnosis of Human Prion Disease Using Real-Time Quaking-Induced Conversion Testing of Olfactory Mucosa and Cerebrospinal Fluid Samples
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Long-Term Preclinical Magnetic Resonance Imaging Alterations in Sporadic Creutzfeldt-Jakob Disease
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Gertsmann-Straussler Schneinker Syndrome
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Diagnosing variant Creutzfeldt-Jakob disease: a retrospective analysis of the first 150 cases in the UK
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Cortical Restricted Diffusion as the Predominant MRI Finding in Sporadic Creutzfeldt-Jakob Disease
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Sporadic Creutzfeldt-Jakob Disease in Two Adolescents
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Systematic Review of Therapeutic Intervention in Human Prion Disease
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Transmissible Spongiform Encephalopathy in the 21st Century: Neuroscience for the Clinical Neurologist
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Rapidly Progressive Dementia
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MR Imaging of Familial Creutzfeldt-Jakob Disease: A Blinded and Controlled Study
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Neuroimaging Findings in Human Prion Disease
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Early Clinical Signs and Imaging Findings in Gerstmann-Straussler-Scheinker Syndrome (Pro102Leu)
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Kuru in the 21st Century--An Acquired Human Prion Disease With Very Long Incubation Periods
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Onset of Creutzfeldt-Jakob Disease Mimicking an Acute Cerebrovascular Event
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Clinical Presentation and Pre-Mortem Diagnosis of Variant Creutzfeldt-Jakob Disease Associated With Blood Transfusion: A Case Report
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Clinicopath Conf, Prion Disease (Sporadic Creutzfeldt-Jakob Disease)
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Transmissible Spongiform Encephalopathies
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Tissue Distribution of Bovine Spongiform Encephalopathy Agent in Primates after Intravenous or Oral Infection
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Possible Transmission of Variant Creutzfeldt-Jakob Disease by Blood Transfusion
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Prion Deposition in Olfactory Biopsy of Sporadic Creutzfeldt-Jakob Disease
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Novel Methods for Disinfection of Prion-Contaminated Medical Devices
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Preclinical vCJD After Blood Transfusion in a PRNP Codon 129 Heterozygous Patient
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Detection of Pathologic Prion Protein in the Olfactory Epithelium in Sporadic Creutzfeldt-Jakob Disease
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Diffusion-Weighted Imaging Discriminates Progressive Supranuclear Palsy from PD, But Not From the Parkinson Variant of Multiple System Atrophy
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Neurodegenerative Diseases and Prions
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14-3-3 Testing in Diagnosing Creutzfeldt-Jakob Disease
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Investigation of Variant Creutzfeldt-Jakob Disease and Other Human Prion Diseases with Tonsil Biopsy Samples
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Prion Protein Conformation in a Patient with Sporadic Fatal Insomnia
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Risk of Transmission of Bovine Spongiform Encephalopathy to Humans in the United States, Report of the Council on Scientific Affairs
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Variant Creutzfeldt-Jakob Disease
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Clinicopath Conf, Creutzfeldt-Jakob Disease,Case 28-1999
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Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
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The Risk of Bovine Spongiform Encephalopathy ('Mad Cow Disease') to Human Health
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New Variant Creutzfeldt-Jakob Disease:Neurological Features and Diagnostic Tests
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Cerebral & Cerebellar Atrophy on Serial MRI in an Initially Symptom Free Subject at Risk of Familial Prion Disease
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