Neurodegenerative Diseases of Childhood:MR and CT Evaluation
J Comput Assist Tomogr 15:210-222, Mirowitz,S.A.,et al, 1991

Dementia Presenting with Aphasia:Clinical Characteristics
JNNP 54:542-545, Mendez,M.F.&Zander,B.A., 1991

Serial MR Imaging in Creutzfeldt-Jakob Disease
Neuroradiology 33:364-367, Uchino,A.,et al, 1991

Genetic Predisposition to Iatrogenic Creutzfeldt-Jakob Disease
Lancet 337:1441-1442, Collinge,J.,et al, 1991

Creutzfeldt-Jakob Disease in a Patient with a Cadaveric Dural Graft
Neurol 41:940-941, Miyashita,K.,et al, 1991

Mutation of the Prion Protein in Libyan Jews with Creutzfeldt-Jakob Disease
NEJM 324:1091-1097, Hsiao,K.,et al, 1991

Inherited Human Prion Diseases
Neurol 40:1820-1827, Hsiao,K.&Prusiner,S.B., 1990

Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
Neurol 40:1876-1882, Gascon,G.G.,et al, 1990

Familial Creutzfeldt-Jakob Disease without Periodic EEG Activity
Ann Neurol 28:585-588, Tietjen,G.E.&Drury,I., 1990

Prion Dementia Without Characteristic Pathology
Lancet 336:7-9, 21-221990., Collinge,J.,et al, 1990

MR Findings in Patients with Subacute Necrotizing Encephalomyelopathy (Leigh Syndrome)
AJR 154:1269-1274, Medina,L.,et al, 1990

Rapid Detection of Creutzfeldt-Jakob Disease and Scrapie Prion Porteins
Neurol 40:110-117, Serban,D.,et al, 1990

A Simple & Effective Method for Inactivating Virus Infectivity from Patients with Creutzfeldt-Jakob Disease
Neurol 40:887-890, Brown,P.,et al, 1990

Positron Emission Tomography in Creutzfeldt-Jakob Disease
Arch Neurol 47:1035-1038, Holthodd,V.A.,et al, 1990

The Nucleus Basalis of Meynert in 20 Definite Cases of Creutzfeldt-Jakob Disease
JNNP 52:304-309, Cartier,L.,et al, 1989

Creutzfeldt-Jakob Disease Presenting as Isolated Aphasia
Neurol 39:55-58, Mandell,A.M.,et al, 1989

Diagnosis of Gerstmann-Straussler Syndrome in Familial Dementia with Prion Protein Gene Analysis
Lancet 2:15-17, Collinge,J.,et al, 1989

Leigh Disease:Value of CT in Presymptomatic Patients and Variability of the Lesions with Time
J Comput Assist Tomogr 13:207-210, Taccone,A.,et al, 1989

Transplanted Infections:Donor-To-Host Transmission with the Allograft
Ann Int Med 110:1001-1016, Gottesdiener,K.M., 1989

Transmission of Alpers'Disease (Chr Prog Encephalopathy) Produces Exper Creutzfeldt-Jakob Disease in Hamsters
Neurol 39:615-621, Manuelidis,E.E.,et al, 1989

Gerstmann-Straussler-Scheinker Disease, I, Extending the Clinical Spectrum
Neurol 39:1446-1452, Farlow,M.R.,et al, 1989

Gerstmann-Straussler-Scheinker Disease, II, Neurofibrillary Tangles & Plaques with PrP-amyloid in an Affected Family
Neurol 39:1453-1461, Ghetti,B.,et al, 1989

Diffuse Lewy Body Disease and Progressive Dementia
Neurol 38:1520-1528, Burkhardt,C.R.,et al, 1988

Familial Alzheimer's Disease with Myoclonus and'Spongy Change'
Arch Neurol 45:1097-1100, Duffy,P.,et al, 1988

Improvement of Cerebral CT Abnor Following Liver Transplant in a Patient with Wilson Disease
J Comput Assist Tomogr 12:138-149, Rothfus,W.E.,et al, 1988

Routine Use of Phenolized Formalin in Fixation of Autopsy Brain Tissue to Reduce Risk of Inadvert Trans of Creutzfeldt-Jakob Dis
NEJM 319:654, Brumback,R.A., 1988

Creutzfeldt-Jakob Disease:Correlation of MRI & Neuropathologic Findings
Neurol 38:1481-1482, Gertz,H.J.,et al, 1988

The Decline and Fall of Creutzfeldt-Jakob Disease Associated with Human Growth Hormone Therapy
Neurol 38:1135-1137, Brown,P., 1988

Creutzfeldt-Jakob Disease Following Pituitary-Derived Human Growth Hormone Therapy:A New American Case
Neurol 38:1131-1133, Marzewski,D.J.,et al, 1988

Human Growth Hormone Therapy & Creutzfeldt-Jakob Disease:A Drama in Three Acts
Pediatrics 81:85-92, Brown,P., 1988

Leigh Disease (Subacute Necrotizing Encephalomyelopathy) :CT & MR in Five Cases
J Comput Assist Tomogr 12:40-44, Geyer,C.A.,et al, 1988

Rapidly Progressive Dementia Caused by Spongiform Encephalopathy
West J Med 148:313-319, Enos,B.E.&Vinters,H.V., 1988

A Creutzfeldt-Jakob Like Syndrome Due to Lithium Toxicity
JNNP 51:120-123, Smith,S.J.M.&Kocen,R.S., 1988

Creutzfeldt-Jakob Disease without Periodic Sharp Wave Complexes:A Clinical, EEG, and Path Study
Neurol 38:1056-1060, Zochodne,D.W.,et al, 1988

Prions & Neurodegenerative Diseases
NEJM 317:1571-1581, 15971987., Prusiner,S.B., 1987

The Epidemiology of Creutzfeldt-Jakob Disease:Conclusion of a 15-year Investigation in France & Review of the Literature
Neurol 37:895-904, Brown,P.,et al, 1987

Iatrogenic Creutzfeldt-Jakob Disease
Neurol 37:1520-1522, Rappaport,E.B., 1987

Magnetic Resonance Imaging in Autopsy-Proved Adult Subacute Necrotizing Encephalomyelopathy (Leigh's Disease)
Arch Neurol 44:563-566, Kissel,J.T.,et al, 1987

Cytochrome c Oxidase Deficiency in Leigh Syndrome
Ann Neurol 22:498-506, DiMauro,S.,et al, 1987

Infantile Beriberi Presenting as Subacute Necrotizing Encephalomyelopathy
J Pediatr 110:888-892, Wyatt,D.T.,et al, 1987

Progressive Aphasia without Dementia:Two Cases with Focal Spongiform Degeneration
Ann Neurol 22:527-532, Kirshner,H.S.,et al, 1987

Progressive Dystonia with Bilateral Putaminal Hypodensities
Arch Neurol 44:1184-1187, Berkovic,S.F.,et al, 1987

Abnormal Proteins in the Cerebrospinal Fluid of Patients with Creutzfeldt-Jakob Disease
NEJM 315:279-283, Harrington,M.G.,et al, 1986

Unilateral Creutzfeldt-Jakob Disease
Neurol 36:1517-1520, Yamanouchi,H.,et al, 1986

Creutzfeldt-Jakob Disease:Clinical Analysis of a Consecutive Series of 230 Neuropathologically Verified Cases
Ann Neurol 20:597-602, Brown,P.,et al, 1986

Precautions in Handling Tissues
Fluids, & Other Contam Materials from Patients with Documented or Suspected Creutzfeldt-Jakob Diseas, , Aeurol 19:75-77,1986., 1986

Diagnosis of Creutzfeldt-Jakob Disease by Western Blot Identification of Marker Protein in Human Brain Tissue
NEJM 314:547-551, Brown,P.,et al, 1986

Gerstmann-Straussler-Scheinker Disease:Autopsy Study of a Familial Case
Ann Neurol 20:540-543, Vinters,H.V.,et al, 1986

Subacute Spongiform Encephalopathy (Creutzfeldt-Jakob Disease) with Amyloid Angiopathy
JNNP 48:1175-1178, Keohane,C.,et al, 1985

Ataxic Creutzfeldt-Jakob Disease:Diagnostic Techniques & Neuropathologic Observations in Early Disease
Neurol 35:254-257, Jones,H.R.,et al, 1985