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abducens nerve paralysis

adenosine deaminase deficiency

adverse drug reaction

agenesis of corpus callosum

alcohol, neurologic complications with

alpha-fetoprotein

alternating hemiplegia

alternating hemiplegia of childhood

anterior spinal artery

apnea, primary central

apraxia of eye movements

Arnold Chiari malformation

ataxia telangiectasia

ataxia, cerebellar

ataxia, hereditary

ataxia, paroxysmal

ataxia, progressive

ataxia, truncal

atlanto-axial subluxation

autonomic dysfunction

autosomal rcessive spastic ataxia of Charlevoix-Saguenay

bacterial infection

basal ganglia, lesion of

basal ganglia, lesion, bilateral

behavioral disorder

benign essential tremor

bone marrow biopsy

brainstem, atrophy

brainstem, dysfunction

brainstem, hypoplasia

brainstem, lesion of

brainstem, malformation

brainstem, neoplasms of

Brown-Vialetto-Van Laere syndrome

Canavan's disease

carotid angiogram

CAT scan, abnormal

cerebellar ataxia, children

cerebellar ataxia, hereditary

cerebellar ataxia, neuropathy and vestibular areflexia syndrome

cerebellar ataxia, primary

cerebellar atrophy, primary

cerebellar atrophy, secondary

cerebellar degeneration

cerebellar hypoplasia

cerebellar peduncle

cerebellar vermis

cerebellum, disease of

cerebellum, neoplasms of

cerebrospinal fluid

cerebrospinal fluid, lactic acid concentration

cerebrovascular accident

cerebrovascular accident, multiple

cerebrovascular accident, young adult

Chediak-Higashi syndrome

cherry red spot

choreoathetosis

chromosomal abnormality

Clinical Pathologic Conference(C.P.C.)

clubfoot as related to neurologic disease

complicated migraine

congenital malformation

congenital ocular motor apraxia

contractures, joint

conus medullaris, lesion of

corneal dystrophy

cranial nerve palsies

cranial neuropathy

cranial neuropathy, multiple

cranio-cervical junction

cultured skin fibroblasts

deafness, bilateral progressive vs.unilateral acute

deafness, unilateral

degenerative diseases of CNS

dementia, familial

dementia, frontotemporal

dementia, presenile

demyelinating disease

developmental abnormality of brain

developmental milestones

developmental milestones, loss of

developmental retardation

diabetes insipidus

diabetes mellitus

diabetes mellitus, chemical

diabetes mellitus, neurologic manifestations of

diabetes mellitus, ocular complications in

diabetic cranialneuropathies

diagnostic criteria

differential diagnosis

disconnection syndrome

down-beat nystagmus

down-beat nystagmus, primary position of gaze

dysdiadochokinesia

electroencephalogram

electroencephalogram, abnormalities of

electronystagmography

electroretinograph

epidemiology of neurology

episodic disorders

episodic neurologic deficits

evoked potentials

eye movement, disorders of

Fabry's disease

face, numbness of

facial nerve palsy

facial nerve palsy, bilateral

failure to thrive

familial hemiplegic migraine

familial periodic ataxia

feeding disorder

finger nose finger test

fourth ventricle, enlargement of

Friedreich's ataxia

frontotemporal dementia, behavioral variant

fundus, abnormality of

gaze palsy, congenital horizontal

gaze palsy, horizontal

gaze palsy, horizontal-bilateral

gaze palsy, supranuclear

gaze palsy, vertical

genetic counselling

genetic neurologic disorders

genetic testing

Gerstmann-Straussler-Scheinker disease

granulomatosis with polyangiitis

granulomatous disease

head circumference

hemangioblastoma

hemophagocytic lymphohistiocytosis, cerebromeningeal

hemophagocytosis

hepatosplenomegaly

Horner's syndrome

hyperthyroidism

hypertriglyceridemia

hypofibrinogenemia

hypomyelination

immunologic disease

immunosuppression

inborn errors of metabolism

inclusion bodies, intracytopasmic

infantile bilateral striatal necrosis

infection, recurrent

intellectual deficit

internuclear ophthalmoplegia

internuclear ophthalmoplegia, bilateral

intracranial pressure, increased

Jakob-Creutzfeldt disease

Joubert syndrome

kyphoscoliosis, neurologic causes of

lactic acidemia

Leber's congenital amaurosis

Leigh's disease

leukocyte peroxidase

leukoencephalopathy

leukoencephalopathy, differential diagnosis

light-near dissociation, causes of

lipid storage disorder of CNS

livedo reticularis

lymphadenopathy

lymphoma involving CNS

lymphomatoid granulomatosis

malformation, CNS, congenital

medulla oblongata

medulla oblongata, lesion of

medulla oblongata, malformation

memory, impairment of

meningitis, carcinomatous

middle cerebellar peduncle, lesion

middle cerebellar peduncle, lesion, bilateral

migraine, hemiplegic

mitochondrial disease

molecular genetics

movement disorder

movement disorder, extrapyramidal

movement disorder, hyperkinetic

MRI, contrast enhanced

MRI, spinal cord

multiple sclerosis, differential diagnosis of

multiple system atrophy

myasthenia gravis

myasthenia gravis, familial incidence of

myasthenia gravis, nystagmus in

myasthenia gravis, ocular

myasthenia gravis, sensory loss with

myoclonic jerks

myoclonus, epilepsy

nausea and vomiting

neoplasm, primary of CNS

neurologic complications of, systemic disease

neurologic disease, diagnoses of

neurologic signs

neuronopathy, sensory

neuroophthalmology

neuropathy, demyelinating

neuropathy, peripheral

next-generation sequencing

Niemann-Pick disease

nystagmus, dissociated

nystagmus, gaze-evoked

nystagmus, gaze-paretic

nystagmus, hereditary

nystagmus, monocular

nystagmus, pendular

nystagmus, periodic

nystagmus, primary position of gaze

nystagmus, rotary

nystagmus, upbeating-in primary position of gaze

nystagmus, vertical

ocular motility, disorders of

ophthalmic artery occlusion

ophthalmoplegia

optical coherence tomography

optokinetic nystagmus, abnormal

palatal myoclonus

paraparesis, spastic

Parkinson disease

Parkinson disease, dystonia with

Parkinsonism syndrome

paroxysmal hemiplegia

paroxysmal neurologic deficits

Pelizaeus Merzbacher

personality change

pleocytosis of cerebrospinal fluid

pons, hypoplasia

precipitating factors

pregnancy, neurologic complications in

pretectal syndrome

primary episodic ataxia

progressive neurologic disorder

pseudointernuclear ophthalmoplegia

psychiatric problems in neurologic disorders

psychological testing, neurologic problems

psychomotor retardation

pulmonary infiltrates

pupil, abnormality in neurologic disorders

pupil, light reflex, abnormal

pursuit eye movements, abnormal

pyramidal tract dysfunction

pyramidal tract, uncrossed

pyruvate metabolism, abnormality of

rapid onset dystonia parkinsonism

rapidly progressing neurologic illness

release phenomena

renal tubular acidosis

respiratory failure

retinal degeneration

rheumatoid arthritis

rheumatoid arthritis, neurologic complications of

riboflavin transporter deficiency

scoliosis, neurologic association with

seizure, children

sensorineural hearing loss

sensory loss, leg

skin, lesions in neurologic disorders

Sneddon's syndrome

spastic diplegia

speech, loss of

spinal cord, ischemic lesion of

spinal cord, neoplasm

spinocerebellar ataxia

spinocerebellar ataxia type 1

spinocerebellar ataxia type 3/Machado Joseph disease

spinocerebellar ataxia type 6

spinocerebellar degeneration

spinopontine atrophy, dominant

spongy degeneration of brain

status epilepticus

steroid therapy, CNS treatment and complications with

stress, emotional

striatonigral degeneration

striatonigral degeneration, infantile

striatum, lesion of

striatum, lesion of, bilateral

subcortical U fibers

syphilis, neurologic complications with

tandem gait, ataxic

thalamus, lesion of

thalamus, lesion of-bilateral

thrombocytopenia

transient neurologic deficit

treatment of neurologic disorder

tremor, cerebellar

tremor, intention

trinucleotide repeats

urinary incontinence

vertigo, episodic

vertigo, treatment of

vestibular areflexia

vision, failure of in childhood

visual acuity, decreased

visual evoked response

Von Hippel Lindau

walking, difficulty with

walking, difficulty with in dark

weakness, generalized

weakness, progressive

white matter disease

wide based gait

Wolfram syndrome

Showing articles 750 to 800 of 2207 << Previous Next >>

Spastic Paraparesis after Anaesthesia
Lancet 353:554, Lee,P.,et al, 1999

A Locus for Febrile Seizures (FEB3) Maps to Chromosome 2q23-24
Ann Neurol 46:671-678, Peiffer,A.,et al, 1999

Localization of a Gene for Myoclonus-Dystonia to Chromosome 7q21-q31
Ann Neurol 46:794-798, Nygaard,T.G.,et al, 1999

Genetic Localization of the Familial Adult Myoclonic Epilepsy (FAME) Gene to Chromosome 8q24
Neurol 53:1180-1183, Plaster,N.M.,et al, 1999

MR Angiography as a Screening Tool for Intracranial Aneurysms:Feasibility, Test Characteristics, and Interobserver Agreement
AJR 173:1469-1475, Raaymakers,T.W.M.,et al, 1999

Diagnosis and Treatment of Wilson's Disease
Semin Neurol 19:261-270, Brewer,G.J.,et al, 1999

Suppression of Pendular Nystagmus by Smoking Cannabis in a Patient with Multiple Sclerosis
Neurol 53:2209-2210, Schon,F.,et al, 1999

Ion Channel Diseases:Episodic Disorders of the Nervous System
Semin Neurol 19:363-369, Ptacek,L.J., 1999

Distal Myopathies:Clinical and Molecular Diagnosis and Classification
JNNP 67:703-709, Mastaglia,F.J.&Laing,N.G., 1999

Lateral Medullary Infarction
Stroke, Pathophysiology, Diagnosis and management, Churchhill Livingstone, NY 3rd Ed, Ch 22, p. 534, Amarenco,P.,et al, 1998

Hereditary Cerebral Cavernous Angiomas:Clinical and Genetic Features in 57 French Families
Lancet 352:1892-1897, Labauge,P.,et al, 1998

Dipsticks and Convulsions
Lancet 352:1824, Koch,H., 1998

Clinicopath Conf,Syndrome of Mitochondrial Encephalopathy,Lactic Acidosis,and Stroke-Like Episodes (MELAS),Case 39-1998
NEJM 339:1914-1923, , 1998

Parkinson's Disease
NEJM 339:1044-1053,1130-1143, Lang,A.E.&Lozano,A.M., 1998

Is There a Familial Carpal Tunnel Syndrome? An Evaluation and Literature Review
Muscle & Nerve 21:1533-1536, Gossett,J.G.&Change,P.F., 1998

Ion Channels and Neurological Disease:DNA Based Diagnosis is Now Possible,and Ion Channels May be Important in Common Paroxysmal Disorders
JNNP 65:427-431, Hanna,M.G.,et al, 1998

The Human Genome Project,Application in the Diagnosis and Treatment of Neurologic Diseases
Arch Neurol 55:1287-1290, Evans,G.A., 1998

Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
NEJM 339:1994-2004, Johnson,R.T. & Gibbs,Jr.,C.J., 1998

Granulomatous Compressive Thoracic Myelopathy as the Initial Manifestation of Wegener's Granulomatosis
Neurol 51:1769-1770, Kelly,P.J.,et al, 1998

The Muscular Dystrophies
BMJ 317:991-995, Emery,A.E.H., 1998

Unilateral Thalamic Deep Brain Stimulation for Refractory Essential Tremor and Parkinson's Disease Tremor
Neurol 51:1063-1069, Ondo,W.,et al, 1998

Inherited Prothrombotic States and Ischaemic Stroke in Childhood
JNNP 65:508-511, Ganesan,V.,et al, 1998

Localization of the Giant Axonal Neuropathy Gene to Chromosome 16q24
Ann Neurol 43:143-148, Flanigan,K.M.,et al, 1998

PCR-Based Strategy for Dx of Hered Neuropathy with Liability to Pressure Palsies & Charcot-Marie-Tooth Dis Type 1A
Neurol 50:760-763, Young,P.,et al, 1998

The Phenotypic Spectrum of CADASIL:Clinical Findings in 102 Cases,
Ann Neurol 44:731-739,715, Dichgans,M.,et al, 1998

Factor V Leiden Mutation is a Risk Factor for Cerebral Venous Thrombosis,A Case-Control Study of 55 Patients
Stroke 29:2507-2510, Ludemann,P.,et al, 1998

Initial and Follow-up Screening for Aneurysms in Families with Familial Subarachnoid Hemorrhage
Neurol 51:1125-1130, Raaymakers,T.W.M.,et al, 1998

Transdural Spinal Cord Herniation:Imaging and Clinical Spectra
AJNR 19:1337-1344, 11851998., Watters,M.R.,et al, 1998

Epilepsies in Twins:Genetics of the Major Epilepsy Syndromes
Ann Neurol 43:435-445, Berovic,S.F.,et al, 1998

Acute Vestibular Syndrome
NEJM 339:680-685, Hotson,J.R.&Baloh,R.W., 1998

Genetic Analysis Enables Definite and Rapid Diagnosis of Cerebrotendinous Xanthomatosis
Neurol 51:865-867, Chen,W.,et al, 1998

CADASIL in a North American Family:Clinical, Pathological, and Radiologic Findings
Neurol 51:844-849, Desmond,D.W.,et al, 1998

Cerebral Manifestation of Wilson's Disease Successfully Treated with Liver Transplantation
Neurol 51:863-865, Bax,R.T.,et al, 1998

CAG Repeat Number Correlates with the Rate of Brainstem and Cerebellar Atrophy in Machado-Joseph Disease
Neurol 51:882-884, Abe,Y.,et al, 1998

Chromosome 20 Ring:A Chromosomal Disorder Associated with a Particular Electroclinical Pattern
Epilepsia 39:942-951, Canevini,M.P.,et al, 1998

Incidence of Dominant Spinocerebellar and Friedreich Triplet Repeats Among 361 Ataxic Families
Neurol 51:1666-1671, Moseley,M.L.,et al, 1998

Reduced Penetrance,Variable Expressivity,and Genetic Heterogeneity of Familial Atrial Septal Defects
Circulation 97:2043-2048, Benson,D.W.,et al, 1998

Retinocochleocerebral Vasculopathy
Medicine 77:12-40, Petty,G.W.,et al, 1998

Primary Position Upbeat Nystagmus Due to Unilateral Medial Medullary Infarction
Ann Neurol 43:403-406, Hirose,G.,et al, 1998

Progressive Atrophy of Cerebellum & Brainstem, Age & Size of Expanded CAG Repeats in the MJDI Gene in Machado-Joseph Dis
Ann Neurol 43:288-296, Onokera,O.,et al, 1998

Reduction in Voice Tremor Under Thalamic Stimulation
Neurol 50:796-798, Carpenter,M.A.,et al, 1998

MR of Hereditary Hemorrhagic Telangiectasia:Prevalence and Spectrum of Cerebrovascular Malformations
AJNR 19:477-484, Fulbright,R.K.,et al, 1998

The Genetics of Alzheimer Disease, Current Status and Future Prospects
Arch Neurol 55:294-296, Blacker,D.&Tanzi,R.E., 1998

Creutzfeldt-Jacob Disease in a Husband and Wife
Neurol 50:684-688, Brown,P.,et al, 1998

Distal Hereditary Upper Limb Muscular Atrophy
JNNP 64:217-220, Gross,D.W.,et al, 1998

Neuroradiologic Findings in Marinesco-Sjogren Syndrome
AJNR 19:281-283, Georgy,B.A.,et al, 1998

Middle Cerebral Artery Main Stem Thrombosis in Two Siblings with Familial Thrombotic Thrombocytopenic Purpura
Neurol 50:1157-1160, Kelly,P.J.,et al, 1998

Detection of a Varient Protein in Hair:New Diagnostic Method in Portuguese Type Familial Amyloid Polyneuropathy
BMJ 316:1500-1501, Ando,Y.,et al, 1998

Consequences of the Delayed Diagnosis of Ataxia-Telangiectasia
Pediatrics 102:98-100, Cabana,M.D.,et al, 1998

Wobbly Handwriting
Lancet 351:336, Rosario,M.A.F.,et al, 1998

Showing articles 750 to 800 of 2207 << Previous Next >>