Huntington Disease: Clinical Features and Diagnosis
UptoDate Dec 2017, Oksana Suchowersky, 2017
Intrathecal 2-hydroxypropyl-�-cyclodextrin Decreases Neurological Disease Progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1-2 trial
Lancet 390:1758-1768, Ory, D.S.,et al, 2017
Histopathological Findings in Brain Tissue Obtained during Epilepsy Surgery
NEJM 377:1648-1656, Blumcke, I.,et al, 2017
A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
Neurol 89:e220-e223, Xiao, F. & Wang, X.F., 2017
A Returning Traveler with Epilepsy
BMJ 359:J4664, Bandi, H.,et al, 2017
A Patient with a History of Encephalomyelitis and Recurrent Optic Neuritis
Neurol 89:e231-e234, Gutman, J.M.,et al, 2017
Disseminated Aspergillosis in an HIV-positive Cannabis user taking steroid treatment
Lancet Infect Dis 17:882, Salam, A.P. & Pozniak, A.L., 2017
Trial of Cannabidiol for Drug-Resistant Seizures in the Dravet Syndrome
NEJM 376:2011-2020, Devinsky, O.,et al, 2017
Autoimmune Encephalitides: A Broadening Field of Treatable Conditions
Neurologist 22:1-13, Kalman, B., 2017
Successful Management of Super-Refractory Status Epilepticus with Thalamic Deep Brain Stimulation
Ann Neurol 81:142-146, Lehtimaki, K.,et al, 2017
Clinicopathologic Conference, Granulomatous Amebic Encephalitis and Sarcoidosis (Inactive)
NEJM 376:368-379, Case 3-2017, 2017
Cerebellar Ataxia and Hearing Impairment
JAMA Neurol 74:243-244, Lin, C.Y. & Kuo, S.H., 2017
Investigations in GABA? Receptor Antibody-Associated Encephalitis
Neurol 88:1012-1020,1010, Spatola, M.,et al, 2017
Arteriovenous Malformations of the Brain
NEJM 376:1859-1866, Solomon, R.A. & Connolly, E.S., 2017
Autoimmune Encephalitis: Pathophysiology and Imaging Review of an Overlooked Diagnosis
AJNR 38:1070-1078, Kelley, B.P.,et al, 2017
Intractable Epilepsy and Progressive Cognitive Decline in a Young Man
JAMA Neurol 74:737-740, Cohen, A.L.,et al, 2017
Clinicopathologic Conference, Advanced AIDS Complicated by HSV-1 Encephalopathy. Basal-Cell Carcinoma. Kaposis Sarcoma.
NEJM 376:2580-2589, Case 20-2017, 2017
An Older Man with Memory Impairment and Convulsions
BMJ 358:J2824, Zhao, X.,et al, 2017
CNS Posttransplant Lymphoproliferative Disorder
Neurol 89:e32-e37, Kesari, N.K.,et al, 2017
Subarachnoid Hemorrhage
NEJM 377:257-266, Lawton, M.T. & Vates, G.E., 2017
A Demure Teenager and Her Dystonic Foot
Neurol 89:e71-e75, Cullinane, P.W.,et al, 2017
Adult-Onset Leukoencephalopathy with Intracranial Calcifications and Cysts (Labrune Syndrome)
Neurol 88:e113-e114, Villar-Quiles, R.et al, 2017
A Woman in her 40s with Headache and New-Onset Seizures
JAMA Neurol 74:476-480, Graham, M.S.,et al, 2017
Neurological Autoantibody Prevalence in Epilepsy on Unknown Etiology
JAMA Neurol 74:397-402,384, Dubey, D.,et al, 2017
The Tadpole Pupil
JAMA Neurol 74:481, Aggarwal, K. & Hildebrand, G.D., 2017
Primary Angiitis of the Central Nervous System
Stroke 48:1248-1255, Boulouis, G.,et al, 2017
Clinicopathologic Conference, MELAS (mitochondrial encephalopathy, lactic acidosis, and stroke like episodes)
NEJM 376:1668-1678, CASE 13-2017, 2017
Recurrence Risk of Ictal Asystole in Epilepsy
Neurol 89:785-791, Hampel, K.G.,et al, 2017
A 57-year-old man with Unilateral Anosmia, Papilledema, and Meningismus
Neurol 89:e86-e90, Bradshaw, M.J.,et al, 2017
Neuroimaging Changes in Menkes Disease, Part 1
AJNR 38:1850-1857, Manara, R.,et al, 2017
Autoimmune Encephalitis: Pathophysiology and Imaging Review of an Overlooked Diagnosis
AJNR 38:1070-1078, Kelley, B.P.,et al, 2017
Central Nervous System Brucellosis Granuloma and White Matter Disease in Immunocompromised Patient
Emerg Infect Dis 23:978-981, Alqwaifly,M.,et al, 2017
Cysticercal Encephalitis: An Unusual Differential in the List of Encephalitis
IJCMR 3:2264-2266, Ajeet, S.,et al, 2016
Differential Diagnosis
Thoracic Key, Southerland,A.W.,et al, 2016
Central Nervous System Vasculitis in Rheumatoid Arthritis:A Case Report
JSM Arthritis 1:1005, Lagrutta,M.,et al, 2016
Chronic Herpes Simplex Type-1 Encephalitis with Intractable Epilepsy in an Immunosuppressed Patient
Infection 44:121-125, Laohathai, C.,et al, 2016
Severe Acute Hyponatremia as an Initial Presentation of Acute Intermittent Porphyria Triggered by a Subdermal Etonogestrel Implant
J Nephrol Renal Ther 2:1-4, Valente, J.R.,et al, 2016
Subarachnoid Hemorrhage
Medscape Aug, Becske, T. & Lutsep, H.L., 2016
Neonatal Abstinence Syndrome
NEJM 375:2468-2479, McQueen, K. & Murphy-Oikonen, J., 2016
Clinicopathologic Conference, Oligdendroglioma II/IV with IDH1 R132H mutation and codelation of 1p and 19q
NEJM 375:2381-2389, Case 38-206, 2016
A Woman with Intellectual Disability, Amenorrhoea, Seizures, and Balance Problems
JAMA Neurol 73:1494-1495, Hughes, A.J.C.,et al, 2016
Long-Term Treatment of Epilepsy with Everolimus in Tuberous Sclerosis
Neurol 87:2408-2415, Krueger, D.A.,et al, 2016
Cerebral Toxoplasmosis in an HIV-Negative Patient
Arch Clin Infect Dis 11:e30759, Arab-Mazar, Z.,et al, 2016
Spectrum of Imaging Appearances of Intracranial Cryptococcal Infection in HIV/AIDS Patients in the Anti-Retroviral Therapy Era
Clin Radiol 71:9-17, Offiah, C.E. & Naseer, A., 2016
NMDA-Receptor Encephalitis
DynaMed Plus Sept 2016, Rae-Grant, A.,et al, 2016
Tranexamic Acid-Associated Seizures: Causes and Treatment
Ann Neurol 79:18-26, Lecker, I.,et al, 2016
An 11-year-old Boy with Language Disorder and Epilepsy
Neurol 86:e48-e53, Dong, L. & Zhou, X., 2016
Faciobrachial Dystonic Seizures
Neurol 86:e60-e61, Schmerler, D.A.,et al, 2016
Leukodystrophy and Progressive Myoclonic Epilepsy Disclosing DRPLA
Neurol 86:e58-e59, Sgobbi de Souza, P.V.,et al, 2016
Validation of Clinicoradiological Criteria for the Diagnosis of Cerebral Amyloid Angiopathy-Related Inflammation
JAMA Neurol 73:197-202, Auriel, E.,et al, 2016