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abdominal reflex, absent

abducens nerve paralysis

abscess, spinal cord

achilles tendon, enlarged

acquired immunodeficiency syndrome

acquired immunodeficiency syndrome myelopathy

addiction, heroin-neurologic complications with

Addison's disease

adrenoleukodystrophy

adrenoleukodystrophy, adult onset

adrenoleukodystrophy, carrier

adrenomyeloneuropathy

adult polyglucosan body disease

advances in neurology

adverse drug reaction

agenesis of corpus callosum

Aicardi-Goutieres syndrome

alcohol injection

alcohol, neurologic complications with

Alexanders disease

Alexanders disease, adult onset

Alzheimer's disease

aminoacidopathies

amyloid plaques

amyotrophic lateral sclerosis

amyotrophic lateral sclerosis, bulbar

amyotrophic lateral sclerosis, atypical

amyotrophic lateral sclerosis, diagnosis of

amyotrophic lateral sclerosis, etiology of

amyotrophic lateral sclerosis, juvenile

amyotrophic lateral sclerosis, prognosis

amyotrophic lateral sclerosis, treatment of

anemia, megaloblastic

anesthesia, general

angiitis, granulomatous of CNS

angiitis, isolated of CNS

angiography, neurologic complications with

ankle reflex, absent

anterior spinal artery

antispasticity drugs

arteritis, temporal

asterixis, causes of

asterixis, unilateral

ataxia, cerebellar

ataxia, hereditary

ataxia, progressive

ataxia, sensory

ataxia, truncal

atherosclerosis, premature

atlanto-axial subluxation

atrioventricular block

auditory evoked brainstem potentials

autonomic dysfunction

autosomal rcessive spastic ataxia of Charlevoix-Saguenay

B 12 deficiency

bacterial infection

bacterial infection, CNS

basal ganglia, calcification of

basal ganglia, lesion of

basal ganglia, lesion, bilateral

behavioral disorder

Behcet's syndrome

bladder dysfunction

blood dyscrasias, neurologic findings with

blood transfusion

bone marrow transplantation

brainstem, atrophy

brainstem, dysfunction

brainstem, lesion of

Brown Sequard syndrome

brucellosis, nervous system involvement with

bulbar palsy, progressive

calcification, intracranial

carotid angiogram

CAT scan, abnormal

CAT scan, demyelinating disease

CAT scan, myelogram with

CAT scan, serial

CAT scan, spinal cord

CAT scan, spine

cavernous hemangioma

central nervous system, infection of

cerebellar ataxia, children

cerebellar ataxia, hereditary

cerebellar ataxia, primary

cerebellar atrophy, primary

cerebellar degeneration

cerebellar lesion

cerebellar plaques, amyloid

cerebellar vermis

cerebral cortical atrophy

cerebrospinal fluid

cerebrospinal fluid, abnormal

cerebrospinal fluid, amonia

cerebrospinal fluid, culture of, viral

cerebrospinal fluid, elevated protein of

cerebrospinal fluid, gammaglobulin of

cerebrospinal fluid, glutamine

cerebrospinal fluid, lactic acid concentration

cerebrospinal fluid, oligoclonal IgG in

cerebrotendinous xanthomatosis

cerebrovascular accident

cervical spine injury, compression

cervical spondylosis

Charcot-Marie-Tooth

chilbran skin lesions

chorea, causes of

chorea, familial

choreoathetosis

chromosomal abnormality

chronic progressive external ophthalmoplegia

Clinical Pathologic Conference(C.P.C.)

clubfoot as related to neurologic disease

color vision, impaired

compression fracture

congenital malformation

congenital malformation, non CNS

cornea, opacity of

corpus callosum

corpus callosum, atrophy of

corpus callosum, thinning

cortical blindness

cranial neuropathy

cranial neuropathy, multiple

crossed adductor reflex

crying, pathologic

cultured skin fibroblasts

deafness, bilateral progressive vs.unilateral acute

deafness, unilateral

decerebrate posture

deep gray nuclei

degenerative diseases of CNS

delay in diagnosis

dementia, childhood

dementia, familial

dementia, presenile

dementia, subcortical

dementia, thalamic

demyelinating disease

dentate nuclei, lesion of

developmental milestones

developmental milestones, loss of

developmental retardation

diagnostic criteria

differential diagnosis

digits, abnormal

distal muscle atrophy

distal muscle weakness

Dravet syndrome

drug abuse, inhalation

drug abuse, neurologic complications of

dystonia, children

ears of the Lynx MR sign

electrical sensation

electroencephalogram

electroencephalogram, abnormalities of

emergencies, neurologic

emotional lability

encephalopathy, metabolic

enzyme, muscle disease

epicanthal folds

epidemiology of neurology

epileptic encephalopathy

erythema migrans

evoked potentials

exome sequencing

facial anomalies

facial appearance, abnormal

facial nerve palsy

facial nerve palsy, bilateral

facial weakness

facial weakness, bilateral

failure to thrive

FARS2 deficiency

fatal familial insomnia

fatty acid, elevated plasma content

feeding disorder

fetal alcohol syndrome

fine motor function, impaired

finger nose finger test

fistula, arterio-venous, dural

Friedreich's ataxia

galactocerebrosidase

gamma amino butyric acid-mimetic drug

genetic counselling

genetic diagnosis, prenatal

genetic linkage

genetic neurologic disorders

genetic screening

genetic testing

geographic location

Gerstmann-Straussler-Scheinker disease

globus pallidus

globus pallidus, lesion of

globus pallidus, lesion of, bilateral

gram negative rod

granulomatosis with polyangiitis

granulomatous disease

Hallervorden Spatz disease

hearing problems in children

heart block, complete

hemangioma, vertebral

hematopoietic tissue, extramedullary

hematuria, microscopic

hemoglobin abnormality, neurologic complications of

hepatic encephalopathy

hepatic failure

hepatolenticular degeneration, non-Wilsonian

herpes virus infection

high arched feet

Horner's syndrome

human herpesvirus 6

human immunodeficiency virus type 1

human T-lymphotropic virus type I(HTLV-I)

human T-lymphotropic virus type II(HTLV-II)

hydrocephalus, congenital

hydrocephalus, fetal

hydrocephalus, intrauterine

hyperammonemic encephalopathy

hyperparathyroidism

hyperpigmentation of skin

hyperpyrexia, CNS disorder causing

hyperthyroidism

hypomyelination

hypopigmentation of skin

hypothalamus, disturbance of

hypothermia, causes of

iatrogenic neurologic disorders

immunosuppression

immunosuppressive agents

inborn errors of metabolism

inclusion bodies

incontinence, fecal

intellectual deficit

intellectual deficit, treatable causes of

intellectual deterioration

intelligence quotient

interferon alpha

intracerebral hemorrhage

intrathecal antispasticity drugs

intrinsic hand muscles, wasting of

Jamaica ginger paralysis

jaw jerk, abnormal

Krabbe's disease

kyphoscoliosis, neurologic causes of

lactic acidemia

laughing, pathologic

leg weakness, bilateral

Leigh's disease

Leigh's disease, adult variety

lenticular nucleus, lesion of, bilateral

leukemia, neurologic findings assoc.with

leukocyte enzyme abnormality

leukoencephalopathy

leukoencephalopathy, differential diagnosis

Lhermitte's sign

life expectancy

lymphadenopathy

lymphocytic pneumonitis

lymphoma involving CNS

lymphomatoid granulomatosis

magnetic stimulation

magnetic stimulation, brain

malformation, CNS, congenital

malformation, vascular

malformation, vascular, treatment of

medulla oblongata, lesion of

meningeal enhancement

meningitis, brucellosis

meningitis, CSF cell count-normal

meningomyelitis

meningovascular syphilis

mental retardation

metabolic disorder, primary

metachromatic leukodystrophy

metachromatic leukodystrophy, adult onset

methylmalonic aciduria

middle cerebellar peduncle

middle cerebellar peduncle, lesion, bilateral

mitochondrial disease

molecular genetics

mononeuropathy multiplex

Morquio syndrome

motor neuron disease

movement disorder

movement disorder, extrapyramidal

MRI, contrast enhanced

MRI, demyelinating disease

MRI, false negative

MRI, high signal foci on

MRI, high signal intensity of basal ganglia

MRI, spinal cord

MRI, spinal cord, increased intramedullary cord signal

MRI, T1 weighted high signal foci

MRI, target sign

mucopolysaccharidoses

multiple sclerosis

multiple sclerosis, chronic progressive

multiple sclerosis, diagnosis of

multiple sclerosis, differential diagnosis of

multiple sclerosis, misdiagnosis

multiple sclerosis, prognosis

multiple sclerosis, spinal form

multiple sclerosis, treatment of

multiple system atrophy

muscle twitching

muscle wasting, diffuse

muscle weakness

myelitis, longitudinal

myelitis, transverse

myelogram, thoracic

myeloneuropathy

myelopathy, chronic progressive

myelopathy, hepatic

myelopathy, vacuolar

myeloradiculopathy

myoclonic jerks

myoclonus, epilepsy

Native Americans

nerve conduction studies

nerve root enhancement

neurocutaneous disease

neuroendocrinology

neurogenic bladder

neuroichthyosis

neurologic complications of, systemic disease

neurologic disease

neurologic disease, diagnoses of

neurologic examination

neurologic signs

neurologic symptoms

neuronal ceroid-lipofuscinosis

neuropathology, brain

neuropathy, demyelinating

neuropathy, hereditary peripheral

neuropathy, peripheral

neuropathy, sensory

neuropathy, vasculitic, systemic

next-generation sequencing

night blindness

nystagmus, dissociated

nystagmus, rotary

nystagmus, vertical

occupational neurologic disorders

ocular motility, disorders of

oculodentodigital dysplasia

ophthalmoplegia

ophthalmoplegia, progressive external

opportunistic infection

optic atrophy, hereditary

optic nerve, lesion of

oral ulcerations

pain, abdominal

palatal myoclonus

paraparesis, familial spastic

paraparesis, familial spastic, classification

paraparesis, familial spastic, variants

paraparesis, painful

paraparesis, spastic

paraparesis, spastic, tropical

parathyroid adenoma

Parkinson disease

Parkinsonism multiple-system atrophy

Parkinsonism syndrome

Pelizaeus Merzbacher

pernicious anemia

peroneal nerve palsy

peroneal nerve, lesion of

peroxisomal disease

personality change

phenylketonuria

phenylketonuria, adult onset

pleocytosis of cerebrospinal fluid

poison, organophosphate

polycythemia, primary

polyglucosan body

polyglucosan body disease

polymerase chain reaction

polyneuropathy, familial

pons, lesion of

portal caval shunt

posterior longitudinal ligament, ossification of

precocious puberty

prenatal diagnosis by amniocentesis

primary lateral sclerosis

prisoners of war, neurologic complications in

progressive neurologic disorder

pseudobulbar palsy

pseudomonas aeruginosa

psychiatric disorder

psychiatric problems in neurologic disorders

psychological testing

psychological testing, neurologic problems

psychomotor retardation

pulmonary infiltrates

pursuit eye movements, abnormal

pyramidal tract

pyramidal tract dysfunction

pyruvate metabolism, abnormality of

radiation encephalopathy, delayed

radiation therapy, CNS treatment and complications with

Raynaud's phenomenon

release phenomena

respiratory failure

reticulum cell sarcoma

retinitis pigmentosa

reversible neurologic disorder

rheumatoid arthritis

rheumatoid arthritis, neurologic complications of

Rosenthal fibers

sarcoidosis, CNS

Schilder's disease

sclerae, hyperpigmented

scleroderma, neurologic involvement with

sea-blue histiocytes

sedimentation rate, elevated

seizure, children

seizure, familial

seizure, febrile

seizure, intractable

seizure, neonatal

seizure, tonic-clonic

sensorineural hearing loss

serologic testing

serologic testing of cerebrospinal fluid

sickle cell disease

Sjogren-Larsson syndrome

Sjogren's syndrome

skin, darkening of

skin, lesions in neurologic disorders

sleep pathology and physiology

sodium channel dysfunction

somatosensory evoked potentials

spastic diplegia

spastic paraplegia, type 11

spastic paraplegia, type 15

spastic paraplegia, type 7

spasticity, treatment of

speech disorder

speech disorder, childhood

speech, loss of

spinal cord, biopsy

spinal cord, cervical

spinal cord, compression of

spinal cord, enlargement

spinal cord, herniation

spinal cord, infarction of

spinal cord, injury of

spinal cord, injury, management of

spinal cord, ischemic lesion of

spinal cord, lesion of

spinal cord, neoplasm

spinal cord, neoplasm, extramedullary

spinal cord, neoplasm, meningioma

spinal cord, pathologic exam of

spinal cord, vascular disorders Affecting

spinal cord, vascular malformation of

spinal xanthomatosis

spinocerebellar ataxia type 1

spinocerebellar ataxia type 3/Machado Joseph disease

spinocerebellar degeneration

spirochete infection

spongy degeneration of brain

startle reaction

status epilepticus

steroid therapy, CNS treatment and complications with

striatonigral degeneration

striatonigral degeneration, infantile

striopallidodentate calcifications, familial idiopathic

subacute sclerosing panencephalitis(S.S.P.E.)Dawson's disease

subarachnoid hemorrhage

subcortical U fibers

substantia nigra

symmetric brain lesions

syphilis, meningomyelitis

syphilis, neurologic complications with

systemic illness

teeth, abnormal

tendon, enlarged

testicular atrophy

thalamus, lesion of

thrombocytopenia

tongue, atrophy

tongue, fasciculations of

tongue, impaired movements of

tongue, weakness

toxins, nervous system

transposition of the great vessels

treatment of neurologic disorder

tremor, intention

trinucleotide repeats

tuberculoma of CNS

tuberculosis, spinal

tuberous sclerosis

urinary frequency

urinary incontinence

urinary urgency

vibratory sensation, abnormal

viral infection

viral infection, CNS

viral isolation

visual acuity, decreased

visual evoked response

walking, difficulty with

weakness, progressive

Werdnig-Hoffman disease

Werner's syndrome

Western immunoblot test

white matter disease

wide based gait

xanthoma, tendon

x-linked hydrocephalus

Showing articles 1650 to 1700 of 2262 << Previous Next >>

Criteria for Establishing the Validity of Genetic Recombination in Myotonic Dystrophy
Neurol 39:420-421, Griggs,R.C.,et al, 1989

Mitochondrial DNA and Genetic Disease
Editorial, Lancet 1:250-2511989., , 1989

Electroencephalographic Abnormalities in Human T-Cell Lymphotropic Virus Type I-Associated Myelopathy
Arch Neurol 46:513-516, Yonenaga,Y.,et al, 1989

HTLV-I Polymyositis in a Patient Also Infected with the Human Immunodeficiency Virus
NEJM 320:992-995, Wiley,C.A.,et al, 1989

Shy-Drager Syndrome and Human T-Lymphotropic Virus Type I Infection
Ann Neurol 25:420-421, Kano,M.,et al, 1989

Human T-Lymphotropic Virus Type I-Associated Myelopathy Presenting as Spinocerebellar Syndrome
Ann Neurol 25:419-420, Iwasaki,Y.,et al, 1989

Hereditary Long Q-T Syndrome Presenting as Epilepsy:Electroencephalography Laboratory Diagnosis
Ann Neurol 25:514-516, Gospe,S.M.&Choy,M., 1989

Problems in Genetic Prediction for Huntington's Disease
Lancet 2:601-603, Morris,M.J.,et al, 1989

Uptake of Presymptomatic Predictive Testing for Huntington's Disease
Lancet 2:603-605, Craufurd,D.,et al, 1989

Caze Distractibility in Wilson's Disease
Ann Neurol 25:415-417, Lennox,G.&Jones,R., 1989

Homing in on Wilson's Disease
Editorial, Lancet 1:822-8231989., , 1989

Diagnosis of Gerstmann-Straussler Syndrome in Familial Dementia with Prion Protein Gene Analysis
Lancet 2:15-17, Collinge,J.,et al, 1989

Ethanol and the Nervous System
NEJM 321:442-454, Charness,M.E.,et al, 1989

Primary Progressive Cerebellar Ataxia
Neuroradiology 31:16-18, Bradac,G.B.,et al, 1989

Concurrence of Multiple Sclerosis and Inflammatory Bowel Disease
NEJM 321:762-763, Sadovnick,A.D.,et al, 1989

Neurofibromatosis and Other Disorders Among Children with CNS Tumors and Their Families
Neurol 39:487-492, Baptiste,M.,et al, 1989

The Diagnosis of Neurofibromatosis-1 in the Child Under the Age of 6 Years
Am J Dis Child 143:717-719, Obringer,A.C.,et al, 1989

Refsum Disease
In Rowland's Merritt's Textbk of Neurology, Lea & Febiger, Phila, 8thEd, p. 509, Menkes,J.H., 1989

Congenital AIDS:Review of Neurological Problems
Child's Nerv Syst 5:9-11, Curles,R.G., 1989

Intramedullary Cavernous Angioma with Trigeminal Neuralgia:A Case Report and Reivew of the Literature
Neurosurgery 25:97-101, Saito,N.,et al, 1989

Renal Replacement Treatment in Patients with Spina Bifida or Spinal Cord Injury
BMJ 299:1506, Muralikrishna,G.S.,et al, 1989

Thyrotoxic Periodic Paralysis
Arch Int Med 149:2597-2600, Kelley,D.E.,et al, 1989

Peripheral Neuropathy in Amyotrophic Chorea-Acanthocytosis
Ann Neurol 26:583-587, Vista,G.,et al, 1989

REcurrent Familial Brachial Plexus Palsies as the ONly Clinical Expression of'Tomaculous'Neuropathy
Eur Neurol 29:61-66, Martinelli,P.,et al, 1989

Friedreich Ataxia
In Rowland, L. P. Merritt's Textbook of Neurology, 8th Ed, Lea & Febiger, Phila, Ch 13, p627, Rosenberg,R.N., 1989

Follow-up and Diagnostic Reappraisal of 75 Patients with Leber's Congenital Amaurosis
Am J Ophthalmol 107:624-631, Lambert,S.R.,et al, 1989

DNA Restriction Fragment Length Polymorphisms in Diff Dx of Genetic Disease:Appl in Neuromusc Dis
Hum Genet 82:55-58, Defesche,J.C.,et al, 1989

Paroxysmal Cerebellar Ataxia
Aust NZ J Med 19:113-117, Feeney,G.F.&Boyle,R.S., 1989

Cerebral Infarction in Hereditary Spherocytosis
Stroke 20:1755-1756, van Hilten,J.J.,et al, 1989

Emery-Dreifuss Muscular Dystrophy:Disease Spectrum and Differential Diagnosis
Neuropediatrics 19:62-71, Voit,T.,et al, 1988

The Lambert-Eaton Myasthenic Syndrome, A Review of 50 Cases
Brain 111, 577-5961988., O'Neill,J.H.,et al, 1988

Paraplegia and Quadriplegia after Intrathecal Chemotherapy
Arch Phys Med Rehabil 69:1054-1056, Werner,R.A., 1988

Retinitis Pigmentosa
Surv Ophthalmol 33:137-177, Pagon,R.A., 1988

Hereditary Dentatorubral-Pallidoluysian Atrophy:Clinical and Pathologic Variants in a Family
Neurol 38:1065-1070, Takahashi,H.,et al, 1988

McArdle's Disease:Biochemical and Molecular Genetic Studies
Ann Neurol 24:774-781, Servidei,S.,et al, 1988

Meningitis in Familial Mediterranean Fever
Am J Med 85:715-717, Schwabe,A.D., 1988

Cauda Equina Syndrome Secondary to Disseminated Zygomycosis
JAMA 260:3638-3640, Rozich,J.,et al, 1988

Anderson-Fabray Disease, A Commonly Missed Diagnosis
BMJ 297:872-873, Morgan,S.H.&Crawfurd,M., 1988

Hysterical Conversion Reactions Mimicking Neurological Disease
Am J Dis Child 142:1203-1206, Bangash,I.H.,et al, 1988

Familial Oculoleptomeningeal Amyloidosis, Report of a New Family with Unusual Features
Arch Neurol 45:1118-1122, Uitti,R.J.,et al, 1988

Risk of Brain Infarction in Familial Hypercholesterolemia
Stroke 19:1097-1100, Kaste,M.&Koivisto,P., 1988

Mutation in Cystatin C Gene Causes Hereditary Brain Hemorrhage
Lancet 2:603-604, Palsdottir,A.,et al, 1988

Rett Syndrome:Natural History and Management
Pediatrics 82:1-10, Moeschler,J.B.,et al, 1988

Predictive Testing for Huntington's Disease with Use of a Linked DNA Marker
NEJM 318:535-542, Meissen,G.J.,et al, 1988

Improvement of Cerebral CT Abnor Following Liver Transplant in a Patient with Wilson Disease
J Comput Assist Tomogr 12:138-149, Rothfus,W.E.,et al, 1988

Efficacy of Alprazolam for Essential Tremor
Neurol 38:241-243, Huber,S.J.&Paulson,G.W., 1988

Retroviruses in the Nervous System:Neurological Involv in AIDS
Neurological Disorders Assoc with HTLV-I, NIH Symposium (Suppl) , Ann Neurol 23:S1-S2178., , 1988

Brain Abscess:Association with Pulmonary Arteriovenous Fistula and Hereditary Hemorrhagic Telangiectasia:3 Cases
Am J Med 85:718-720, Gelfand,M.S.,et al, 1988

Portosystemic Encephalopathy in Hereditary Hemorrhagic Telangiectasia
Am J Med 85:858-860, Fagel,W.J.,et al, 1988

The Molecular Genetic Revolution, Its Impact on Clinical Neurology
Arch Neurol 45:1366-1376, Payne,C.S.&Roses,A.D., 1988

Showing articles 1650 to 1700 of 2262 << Previous Next >>