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abdominal reflex, absent

abducens nerve paralysis

abscess, spinal cord

achilles tendon, enlarged

acquired immunodeficiency syndrome

acquired immunodeficiency syndrome myelopathy

addiction, heroin-neurologic complications with

Addison's disease

adrenoleukodystrophy

adrenoleukodystrophy, adult onset

adrenoleukodystrophy, carrier

adrenomyeloneuropathy

adult polyglucosan body disease

advances in neurology

adverse drug reaction

agenesis of corpus callosum

Aicardi-Goutieres syndrome

alcohol injection

alcohol, neurologic complications with

Alexanders disease

Alexanders disease, adult onset

Alzheimer's disease

aminoacidopathies

amyloid plaques

amyotrophic lateral sclerosis

amyotrophic lateral sclerosis, bulbar

amyotrophic lateral sclerosis, atypical

amyotrophic lateral sclerosis, diagnosis of

amyotrophic lateral sclerosis, etiology of

amyotrophic lateral sclerosis, juvenile

amyotrophic lateral sclerosis, prognosis

amyotrophic lateral sclerosis, treatment of

anemia, megaloblastic

anesthesia, general

angiitis, granulomatous of CNS

angiitis, isolated of CNS

angiography, neurologic complications with

ankle reflex, absent

anterior spinal artery

antispasticity drugs

arteritis, temporal

asterixis, causes of

asterixis, unilateral

ataxia, cerebellar

ataxia, hereditary

ataxia, progressive

ataxia, sensory

ataxia, truncal

atherosclerosis, premature

atlanto-axial subluxation

atrioventricular block

auditory evoked brainstem potentials

autonomic dysfunction

autosomal rcessive spastic ataxia of Charlevoix-Saguenay

B 12 deficiency

bacterial infection

bacterial infection, CNS

basal ganglia, calcification of

basal ganglia, lesion of

basal ganglia, lesion, bilateral

behavioral disorder

Behcet's syndrome

bladder dysfunction

blood dyscrasias, neurologic findings with

blood transfusion

bone marrow transplantation

brainstem, atrophy

brainstem, dysfunction

brainstem, lesion of

Brown Sequard syndrome

brucellosis, nervous system involvement with

bulbar palsy, progressive

calcification, intracranial

carotid angiogram

CAT scan, abnormal

CAT scan, demyelinating disease

CAT scan, emission, abnormal

CAT scan, myelogram with

CAT scan, serial

CAT scan, spinal cord

CAT scan, spine

cavernous hemangioma

central nervous system, infection of

cerebellar ataxia, children

cerebellar ataxia, hereditary

cerebellar ataxia, primary

cerebellar atrophy, primary

cerebellar atrophy, secondary

cerebellar degeneration

cerebellar lesion

cerebellar plaques, amyloid

cerebellar vermis

cerebral cortical atrophy

cerebrospinal fluid

cerebrospinal fluid, abnormal

cerebrospinal fluid, amonia

cerebrospinal fluid, culture of, viral

cerebrospinal fluid, elevated protein of

cerebrospinal fluid, gammaglobulin of

cerebrospinal fluid, glutamine

cerebrospinal fluid, lactic acid concentration

cerebrospinal fluid, oligoclonal IgG in

cerebrotendinous xanthomatosis

cerebrovascular accident

cervical spine injury, compression

cervical spondylosis

Charcot-Marie-Tooth

chenodeoxycholic acid

chilbran skin lesions

chorea, causes of

chorea, familial

choreoathetosis

chromosomal abnormality

chronic progressive external ophthalmoplegia

Clinical Pathologic Conference(C.P.C.)

clubfoot as related to neurologic disease

color vision, impaired

compression fracture

congenital malformation

congenital malformation, non CNS

cornea, opacity of

corpus callosum

corpus callosum, atrophy of

corpus callosum, thinning

cortical blindness

cranial neuropathy

cranial neuropathy, multiple

crossed adductor reflex

crying, pathologic

cultured skin fibroblasts

deafness, bilateral progressive vs.unilateral acute

deafness, unilateral

decerebrate posture

deep gray nuclei

degenerative diseases of CNS

delay in diagnosis

dementia, childhood

dementia, familial

dementia, presenile

dementia, subcortical

dementia, thalamic

demyelinating disease

dentate nuclei, lesion of

developmental milestones

developmental milestones, loss of

developmental retardation

diagnostic criteria

differential diagnosis

digits, abnormal

distal muscle atrophy

distal muscle weakness

Dravet syndrome

drug abuse, inhalation

drug abuse, neurologic complications of

dystonia, children

ears of the Lynx MR sign

electrical sensation

electroencephalogram

electroencephalogram, abnormalities of

emergencies, neurologic

emotional lability

encephalopathy, metabolic

enzyme, muscle disease

epicanthal folds

epidemiology of neurology

epileptic encephalopathy

erythema migrans

evoked potentials

exome sequencing

eye movement, disorders of

facial anomalies

facial appearance, abnormal

facial nerve palsy

facial nerve palsy, bilateral

facial weakness

facial weakness, bilateral

failure to thrive

FARS2 deficiency

fatal familial insomnia

fatty acid, elevated plasma content

feeding disorder

fetal alcohol syndrome

fine motor function, impaired

finger nose finger test

fistula, arterio-venous, dural

Friedreich's ataxia

galactocerebrosidase

gamma amino butyric acid-mimetic drug

genetic counselling

genetic diagnosis, prenatal

genetic linkage

genetic neurologic disorders

genetic screening

genetic testing

geographic location

Gerstmann-Straussler-Scheinker disease

globus pallidus

globus pallidus, lesion of

globus pallidus, lesion of, bilateral

gram negative rod

granulomatosis with polyangiitis

granulomatous disease

Hallervorden Spatz disease

hearing loss, bilateral

hearing problems in children

heart block, complete

hemangioma, vertebral

hematopoietic tissue, extramedullary

hematuria, microscopic

hemoglobin abnormality, neurologic complications of

hepatic encephalopathy

hepatic failure

hepatolenticular degeneration, non-Wilsonian

herpes virus infection

high arched feet

Horner's syndrome

human herpesvirus 6

human immunodeficiency virus type 1

human T-lymphotropic virus type I(HTLV-I)

human T-lymphotropic virus type II(HTLV-II)

hydrocephalus, congenital

hydrocephalus, fetal

hydrocephalus, intrauterine

hyperammonemic encephalopathy

hyperparathyroidism

hyperpigmentation of skin

hyperpyrexia, CNS disorder causing

hyperthyroidism

hypomyelination

hypopigmentation of skin

hypothalamus, disturbance of

hypothermia, causes of

iatrogenic neurologic disorders

immunosuppression

immunosuppressive agents

inborn errors of metabolism

inclusion bodies

incontinence, fecal

intellectual deficit

intellectual deficit, treatable causes of

intellectual deterioration

intelligence quotient

interferon alpha

internal capsule

intracerebral hemorrhage

intrathecal antispasticity drugs

intrinsic hand muscles, wasting of

Jamaica ginger paralysis

jaw jerk, abnormal

Krabbe's disease

kyphoscoliosis, neurologic causes of

lactic acidemia

laughing, pathologic

leg weakness, bilateral

Leigh's disease

Leigh's disease, adult variety

lenticular nucleus, lesion of, bilateral

leukemia, neurologic findings assoc.with

leukocyte enzyme abnormality

leukoencephalopathy

leukoencephalopathy, differential diagnosis

Lhermitte's sign

life expectancy

lymphadenopathy

lymphocytic pneumonitis

lymphoma involving CNS

lymphomatoid granulomatosis

magnetic stimulation

magnetic stimulation, brain

malformation, CNS, congenital

malformation, vascular

malformation, vascular, treatment of

medulla oblongata, lesion of

meningeal enhancement

meningitis, brucellosis

meningitis, CSF cell count-normal

meningomyelitis

meningovascular syphilis

mental retardation

metabolic disorder, primary

metachromatic leukodystrophy

metachromatic leukodystrophy, adult onset

methylmalonic aciduria

middle cerebellar peduncle

middle cerebellar peduncle, lesion, bilateral

mitochondrial disease

molecular genetics

mononeuropathy multiplex

Morquio syndrome

motor neuron disease

movement disorder

movement disorder, extrapyramidal

MRI, contrast enhanced

MRI, demyelinating disease

MRI, false negative

MRI, high signal foci on

MRI, high signal intensity of basal ganglia

MRI, spinal cord

MRI, spinal cord, increased intramedullary cord signal

MRI, T1 weighted high signal foci

MRI, target sign

mucopolysaccharidoses

multiple sclerosis

multiple sclerosis, chronic progressive

multiple sclerosis, diagnosis of

multiple sclerosis, differential diagnosis of

multiple sclerosis, misdiagnosis

multiple sclerosis, prognosis

multiple sclerosis, spinal form

multiple sclerosis, treatment of

multiple system atrophy

muscle twitching

muscle wasting, diffuse

muscle weakness

myelitis, longitudinal

myelitis, transverse

myelogram, thoracic

myeloneuropathy

myelopathy, chronic progressive

myelopathy, hepatic

myelopathy, vacuolar

myeloradiculopathy

myoclonic jerks

myoclonus, epilepsy

Native Americans

nerve conduction studies

nerve root enhancement

neurocutaneous disease

neuroendocrinology

neurogenic bladder

neuroichthyosis

neurologic complications of, systemic disease

neurologic disease

neurologic disease, diagnoses of

neurologic examination

neurologic signs

neurologic symptoms

neuronal ceroid-lipofuscinosis

neuropathology, brain

neuropathy, demyelinating

neuropathy, hereditary peripheral

neuropathy, peripheral

neuropathy, sensory

neuropathy, vasculitic, systemic

next-generation sequencing

night blindness

nystagmus, dissociated

nystagmus, rotary

nystagmus, vertical

occupational neurologic disorders

ocular motility, disorders of

oculodentodigital dysplasia

ophthalmoplegia

ophthalmoplegia, progressive external

opportunistic infection

optic atrophy, hereditary

optic nerve, lesion of

oral ulcerations

pain, abdominal

palatal myoclonus

paraparesis, familial spastic

paraparesis, familial spastic, classification

paraparesis, familial spastic, variants

paraparesis, painful

paraparesis, spastic

paraparesis, spastic, tropical

parathyroid adenoma

Parkinson disease

Parkinsonism multiple-system atrophy

Parkinsonism syndrome

Pelizaeus Merzbacher

pernicious anemia

peroneal nerve palsy

peroneal nerve, lesion of

peroxisomal disease

personality change

phenylketonuria

phenylketonuria, adult onset

pleocytosis of cerebrospinal fluid

poison, organophosphate

polycythemia, primary

polyglucosan body

polyglucosan body disease

polymerase chain reaction

polyneuropathy, familial

pons, lesion of

portal caval shunt

posterior longitudinal ligament, ossification of

precocious puberty

prenatal diagnosis by amniocentesis

primary lateral sclerosis

prisoners of war, neurologic complications in

progressive neurologic disorder

pseudobulbar palsy

pseudomonas aeruginosa

psychiatric disorder

psychiatric problems in neurologic disorders

psychological testing

psychological testing, neurologic problems

psychomotor retardation

pulmonary infiltrates

pursuit eye movements, abnormal

pyramidal tract

pyramidal tract dysfunction

pyruvate metabolism, abnormality of

radiation encephalopathy, delayed

radiation therapy, CNS treatment and complications with

Raynaud's phenomenon

release phenomena

respiratory failure

reticulum cell sarcoma

retinitis pigmentosa

reversible neurologic disorder

rheumatoid arthritis

rheumatoid arthritis, neurologic complications of

Rosenthal fibers

sarcoidosis, CNS

Schilder's disease

sclerae, hyperpigmented

scleroderma, neurologic involvement with

sea-blue histiocytes

sedimentation rate, elevated

seizure, children

seizure, familial

seizure, febrile

seizure, intractable

seizure, neonatal

seizure, tonic-clonic

sensorineural hearing loss

serologic testing

serologic testing of cerebrospinal fluid

sickle cell disease

Sjogren-Larsson syndrome

Sjogren's syndrome

skin, darkening of

skin, lesions in neurologic disorders

sleep pathology and physiology

sodium channel dysfunction

somatosensory evoked potentials

spastic diplegia

spastic paraplegia, type 11

spastic paraplegia, type 15

spastic paraplegia, type 7

spasticity, treatment of

speech disorder

speech disorder, childhood

speech, loss of

spinal cord, biopsy

spinal cord, cervical

spinal cord, compression of

spinal cord, enlargement

spinal cord, herniation

spinal cord, infarction of

spinal cord, injury of

spinal cord, injury, management of

spinal cord, ischemic lesion of

spinal cord, lesion of

spinal cord, neoplasm

spinal cord, neoplasm, extramedullary

spinal cord, neoplasm, meningioma

spinal cord, pathologic exam of

spinal cord, vascular disorders Affecting

spinal cord, vascular malformation of

spinal xanthomatosis

spinocerebellar ataxia type 1

spinocerebellar ataxia type 3/Machado Joseph disease

spinocerebellar degeneration

spirochete infection

spongy degeneration of brain

startle reaction

status epilepticus

steroid therapy, CNS treatment and complications with

striatonigral degeneration

striatonigral degeneration, infantile

striopallidodentate calcifications, familial idiopathic

subacute sclerosing panencephalitis(S.S.P.E.)Dawson's disease

subarachnoid hemorrhage

subcortical U fibers

substantia nigra

symmetric brain lesions

syphilis, meningomyelitis

syphilis, neurologic complications with

systemic illness

teeth, abnormal

tendon, enlarged

testicular atrophy

thalamus, lesion of

thrombocytopenia

tongue, atrophy

tongue, fasciculations of

tongue, impaired movements of

tongue, weakness

toxins, nervous system

transposition of the great vessels

treatment of neurologic disorder

tremor, intention

trinucleotide repeats

tuberculoma of CNS

tuberculosis, spinal

tuberous sclerosis

urinary frequency

urinary incontinence

urinary urgency

vibratory sensation, abnormal

viral infection

viral infection, CNS

viral isolation

visual acuity, decreased

visual evoked response

walking, difficulty with

weakness, progressive

Werdnig-Hoffman disease

Werner's syndrome

Western immunoblot test

white matter disease

wide based gait

xanthoma, tendon

x-linked hydrocephalus

Showing articles 1800 to 1850 of 2292 << Previous Next >>

Cervicomedullary Compression in Young Patients with Achondroplasia:Value of Neurologic & Respiratory Eval
J Pediatr 110:522-530, Reid,C.S.,et al, 1987

False Negative Results in Patients with fra (X) (q) Mental Retardation Taking Oral Vitamin Supplements
NEJM 316:1093, Froster-Iskenius,U.,et al, 1987

Chronic Muscle Weakness Caused by Borrelia Burgdorferi Meningoradiculitis
Ann Neurol 22:389-392, Wokke,J.H.J.,et al, 1987

Cerebral Ventricular Dilation in Congenital Myotonic Dystrophy
J Pediatr 111:372-376, Regev,R.,et al, 1987

MELAS Syndrome Involving a Mother & Two Children
Arch Neurol 44:971-973, Driscoll,P.F.,et al, 1987

Central Core Disease, Clinical Features in 13 Patients
Medicine 66:389-396, Shuaid,A.,et al, 1987

Neurofibromatosis
Editorial, Lancet 1:663-6641987., , 1987

Renal Cell Carcinoma in von Hippel-Lindau Syndrome
Am J Med 82:236-238, Malek,R.S.,et al, 1987

Adrenoleukodystrophy:Dietary Oleic Acid Lowers Hexacosanoate Levels
Ann Neurol 21:230-231, 232-2391987., Rizzo,W.B.,et al, 1987

A New Dietary Therapy for Adrenoleukodystrophy:Biochemical & Preliminary Clinical Results in 36 Patients
Ann Neurol 21:230-231, 240-2491987., Moser,A.B.,et al, 1987

Evidence That the Gene for Tuberous Sclerosis is on Chromosome 9
Lancet 1:659-661, Fryer,A.E.,et al, 1987

Clinical Assessment of 31 Patients with Wilson's Disease, Correlations with Struct. Changes on MRI
Arch Neurol 44:365-370, Starosta-Rubinstein,S.,et al, 1987

Familial Occurrence of Spontaneous Dissection of the Internal Carotid Artery
Stroke 18:246-251, Mokri,B.,et al, 1987

Cerebral Amyloid Angiopathy, A Critical Review
Stroke 18:311-324, Vinters,H.V., 1987

Caffeine & Tremor
Neurol 37:169-172, Koller,W.,et al, 1987

Spinal Cord Compression Induced by Steroid Therapy:CT Findings
J Comput Assist Tomogr 11:245-247, Jungreis,C.A.&Cohen,W.A., 1987

Cervical Cord Compression Due to Extension of a Papillary Thyroid Carcinoma
Am J Med 82:156-158, Ginsberg,J.,et al, 1987

Prenatal Diagnosis & Detection of Carriers with DNA Probes in Duchenne's Muscular Dystrophy
NEJM 316:985-993, 1018-10201987., Darras,B.T.,et al, 1987

Tourette Syndrome
Editorial, Lancet 1:3081987., , 1987

Dementia of the Alzheimer Type:Clinical & Family Study of 22 Twin Pairs
Neurol 37:359-363, Nee,L.E.,et al, 1987

Genetic Linkage in Neurologic Diseases
Editorial, NEJM 316:1018-10201987., Martin,J.B., 1987

Tropical Spastic Paraparesis Associated with Human T Lymphotropic Virus Type I in an East African Naturalised in Sweden
BMJ 295:1380-1381, Ryberg,B.,et al, 1987

The Aetiology of Mirror Writing:A New Hypothesis
JNNP 50:1572-1578, Tashiro,K.,et al, 1987

Hereditary Neuropathy with Liability to Pressure Palsies
In Handbk of Clin Neurol, Elsevier Sci Publ Co, NY 51:551-562987., Cherry,S.&Mayer,R.F., 1987

Facioscapulohumeral Dystrophy, in Myology, Basic & Clinical
McGraw-Hill Book Co, NY, p1251986., Munsat,T.L., 1986

Phosphorylase Deficiency
In Englel & Banker, Myology, McGraw-Hill Book Co, Ch 52, 1585-1601, DiMauro,S.&Bresolin,N., 1986

Acid Maltase Deficiency
Engel, A. G. in Engel and Banker, Myology, McGraw-Hill Co, New York, Ch 55, p. 1629-1651, , 1986

Gerstmann-Straussler-Scheinker Disease:Autopsy Study of a Familial Case
Ann Neurol 20:540-543, Vinters,H.V.,et al, 1986

Identical Twins with Hereditary Hemorrhagic Telangiectasia Concordant for Cerebrovascular Arteriovenous Malformations
Am J Med 81:931-934, Lesser,B.A.,et al, 1986

The Inheritance of Gilles De La Tourette's Syndrome & Associated Behaviors
NEJM 315:993-997, Pauls,D.L.&Leckman,J.F., 1986

Arteriovenous Malformation Presenting as Hemidystonia
Neurol 36:1590-1593, Friedman,D.I.,et al, 1986

Familial Myoclonic Dementia Masquerading as Creutzfeldt-Jakob Disease
Ann Neurol 20:231-239, Little,B.W.,et al, 1986

Fatal Familial Insomnia & Dysautonomia with Selective Degeneration of Thalamic Nuclei
NEJM 315:997-1003, Lugaresi,E.,et al, 1986

The Role of Glutamate in Neurotransmission & in Neurologic Disease
Arch Neurol 43:1058-1063, Greenamyre,J.T., 1986

Benign Sexual Headach within a Family
Arch Neurol 43:1158-1160, Johns,D.R., 1986

Adult-Onset Autosomal Dominant Limb-Girdle Muscular Dystrophy
Ann Neurol 20:240-248, Chutkow,J.G.,et al, 1986

Location of the Gene for X-Linked Spinal Muscular Atrophy
Neurol 36:1595-1598, Fischbeck,K.H.,et al, 1986

Transketolase Abnormality in Tolazamide-Induced Wernicke's Encephalopathy
Neurol 36:1508-1510, Mukherjee,A.B.,et al, 1986

Ornithine Transcarbamylase Deficiency-A Cause of Bizarre Behavior in a Man
NEJM 315:744-747, DiMagno,E.P.,et al, 1986

Brown Tumor in Secondary Hyperparathyroidism Causing Acute Paraplegia
Am J Med 81:545-547, Bohlman,M.E.,et al, 1986

Hereditary Dystonia-Parkinsonism Syndrome of Juvenile Onset
Neurol 36:1424-1428, Nygaard,T.C.&Duvoisin,R.C., 1986

Familial Long Thoracic Nerve Palsy:A Manifestation of Brachial Plexus Neuropathy
Neurol 36:1251-1253, Phillips,L.H., 1986

Bone-Marrow Transplantation for Neurovisceral Storage Disorders
Editorial, Lancet 2:788-7891986., , 1986

Tethered Spinal Cord
Editorial, Lancet 2:549-5501986., , 1986

Progressive Myoclonus Epilepsies:Specific Causes & Diagnosis
NEJM 315:296-305, Berkovic,S.F.,et al, 1986

Orthostatic Tremor in Familial-Essential Tremor
Neurol 36:1241-1245, Wee,A.S.,et al, 1986

Familial Hyperlipidemia in Stroke in the Young
Stroke 17:1142-1145, Bansal,B.C.,et al, 1986

Neuro-Ophthalmologic Findings in Vestibulocerebellar Ataxia
Arch Neurol 43:1050-1053, Farris,B.K.,et al, 1986

A Population-Based Study of Multiple Sclerosis in Twins
NEJM 315:1638-1642, Ebers,G.C.,et al, 1986

Painless Dissections of the Aorta Presenting as Acute Neurologic Syndromes
Stroke 17:644-647, Gerber,O.,et al, 1986

Showing articles 1800 to 1850 of 2292 << Previous Next >>