Amyotrophic Lateral Sclerosis
Lancet 400:1363-1380, Feldman, E.L.,et al, 2022
Complete Evaluation of Dementia: PET and MRI Correlation and Diagnosis for the Neuroradiologist
AJNR 42:998-1007, Oldan, J.D.,et al, 2021
Amyotrophic Lateral Sclerosis
NEJM 377:162-172, Brown, R.H.,et al, 2017
Non-Alzheimers Dementia 1 Frontotemporal Dementia
Lancet 386:1672-1682, Bang, Jee.,et al, 2015
Degenerative Diseases of the Nervous System, Kennedy Syndrome (X-Linked Bulbospinal Muscular Atrophy)
Adams & Victors Principles of Neurology, Chp 39, pg 1119, Ropper, A.H.,et al, 2014
The Spectrum of Mutations in Progranulin: A Collaborative Study Screening 545 Cases of Neurodegeneration
Arch Neurol 67:161-170,145, Yu,C.-E.,et al, 2010
Primary Lateral Sclerosis With HIV-1 Infection
Neurol 70:575-577, Verma,A. &Berger,J.R., 2008
Frontotemporal Lobar Degeneration with Motor Neuron Disease
Arch Neurol 63:489-490, Clark,C.M. &Forman,M.S., 2006
Brachial Amyotrophic Diplegia in a Patient with Human Immunodeficiency Virus Infection
Arch Neurol 62:817-823, Berger,J.R.,et al, 2005
Kennedy Disease
Arch Neurol 60:893-894, Paparounas,K.,et al, 2003
Jaw Drop in Kennedy's Disease
Neurol 59:1471-1472, Sumner,C.J. &Fischbeck,K.H., 2002
An ALS-Like Syndrome with New HIV Infection and Complete Response to Antiretroviral Therapy
Neurol 57:1094-1097,945, MacGowan,D.J.L.,et al, 2001
Reversible ALS-Like Disorder in HIV Infection
Neurol 57:995-1001,945, Moulignier,A.,et al, 2001
Amyotrophic lateral Sclerosis Mimic Syndromes, A Population-Based Study
Arch Neurol 57:109-113, Traynor,B.J.,et al, 2000
Linkage of Familial Amyotrophic Lateral Sclerosis with Frontotemporal Dementia to Chromosome 9q21-q22
JAMA 284:1664-1669, Hosler,B.A.,et al, 2000
MR Imaging of the Cauda Equina in Hereditary Motor Sensory Neuropathies: Correlations with Sural Nerve Biopsy
AJNR 21:1793-1798,1779, Cellerini,M.,et al, 2000
Hypertrophy of Multiple Cranial Nerves and Spinal Roots in Chronic Inflammatory Demyelinating Neuropathy
JNNP 67:685-687, Duarte,J.,et al, 1999
HTLV-I-Associated Myelopathy:Acute Progression and Atypical MR Findings
AJNR 20:1417-1421, Shakudo,M.,et al, 1999
Compression of Spinal Cord and Cauda Equina in Charcot-Marie-Tooth Disease Type 1A
Neurol 52:890-891, Butefisch,C.,et al, 1999
Olfactory Dysfunction in Guamanian ALS,Parkinsonism,and Dementia
Neurol 51:1672-1677, Ahlskog,J.E.,et al, 1998
Familial Nature and Continuing Morbidity of the Amyotrophic Lateral Sclerosis-Parkinsonism Dementia Complex of Guam
Neurol 49:400-409, McGeer,P.L.,et al, 1997
Spinobulbar Muscular Atrophy Can Mimic ALS:The Importance of Genetic Testing in Male Patients with Atypical ALS
Neurol 49:568-572, Parboosingh,J.S.,et al, 1997
Diagnosing Motor Neurone Disease
BMJ 312:650-651, Chancellor,A.M., 1996
Trinucleotide Repeat Expansion in Neurological Disease
Ann Neurol 36:814-822, LaSpada,A.R.,et al, 1994
Molecular Genetics in Neurology
Ann Neurol 34:757-773, Martin,J.B., 1993
Recurrent Encephalopathy and Seizures in a US Native with HTLV-I-Associated Myelopathy/Tropical Spastic Paraparesis
Neurol 42:658-661, Smith,C.R.,et al, 1992
Clinical and Electrodignostic Features of X-Linked Recessive Bulbospinal Neuronopathy
Neurol 41:823-828, Olney,R.K.,et al, 1991
HIV-Related Neuromuscular Syndrome Simulating Motor Neuron Disease
Neurol 40:544-546, Verma,R.K.,et al, 1990
2-Amino-3- (methylamino) -Propanoic Acid (BMAA) in Cycad Flour:An Unlikely Cause of ALS & Parkinsonism-Dementia of Guam
Neurol 40:767-772, Duncan,M.W.,et al, 1990
X-Linked Spinal Muscular Atrophy (Kennedy's Syndrome) A Kindred with Hypobetalipoproteinemia
Arch Neurol 47:1117-1120, Warner,C.L.,et al, 1990
Non Alzheimer's Disease Forms of Cerebral Atrophy
Editorial, JNNP 53:929-9311990., Neary,D., 1990
Compression Syndromes Due to Hypertrophic Nerve Roots in Hereditary Motor Sensory Neuropathy Type I
Neurol 39:1173-1177, Rosen,S.A.,et al, 1989
Neurological Clues from Environmental Neurotoxins
BMJ 295:346-347, Martyn,C.N., 1987
Isolation of LAV/HTLV-III From a Patient with Amyotrophic Lateral Sclerosis
NEJM 313:324-325, Hoffman,P.M.,et al, 1985
Benign Focal Amyotrophy
Arch Neurol 41:678-679, Riggs,J.E.,et al, 1984
Benign Familial Spinal Muscular Atrophy With Hypertrophy of the Calves
Arch Neurol 39:657-660, D'Alessandro,R.,et al, 1982
Cellular Immunity In Guamanians with Amyotrophic Lateral Sclerosis & Parkinsonism-Dementia
NEJM 299:680-685, Hoffman,P.M.,et al, 1978
Chronic Neurogenic Quadriceps Amyotrophy
Ann Neurol 2:528, Furukawa,T.,et al, 1977
Quadriceps Myopathy-Entity or Syndrome
Arch Neurol 31:60, Boddie,H.,et al, 1974
Neurotoxicity of Commonly Used Antineoplastic Agents
NEJM 291:75, 1271974., Weiss,H.,et al, 1974
Neurogenic Muscular Atrophy Simulating Facioscapulohumeral Muscular Dystrophy
J Neurol Sci 9:389, Furukawa,T.,et al, 1969
Amyotrphic Lateral Sclerosis
Arch Neurol 16:357, Hirano,A.,et al, 1967
A 60-Year-Old Man with Weakness and Gait Dysfunction
JAMA Neurol 82:305-306, Jones,F.J.S.,et al, 2025
Leptomeningitis with Communicating Hydrocephalus in an Immunocompromised Patient with Disseminated Sporotrichosis
Neurol 103:e209586, Taborda,M.H.,et al, 2024
A 26-Year-Old Woman with Chronic Progressive Gait Dysfunction
Neurol 103:e2098-e2030, Jones,F.J.S. & Orthmann-Murphy,J., 2024
Multidisciplinary End-of-Life Care for a Patient with Amyotrophic Lateral Sclerosis Requesting Euthanasia
Lancet 402:484, Kruithof,W.J.,et al, 2023
Disabling Jaw Clonus in a Patient with Bulbar-Onset Amyotrophic Lateral Sclerosis Successfully Treated with Botulinum Toxin
Neurol 99:671, Santos, M.O.,et al, 2022
Clinicopathologic Conference, Anti-IgLON5 IgG-Associated Neurologic Disorder
NEJM 386:173-180, Case 1-2022, 2022
Teaching Video NeuroImages: Jaw Clonus in Amyotrophic Lateral Sclerosis
Neurol 96:e2563, Goel, A.,et al, 2021
Natural History of "Pure" Primary Lateral Sclerosis
Neurol 96:e2231-e2238, Hassan, A.,et al, 2021