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From Enigmatic to Problematic:The New Molecular Genetics of Childhood Spinal Muscular Atrophy
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Is Chronic Respiratory Failure in Neuromuscular Diseases Worth Treating
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Motor Neuron Disease Presenting as Acute Respiratory Failure:A Clinical and Pathological Study
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Neurodegeneration and Diabetes:UK Nationwide Study of Wolfram (DIDMOAD) Syndrome
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Canavan Disease:From Spongy Degeneration to Molecular Analysis
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Dentatorubral-Pallidoluysian Atrophy:Clin Features Closely Related to Unstable Expansion of Trinucleotide (CAG) Repeat
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Amyotrophic Lateral Sclerosis:Correlation of Clinical & MR Imaging Findings
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Superoxide Dismutase and ALS
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Neuron-Specific Enolase & Myelin Basic Protein:Relation of CSF Concentr to Neuro Cond of Asphyx Full-Term Infants
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Spinal Fluid Cells and Protein in Amyotrophic Lateral Sclerosis
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The Natural History of Amyotrophic Lateral Sclerosis
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Competent Pts with Adv States of Perm Paralysis Have the Right to Forgo Life-Sustaining Therapy
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Motor Neurone Disease:A Hospice Perspective
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Surgical Treatment of Cervical Spondylotic Myelopathy:Time for a Controlled Trial
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Parental Sex Effect in Familial Amyotrophic Lateral Sclerosis
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Linkage of a Gene Causing Familial ALS to Chromosome 21 & Evidence of Genetic-Locus Heterogeneity
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Mapping of Acute (Type 1) Spinal Muscular Atrophy to Chromosome 5q12-q14
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Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
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Functional Recovery, A Major Risk Factor for the Development of Postpoliomyelitis Muscular Atrophy
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The Molecular Genetic Revolution, Its Impact on Clinical Neurology
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Olivopontocerebellar Atrophy in Children:A Report of Seven Cases in Two Families
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